A rare case of alveolar soft-part sarcoma of orbit
Alveolar soft-part sarcoma (ASPS) is a very rare, highly vascular, soft-tissue sarcoma predominantly seen in adolescents and young adults. Orbital involvement is rare, and only few case reports have been published. We report the case of a 12-year-old girl who presented with proptosis of the right ey...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2020-01-01
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| Series: | TNOA Journal of Ophthalmic Science and Research |
| Subjects: | |
| Online Access: | http://www.tnoajosr.com/article.asp?issn=2589-4528;year=2020;volume=58;issue=2;spage=115;epage=118;aulast=Rangarajan |
| _version_ | 1811295588688330752 |
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| author | Viji Rangarajan Sindhuja Murugesan Kavitha Ramakrishnan S Priya |
| author_facet | Viji Rangarajan Sindhuja Murugesan Kavitha Ramakrishnan S Priya |
| author_sort | Viji Rangarajan |
| collection | DOAJ |
| description | Alveolar soft-part sarcoma (ASPS) is a very rare, highly vascular, soft-tissue sarcoma predominantly seen in adolescents and young adults. Orbital involvement is rare, and only few case reports have been published. We report the case of a 12-year-old girl who presented with proptosis of the right eye of 2 months' duration. Magnetic resonance imaging showed a well-defined lesion in the superolateral right orbit, with the possibility of a hemangioma. Right-eye lateral orbitotomy with excision biopsy of the mass was done. Histopathology revealed ASPS, and the patient was referred for metastatic workup. |
| first_indexed | 2024-04-13T05:35:43Z |
| format | Article |
| id | doaj.art-56a02ef1b6664db0887e1b6b4f7a9885 |
| institution | Directory Open Access Journal |
| issn | 2589-4528 2589-4536 |
| language | English |
| last_indexed | 2024-04-13T05:35:43Z |
| publishDate | 2020-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | TNOA Journal of Ophthalmic Science and Research |
| spelling | doaj.art-56a02ef1b6664db0887e1b6b4f7a98852022-12-22T03:00:18ZengWolters Kluwer Medknow PublicationsTNOA Journal of Ophthalmic Science and Research2589-45282589-45362020-01-0158211511810.4103/tjosr.tjosr_114_19A rare case of alveolar soft-part sarcoma of orbitViji RangarajanSindhuja MurugesanKavitha RamakrishnanS PriyaAlveolar soft-part sarcoma (ASPS) is a very rare, highly vascular, soft-tissue sarcoma predominantly seen in adolescents and young adults. Orbital involvement is rare, and only few case reports have been published. We report the case of a 12-year-old girl who presented with proptosis of the right eye of 2 months' duration. Magnetic resonance imaging showed a well-defined lesion in the superolateral right orbit, with the possibility of a hemangioma. Right-eye lateral orbitotomy with excision biopsy of the mass was done. Histopathology revealed ASPS, and the patient was referred for metastatic workup.http://www.tnoajosr.com/article.asp?issn=2589-4528;year=2020;volume=58;issue=2;spage=115;epage=118;aulast=Rangarajanalveolar soft-part sarcomaorbitpediatric |
| spellingShingle | Viji Rangarajan Sindhuja Murugesan Kavitha Ramakrishnan S Priya A rare case of alveolar soft-part sarcoma of orbit TNOA Journal of Ophthalmic Science and Research alveolar soft-part sarcoma orbit pediatric |
| title | A rare case of alveolar soft-part sarcoma of orbit |
| title_full | A rare case of alveolar soft-part sarcoma of orbit |
| title_fullStr | A rare case of alveolar soft-part sarcoma of orbit |
| title_full_unstemmed | A rare case of alveolar soft-part sarcoma of orbit |
| title_short | A rare case of alveolar soft-part sarcoma of orbit |
| title_sort | rare case of alveolar soft part sarcoma of orbit |
| topic | alveolar soft-part sarcoma orbit pediatric |
| url | http://www.tnoajosr.com/article.asp?issn=2589-4528;year=2020;volume=58;issue=2;spage=115;epage=118;aulast=Rangarajan |
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