Doege-Potter syndrome: a rare presentation of a solitary fibrous tumor of the pleura
Solitary fibrous tumors of the pleura usually have a benign behavior, although some may present malignant characteristics - recurrences, metastases, and paraneoplastic syndromes. When a solitary fibrous tumor is responsible for the development of hypoglycemia, we have a case of Doege-Potter syndrome...
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| Format: | Article |
| Language: | English |
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Sociedade Brasileira de Oncologia Clínica, Sociedade Brasileira de Cirurgia Clínica and Sociedade Brasileira de Radioterapia
2021-10-01
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| Series: | Brazilian Journal of Oncology |
| Subjects: | |
| Online Access: | http://www.brazilianjournalofoncology.com.br/details/145/en-US/doege-potter-syndrome--a-rare-presentation-of-a-solitary-fibrous-tumor-of-the-pleura |
| _version_ | 1797673854621974528 |
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| author | Liu Estradioto Rodrigo Bettega de Araujo Nelson Bergonse Vanessa Bettega de Araújo Marlos de Souza Coelho Larissa Luvison Gomes da Silva |
| author_facet | Liu Estradioto Rodrigo Bettega de Araujo Nelson Bergonse Vanessa Bettega de Araújo Marlos de Souza Coelho Larissa Luvison Gomes da Silva |
| author_sort | Liu Estradioto |
| collection | DOAJ |
| description | Solitary fibrous tumors of the pleura usually have a benign behavior, although some may present malignant characteristics - recurrences, metastases, and paraneoplastic syndromes. When a solitary fibrous tumor is responsible for the development of hypoglycemia, we have a case of Doege-Potter syndrome. We describe a case of a male patient that presented recurring and severe hypoglycemia, being also diagnosed with an extensive intrathoracic mass, which was proven to be a solitary fibrous tumor of the pleura. The treatment, through the maintenance of proper serum levels of glucose (administration of solutions with glucose and steroids), followed by the surgical resection of the tumor, promoted the complete resolution of the hypoglycemia episodes. The early recognition of this condition and the proper treatment is essential for a good clinical outcome. It is important to underscore that the multidisciplinary evaluation (oncologists, radiologists, surgeons, and pathologists) of rare tumors is recommended to achieve better therapeutic results. |
| first_indexed | 2024-03-11T21:51:23Z |
| format | Article |
| id | doaj.art-59a7621fb63442bea3215a9df3b600a1 |
| institution | Directory Open Access Journal |
| issn | 2526-8732 |
| language | English |
| last_indexed | 2024-03-11T21:51:23Z |
| publishDate | 2021-10-01 |
| publisher | Sociedade Brasileira de Oncologia Clínica, Sociedade Brasileira de Cirurgia Clínica and Sociedade Brasileira de Radioterapia |
| record_format | Article |
| series | Brazilian Journal of Oncology |
| spelling | doaj.art-59a7621fb63442bea3215a9df3b600a12023-09-26T09:00:16ZengSociedade Brasileira de Oncologia Clínica, Sociedade Brasileira de Cirurgia Clínica and Sociedade Brasileira de RadioterapiaBrazilian Journal of Oncology2526-87322021-10-01170010.5935/2526-8732.20210001Doege-Potter syndrome: a rare presentation of a solitary fibrous tumor of the pleuraLiu Estradioto0Rodrigo Bettega de Araujo1https://orcid.org/0000-0001-7234-7124Nelson Bergonse2Vanessa Bettega de Araújo3Marlos de Souza Coelho4Larissa Luvison Gomes da Silva5Hospital Santa Casa de Misericórdia de Curitiba, Thoracic Surgery - Curitiba - Paraná - BrazilHospital Santa Casa de Misericórdia de Curitiba, Thoracic Surgery - Curitiba - Paraná - BrazilHospital Santa Casa de Misericórdia de Curitiba, Thoracic Surgery - Curitiba - Paraná - BrazilHospital Santa Casa de Misericórdia de Curitiba, Thoracic Surgery - Curitiba - Paraná - BrazilHospital Santa Casa de Misericórdia de Curitiba, Thoracic Surgery - Curitiba - Paraná - BrazilHospital Santa Casa de Misericórdia de Curitiba, Thoracic Surgery - Curitiba - Paraná - BrazilSolitary fibrous tumors of the pleura usually have a benign behavior, although some may present malignant characteristics - recurrences, metastases, and paraneoplastic syndromes. When a solitary fibrous tumor is responsible for the development of hypoglycemia, we have a case of Doege-Potter syndrome. We describe a case of a male patient that presented recurring and severe hypoglycemia, being also diagnosed with an extensive intrathoracic mass, which was proven to be a solitary fibrous tumor of the pleura. The treatment, through the maintenance of proper serum levels of glucose (administration of solutions with glucose and steroids), followed by the surgical resection of the tumor, promoted the complete resolution of the hypoglycemia episodes. The early recognition of this condition and the proper treatment is essential for a good clinical outcome. It is important to underscore that the multidisciplinary evaluation (oncologists, radiologists, surgeons, and pathologists) of rare tumors is recommended to achieve better therapeutic results.http://www.brazilianjournalofoncology.com.br/details/145/en-US/doege-potter-syndrome--a-rare-presentation-of-a-solitary-fibrous-tumor-of-the-pleurasolitary fibrous tumorpleuralparaneoplastic endocrine syndromesthoracic neoplasms |
| spellingShingle | Liu Estradioto Rodrigo Bettega de Araujo Nelson Bergonse Vanessa Bettega de Araújo Marlos de Souza Coelho Larissa Luvison Gomes da Silva Doege-Potter syndrome: a rare presentation of a solitary fibrous tumor of the pleura Brazilian Journal of Oncology solitary fibrous tumor pleural paraneoplastic endocrine syndromes thoracic neoplasms |
| title | Doege-Potter syndrome: a rare presentation of a solitary fibrous tumor of the pleura |
| title_full | Doege-Potter syndrome: a rare presentation of a solitary fibrous tumor of the pleura |
| title_fullStr | Doege-Potter syndrome: a rare presentation of a solitary fibrous tumor of the pleura |
| title_full_unstemmed | Doege-Potter syndrome: a rare presentation of a solitary fibrous tumor of the pleura |
| title_short | Doege-Potter syndrome: a rare presentation of a solitary fibrous tumor of the pleura |
| title_sort | doege potter syndrome a rare presentation of a solitary fibrous tumor of the pleura |
| topic | solitary fibrous tumor pleural paraneoplastic endocrine syndromes thoracic neoplasms |
| url | http://www.brazilianjournalofoncology.com.br/details/145/en-US/doege-potter-syndrome--a-rare-presentation-of-a-solitary-fibrous-tumor-of-the-pleura |
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