Unguarded left atrioventricular orifice: An unusual cause of hypoplastic left ventricle and double-outlet right ventricle with intact ventricular septum
An unguarded atrioventricular orifice is an extremely rare congenital anomaly characterized by the absence of the atrioventricular valve in varying proportions. While atresia of the mitral or aortic valves are usually described as causes for hypoplastic left heart, our case highlights the role of fr...
| Main Authors: | , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2019-01-01
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| Series: | Annals of Pediatric Cardiology |
| Subjects: | |
| Online Access: | http://www.annalspc.com/article.asp?issn=0974-2069;year=2019;volume=12;issue=2;spage=153;epage=155;aulast=Subramanian |
| _version_ | 1819003817528655872 |
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| author | Anand Subramanian A P Bharath M Jayaranganath |
| author_facet | Anand Subramanian A P Bharath M Jayaranganath |
| author_sort | Anand Subramanian |
| collection | DOAJ |
| description | An unguarded atrioventricular orifice is an extremely rare congenital anomaly characterized by the absence of the atrioventricular valve in varying proportions. While atresia of the mitral or aortic valves are usually described as causes for hypoplastic left heart, our case highlights the role of free atrioventricular valve regurgitation and consequent volume loss of the left heart, giving rise to a small left ventricle. There was an associated double-outlet right ventricle and Type B aortic interruption. While we have attempted to discuss the complex management options in this scenario, the parents decided to withdraw further care. |
| first_indexed | 2024-12-20T23:27:02Z |
| format | Article |
| id | doaj.art-57c5aaad3c68431da6f8240dbdd4c1eb |
| institution | Directory Open Access Journal |
| issn | 0974-2069 |
| language | English |
| last_indexed | 2024-12-20T23:27:02Z |
| publishDate | 2019-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Annals of Pediatric Cardiology |
| spelling | doaj.art-57c5aaad3c68431da6f8240dbdd4c1eb2022-12-21T19:23:23ZengWolters Kluwer Medknow PublicationsAnnals of Pediatric Cardiology0974-20692019-01-0112215315510.4103/apc.APC_124_18Unguarded left atrioventricular orifice: An unusual cause of hypoplastic left ventricle and double-outlet right ventricle with intact ventricular septumAnand SubramanianA P BharathM JayaranganathAn unguarded atrioventricular orifice is an extremely rare congenital anomaly characterized by the absence of the atrioventricular valve in varying proportions. While atresia of the mitral or aortic valves are usually described as causes for hypoplastic left heart, our case highlights the role of free atrioventricular valve regurgitation and consequent volume loss of the left heart, giving rise to a small left ventricle. There was an associated double-outlet right ventricle and Type B aortic interruption. While we have attempted to discuss the complex management options in this scenario, the parents decided to withdraw further care.http://www.annalspc.com/article.asp?issn=0974-2069;year=2019;volume=12;issue=2;spage=153;epage=155;aulast=SubramanianCongenital mitral valve absencedouble-outlet right ventriclehypoplastic left ventricle |
| spellingShingle | Anand Subramanian A P Bharath M Jayaranganath Unguarded left atrioventricular orifice: An unusual cause of hypoplastic left ventricle and double-outlet right ventricle with intact ventricular septum Annals of Pediatric Cardiology Congenital mitral valve absence double-outlet right ventricle hypoplastic left ventricle |
| title | Unguarded left atrioventricular orifice: An unusual cause of hypoplastic left ventricle and double-outlet right ventricle with intact ventricular septum |
| title_full | Unguarded left atrioventricular orifice: An unusual cause of hypoplastic left ventricle and double-outlet right ventricle with intact ventricular septum |
| title_fullStr | Unguarded left atrioventricular orifice: An unusual cause of hypoplastic left ventricle and double-outlet right ventricle with intact ventricular septum |
| title_full_unstemmed | Unguarded left atrioventricular orifice: An unusual cause of hypoplastic left ventricle and double-outlet right ventricle with intact ventricular septum |
| title_short | Unguarded left atrioventricular orifice: An unusual cause of hypoplastic left ventricle and double-outlet right ventricle with intact ventricular septum |
| title_sort | unguarded left atrioventricular orifice an unusual cause of hypoplastic left ventricle and double outlet right ventricle with intact ventricular septum |
| topic | Congenital mitral valve absence double-outlet right ventricle hypoplastic left ventricle |
| url | http://www.annalspc.com/article.asp?issn=0974-2069;year=2019;volume=12;issue=2;spage=153;epage=155;aulast=Subramanian |
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