Basal encephalocele associated with morning glory syndrome: case report Encefalocele basal associada a síndrome "morning glory": relato de caso
The basal encephaloceles refer to rare entities and they correspond to herniation of brain tissue through defects of skull along the cribiform plate or the sphenoid bone. A rare morning glory syndrome, with characteristic retinal defect has been reported in association with basal encephaloceles. Hyp...
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Academia Brasileira de Neurologia (ABNEURO)
2007-12-01
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Series: | Arquivos de Neuro-Psiquiatria |
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Online Access: | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2007000600013 |
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author | Ivanete Minotto Nitamar Abdala Adriana Aparecida Siviero Miachon Angela Maria Spinola e Castro Paulo Imamura Roberto Gomes Nogueira |
author_facet | Ivanete Minotto Nitamar Abdala Adriana Aparecida Siviero Miachon Angela Maria Spinola e Castro Paulo Imamura Roberto Gomes Nogueira |
author_sort | Ivanete Minotto |
collection | DOAJ |
description | The basal encephaloceles refer to rare entities and they correspond to herniation of brain tissue through defects of skull along the cribiform plate or the sphenoid bone. A rare morning glory syndrome, with characteristic retinal defect has been reported in association with basal encephaloceles. Hypophysis hormonal deficiencies may occur. We accounted for a pituitary dwarfism with delayed diagnosed transsphenoidal encephalocele associated with morning glory syndrome, showing the alterations found in retinography, computed tomography and magnetic resonance imaging.<br>As encefaloceles basais são entidades raras e correspondem a herniações do tecido cerebral através de um defeito do crânio, ao longo da lâmina crivosa etmoidal ou do osso esfenoidal. A rara síndrome morning glory, com alterações de fundo de olho características pode apresentar-se associada à encefalocele basal. Deficiências hormonais hipofisárias podem ocorrer. Relatamos caso de nanismo hipofisário com encefalocele transesfenoidal de diagnóstico tardio associada à síndrome de morning glory, mostrando as alterações na retinografia, tomografia computadorizada e ressonância magnética. |
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issn | 0004-282X 1678-4227 |
language | English |
last_indexed | 2024-04-12T18:28:01Z |
publishDate | 2007-12-01 |
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record_format | Article |
series | Arquivos de Neuro-Psiquiatria |
spelling | doaj.art-596502bd59e84231bbe80043d58b6d3d2022-12-22T03:21:09ZengAcademia Brasileira de Neurologia (ABNEURO)Arquivos de Neuro-Psiquiatria0004-282X1678-42272007-12-01654a98899110.1590/S0004-282X2007000600013Basal encephalocele associated with morning glory syndrome: case report Encefalocele basal associada a síndrome "morning glory": relato de casoIvanete MinottoNitamar AbdalaAdriana Aparecida Siviero MiachonAngela Maria Spinola e CastroPaulo ImamuraRoberto Gomes NogueiraThe basal encephaloceles refer to rare entities and they correspond to herniation of brain tissue through defects of skull along the cribiform plate or the sphenoid bone. A rare morning glory syndrome, with characteristic retinal defect has been reported in association with basal encephaloceles. Hypophysis hormonal deficiencies may occur. We accounted for a pituitary dwarfism with delayed diagnosed transsphenoidal encephalocele associated with morning glory syndrome, showing the alterations found in retinography, computed tomography and magnetic resonance imaging.<br>As encefaloceles basais são entidades raras e correspondem a herniações do tecido cerebral através de um defeito do crânio, ao longo da lâmina crivosa etmoidal ou do osso esfenoidal. A rara síndrome morning glory, com alterações de fundo de olho características pode apresentar-se associada à encefalocele basal. Deficiências hormonais hipofisárias podem ocorrer. Relatamos caso de nanismo hipofisário com encefalocele transesfenoidal de diagnóstico tardio associada à síndrome de morning glory, mostrando as alterações na retinografia, tomografia computadorizada e ressonância magnética.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2007000600013encefalocele basalsíndrome de "morning glory"tomografia computadorizadaressonância magnéticananismo hipofisáriobasal encephalocelemorning glory syndromecomputed tomographymagnetic resonance imagingpituitary dwarfism |
spellingShingle | Ivanete Minotto Nitamar Abdala Adriana Aparecida Siviero Miachon Angela Maria Spinola e Castro Paulo Imamura Roberto Gomes Nogueira Basal encephalocele associated with morning glory syndrome: case report Encefalocele basal associada a síndrome "morning glory": relato de caso Arquivos de Neuro-Psiquiatria encefalocele basal síndrome de "morning glory" tomografia computadorizada ressonância magnética nanismo hipofisário basal encephalocele morning glory syndrome computed tomography magnetic resonance imaging pituitary dwarfism |
title | Basal encephalocele associated with morning glory syndrome: case report Encefalocele basal associada a síndrome "morning glory": relato de caso |
title_full | Basal encephalocele associated with morning glory syndrome: case report Encefalocele basal associada a síndrome "morning glory": relato de caso |
title_fullStr | Basal encephalocele associated with morning glory syndrome: case report Encefalocele basal associada a síndrome "morning glory": relato de caso |
title_full_unstemmed | Basal encephalocele associated with morning glory syndrome: case report Encefalocele basal associada a síndrome "morning glory": relato de caso |
title_short | Basal encephalocele associated with morning glory syndrome: case report Encefalocele basal associada a síndrome "morning glory": relato de caso |
title_sort | basal encephalocele associated with morning glory syndrome case report encefalocele basal associada a sindrome morning glory relato de caso |
topic | encefalocele basal síndrome de "morning glory" tomografia computadorizada ressonância magnética nanismo hipofisário basal encephalocele morning glory syndrome computed tomography magnetic resonance imaging pituitary dwarfism |
url | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2007000600013 |
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