A cluster of inappropriate shocks in a pediatric S-ICD patient - how to troubleshoot?

We present the case of a 16-year-old male pediatric patient diagnosed with hypertrophic cardiomyopathy (HCM, identified as having a high risk of sudden cardiac death (SCD), who underwent a successful subcutaneous implantable cardiac defibrillator (S-ICD) implantation as a primary prevention measure...

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Main Authors: Christina Menexi, Mohamed ElRefai, David Farwell, Neil Srinivasan
Format: Article
Language:English
Published: Elsevier 2024-03-01
Series:Indian Pacing and Electrophysiology Journal
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S0972629223001328
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author Christina Menexi
Mohamed ElRefai
David Farwell
Neil Srinivasan
author_facet Christina Menexi
Mohamed ElRefai
David Farwell
Neil Srinivasan
author_sort Christina Menexi
collection DOAJ
description We present the case of a 16-year-old male pediatric patient diagnosed with hypertrophic cardiomyopathy (HCM, identified as having a high risk of sudden cardiac death (SCD), who underwent a successful subcutaneous implantable cardiac defibrillator (S-ICD) implantation as a primary prevention measure in 2018.His past medical history included ADHD, Autism, and panic attacks. The patient experienced appropriate shocks that successfully terminated VF episodes. However, he also experienced multiple inappropriate shocks from the S-ICD, triggered by anxiety-induced tachycardia during panic episodes. Meticulous assessment of S-ICD tracings and electrocardiograms (ECGs) revealed the erroneous classification of sinus tachycardia as sustained ventricular tachycardia, leading to unwarranted therapeutic interventions.Clinical intervention involved reprogramming of the S-ICD, emphasizing the pivotal role of personalized device configuration in pediatric cases where fine margins matter. While literature on S-ICD use in pediatric populations remains limited, emerging registries underscore the efficacy and safety of S-ICDs in preventing sudden cardiac death while reducing complications associated with intravascular leads. This case underscores the critical nature of customized device programming in pediatric patients, underscoring S-ICDs as a practical defibrillation alternative that addresses distinct concerns within this cohort of patients.
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spelling doaj.art-56fc72b7ef21408eaae0fff9174a19cf2024-04-03T04:26:07ZengElsevierIndian Pacing and Electrophysiology Journal0972-62922024-03-0124294104A cluster of inappropriate shocks in a pediatric S-ICD patient - how to troubleshoot?Christina Menexi0Mohamed ElRefai1David Farwell2Neil Srinivasan3Cardiothoracic Center, Essex, UK; Corresponding author. Cardiothoracic center, Essex, UK.Cambridge University Hospital, Cambridge, UKCardiothoracic Center, Essex, UKCardiothoracic Center, Essex, UK; Circulatory Health Research Group, Medical Technology Research Centre, School of Medicine, Anglia Ruskin University, Essex, UKWe present the case of a 16-year-old male pediatric patient diagnosed with hypertrophic cardiomyopathy (HCM, identified as having a high risk of sudden cardiac death (SCD), who underwent a successful subcutaneous implantable cardiac defibrillator (S-ICD) implantation as a primary prevention measure in 2018.His past medical history included ADHD, Autism, and panic attacks. The patient experienced appropriate shocks that successfully terminated VF episodes. However, he also experienced multiple inappropriate shocks from the S-ICD, triggered by anxiety-induced tachycardia during panic episodes. Meticulous assessment of S-ICD tracings and electrocardiograms (ECGs) revealed the erroneous classification of sinus tachycardia as sustained ventricular tachycardia, leading to unwarranted therapeutic interventions.Clinical intervention involved reprogramming of the S-ICD, emphasizing the pivotal role of personalized device configuration in pediatric cases where fine margins matter. While literature on S-ICD use in pediatric populations remains limited, emerging registries underscore the efficacy and safety of S-ICDs in preventing sudden cardiac death while reducing complications associated with intravascular leads. This case underscores the critical nature of customized device programming in pediatric patients, underscoring S-ICDs as a practical defibrillation alternative that addresses distinct concerns within this cohort of patients.http://www.sciencedirect.com/science/article/pii/S0972629223001328Subcutaneous implantable cardioverter defibrillatorPediatric cardiologySudden cardiac deathPersonalized device therapyInappropriate shocks
spellingShingle Christina Menexi
Mohamed ElRefai
David Farwell
Neil Srinivasan
A cluster of inappropriate shocks in a pediatric S-ICD patient - how to troubleshoot?
Indian Pacing and Electrophysiology Journal
Subcutaneous implantable cardioverter defibrillator
Pediatric cardiology
Sudden cardiac death
Personalized device therapy
Inappropriate shocks
title A cluster of inappropriate shocks in a pediatric S-ICD patient - how to troubleshoot?
title_full A cluster of inappropriate shocks in a pediatric S-ICD patient - how to troubleshoot?
title_fullStr A cluster of inappropriate shocks in a pediatric S-ICD patient - how to troubleshoot?
title_full_unstemmed A cluster of inappropriate shocks in a pediatric S-ICD patient - how to troubleshoot?
title_short A cluster of inappropriate shocks in a pediatric S-ICD patient - how to troubleshoot?
title_sort cluster of inappropriate shocks in a pediatric s icd patient how to troubleshoot
topic Subcutaneous implantable cardioverter defibrillator
Pediatric cardiology
Sudden cardiac death
Personalized device therapy
Inappropriate shocks
url http://www.sciencedirect.com/science/article/pii/S0972629223001328
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