Basal encephalocele associated with morning glory syndrome: case report Encefalocele basal associada a síndrome "morning glory": relato de caso

The basal encephaloceles refer to rare entities and they correspond to herniation of brain tissue through defects of skull along the cribiform plate or the sphenoid bone. A rare morning glory syndrome, with characteristic retinal defect has been reported in association with basal encephaloceles. Hyp...

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Main Authors: Ivanete Minotto, Nitamar Abdala, Adriana Aparecida Siviero Miachon, Angela Maria Spinola e Castro, Paulo Imamura, Roberto Gomes Nogueira
Format: Article
Language:English
Published: Academia Brasileira de Neurologia (ABNEURO) 2007-12-01
Series:Arquivos de Neuro-Psiquiatria
Subjects:
Online Access:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2007000600013
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author Ivanete Minotto
Nitamar Abdala
Adriana Aparecida Siviero Miachon
Angela Maria Spinola e Castro
Paulo Imamura
Roberto Gomes Nogueira
author_facet Ivanete Minotto
Nitamar Abdala
Adriana Aparecida Siviero Miachon
Angela Maria Spinola e Castro
Paulo Imamura
Roberto Gomes Nogueira
author_sort Ivanete Minotto
collection DOAJ
description The basal encephaloceles refer to rare entities and they correspond to herniation of brain tissue through defects of skull along the cribiform plate or the sphenoid bone. A rare morning glory syndrome, with characteristic retinal defect has been reported in association with basal encephaloceles. Hypophysis hormonal deficiencies may occur. We accounted for a pituitary dwarfism with delayed diagnosed transsphenoidal encephalocele associated with morning glory syndrome, showing the alterations found in retinography, computed tomography and magnetic resonance imaging.<br>As encefaloceles basais são entidades raras e correspondem a herniações do tecido cerebral através de um defeito do crânio, ao longo da lâmina crivosa etmoidal ou do osso esfenoidal. A rara síndrome morning glory, com alterações de fundo de olho características pode apresentar-se associada à encefalocele basal. Deficiências hormonais hipofisárias podem ocorrer. Relatamos caso de nanismo hipofisário com encefalocele transesfenoidal de diagnóstico tardio associada à síndrome de morning glory, mostrando as alterações na retinografia, tomografia computadorizada e ressonância magnética.
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spelling doaj.art-596502bd59e84231bbe80043d58b6d3d2022-12-22T03:21:09ZengAcademia Brasileira de Neurologia (ABNEURO)Arquivos de Neuro-Psiquiatria0004-282X1678-42272007-12-01654a98899110.1590/S0004-282X2007000600013Basal encephalocele associated with morning glory syndrome: case report Encefalocele basal associada a síndrome "morning glory": relato de casoIvanete MinottoNitamar AbdalaAdriana Aparecida Siviero MiachonAngela Maria Spinola e CastroPaulo ImamuraRoberto Gomes NogueiraThe basal encephaloceles refer to rare entities and they correspond to herniation of brain tissue through defects of skull along the cribiform plate or the sphenoid bone. A rare morning glory syndrome, with characteristic retinal defect has been reported in association with basal encephaloceles. Hypophysis hormonal deficiencies may occur. We accounted for a pituitary dwarfism with delayed diagnosed transsphenoidal encephalocele associated with morning glory syndrome, showing the alterations found in retinography, computed tomography and magnetic resonance imaging.<br>As encefaloceles basais são entidades raras e correspondem a herniações do tecido cerebral através de um defeito do crânio, ao longo da lâmina crivosa etmoidal ou do osso esfenoidal. A rara síndrome morning glory, com alterações de fundo de olho características pode apresentar-se associada à encefalocele basal. Deficiências hormonais hipofisárias podem ocorrer. Relatamos caso de nanismo hipofisário com encefalocele transesfenoidal de diagnóstico tardio associada à síndrome de morning glory, mostrando as alterações na retinografia, tomografia computadorizada e ressonância magnética.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2007000600013encefalocele basalsíndrome de "morning glory"tomografia computadorizadaressonância magnéticananismo hipofisáriobasal encephalocelemorning glory syndromecomputed tomographymagnetic resonance imagingpituitary dwarfism
spellingShingle Ivanete Minotto
Nitamar Abdala
Adriana Aparecida Siviero Miachon
Angela Maria Spinola e Castro
Paulo Imamura
Roberto Gomes Nogueira
Basal encephalocele associated with morning glory syndrome: case report Encefalocele basal associada a síndrome "morning glory": relato de caso
Arquivos de Neuro-Psiquiatria
encefalocele basal
síndrome de "morning glory"
tomografia computadorizada
ressonância magnética
nanismo hipofisário
basal encephalocele
morning glory syndrome
computed tomography
magnetic resonance imaging
pituitary dwarfism
title Basal encephalocele associated with morning glory syndrome: case report Encefalocele basal associada a síndrome "morning glory": relato de caso
title_full Basal encephalocele associated with morning glory syndrome: case report Encefalocele basal associada a síndrome "morning glory": relato de caso
title_fullStr Basal encephalocele associated with morning glory syndrome: case report Encefalocele basal associada a síndrome "morning glory": relato de caso
title_full_unstemmed Basal encephalocele associated with morning glory syndrome: case report Encefalocele basal associada a síndrome "morning glory": relato de caso
title_short Basal encephalocele associated with morning glory syndrome: case report Encefalocele basal associada a síndrome "morning glory": relato de caso
title_sort basal encephalocele associated with morning glory syndrome case report encefalocele basal associada a sindrome morning glory relato de caso
topic encefalocele basal
síndrome de "morning glory"
tomografia computadorizada
ressonância magnética
nanismo hipofisário
basal encephalocele
morning glory syndrome
computed tomography
magnetic resonance imaging
pituitary dwarfism
url http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2007000600013
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