Phacomatosis pigmentovascularis of cesioflammea type
Abstract Phacomatosis pigmentovascularis is a rare syndrome, defined as the simultaneous presence of vascular nevus and melanocytic nevus in the same patient. We report the case of a 53-year-old woman presented with dermal melanosis and extensive vascular nevus, which match the typical manifestation...
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| Format: | Article |
| Language: | English |
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Sociedade Brasileira de Dermatologia
2016-10-01
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| Series: | Anais Brasileiros de Dermatologia |
| Subjects: | |
| Online Access: | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962016001100054&tlng=en |
| _version_ | 1798019751454179328 |
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| author | Delky Johanna Villarreal Villarreal Fabiano Leal |
| author_facet | Delky Johanna Villarreal Villarreal Fabiano Leal |
| author_sort | Delky Johanna Villarreal Villarreal |
| collection | DOAJ |
| description | Abstract Phacomatosis pigmentovascularis is a rare syndrome, defined as the simultaneous presence of vascular nevus and melanocytic nevus in the same patient. We report the case of a 53-year-old woman presented with dermal melanosis and extensive vascular nevus, which match the typical manifestations of phakomatosis pigmetovascularis of cesioflammea type, according to Happle's classification. The rare occurrence of this genodermatosis and the clinical exuberance of the skin lesions motivated this case report. |
| first_indexed | 2024-04-11T16:45:59Z |
| format | Article |
| id | doaj.art-59c6293c40bb4087b1b9aac61019d4db |
| institution | Directory Open Access Journal |
| issn | 0365-0596 |
| language | English |
| last_indexed | 2024-04-11T16:45:59Z |
| publishDate | 2016-10-01 |
| publisher | Sociedade Brasileira de Dermatologia |
| record_format | Article |
| series | Anais Brasileiros de Dermatologia |
| spelling | doaj.art-59c6293c40bb4087b1b9aac61019d4db2022-12-22T04:13:33ZengSociedade Brasileira de DermatologiaAnais Brasileiros de Dermatologia0365-05962016-10-01915 suppl 1545610.1590/abd1806-4841.20164516Phacomatosis pigmentovascularis of cesioflammea typeDelky Johanna Villarreal VillarrealFabiano LealAbstract Phacomatosis pigmentovascularis is a rare syndrome, defined as the simultaneous presence of vascular nevus and melanocytic nevus in the same patient. We report the case of a 53-year-old woman presented with dermal melanosis and extensive vascular nevus, which match the typical manifestations of phakomatosis pigmetovascularis of cesioflammea type, according to Happle's classification. The rare occurrence of this genodermatosis and the clinical exuberance of the skin lesions motivated this case report.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962016001100054&tlng=enMelanocytesNevusNevus of OtaPort-wine stainSkin abnormalitiesSkin pigmentation |
| spellingShingle | Delky Johanna Villarreal Villarreal Fabiano Leal Phacomatosis pigmentovascularis of cesioflammea type Anais Brasileiros de Dermatologia Melanocytes Nevus Nevus of Ota Port-wine stain Skin abnormalities Skin pigmentation |
| title | Phacomatosis pigmentovascularis of cesioflammea type |
| title_full | Phacomatosis pigmentovascularis of cesioflammea type |
| title_fullStr | Phacomatosis pigmentovascularis of cesioflammea type |
| title_full_unstemmed | Phacomatosis pigmentovascularis of cesioflammea type |
| title_short | Phacomatosis pigmentovascularis of cesioflammea type |
| title_sort | phacomatosis pigmentovascularis of cesioflammea type |
| topic | Melanocytes Nevus Nevus of Ota Port-wine stain Skin abnormalities Skin pigmentation |
| url | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962016001100054&tlng=en |
| work_keys_str_mv | AT delkyjohannavillarrealvillarreal phacomatosispigmentovascularisofcesioflammeatype AT fabianoleal phacomatosispigmentovascularisofcesioflammeatype |