Hand surgery and hand therapy clinical practice guideline for epidermolysis bullosa
Abstract What is already known about this topic? Epidermolysis bullosa (EB) causes blistering and scarring of the hands resulting in contractures fused web spaces and altered function. Surgery is needed to release contractures and web spaces and hand therapy is essential to maintain results, approac...
| Main Authors: | , , , , , , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
BMC
2022-11-01
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| Series: | Orphanet Journal of Rare Diseases |
| Online Access: | https://doi.org/10.1186/s13023-022-02282-0 |
| _version_ | 1798018188678529024 |
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| author | Rachel Box Catina Bernardis Alexander Pleshkov Nicky Jessop Catherine Miller Jennifer Skye Virginia O’Brien Matthew Veerkamp Anna Carolina Ferreira da Rocha Roger Cornwall |
| author_facet | Rachel Box Catina Bernardis Alexander Pleshkov Nicky Jessop Catherine Miller Jennifer Skye Virginia O’Brien Matthew Veerkamp Anna Carolina Ferreira da Rocha Roger Cornwall |
| author_sort | Rachel Box |
| collection | DOAJ |
| description | Abstract What is already known about this topic? Epidermolysis bullosa (EB) causes blistering and scarring of the hands resulting in contractures fused web spaces and altered function. Surgery is needed to release contractures and web spaces and hand therapy is essential to maintain results, approaches for both differ. What does this study add? These guidelines aim to provide information on the surgical and conservative therapeutic hand management of children and adults diagnosed with EB. They are based on available evidence and expert consensus to assist hand surgeons and therapists in decision making, planning and treatment. They highlight the importance of a holistic multidisciplinary team (MDT) approach, where patient priorities are paramount. |
| first_indexed | 2024-04-11T16:19:53Z |
| format | Article |
| id | doaj.art-5a272292edc44651a20b3c4262ccf1f7 |
| institution | Directory Open Access Journal |
| issn | 1750-1172 |
| language | English |
| last_indexed | 2024-04-11T16:19:53Z |
| publishDate | 2022-11-01 |
| publisher | BMC |
| record_format | Article |
| series | Orphanet Journal of Rare Diseases |
| spelling | doaj.art-5a272292edc44651a20b3c4262ccf1f72022-12-22T04:14:25ZengBMCOrphanet Journal of Rare Diseases1750-11722022-11-0117112110.1186/s13023-022-02282-0Hand surgery and hand therapy clinical practice guideline for epidermolysis bullosaRachel Box0Catina Bernardis1Alexander Pleshkov2Nicky Jessop3Catherine Miller4Jennifer Skye5Virginia O’Brien6Matthew Veerkamp7Anna Carolina Ferreira da Rocha8Roger Cornwall9Hand Therapy Department, Guy’s and St Thomas’ NHS Foundation TrustHand Surgery Department, Guy’s and St Thomas’ NHS Foundation TrustFederal State Budgetary Institution All-Russian Centre for Emergency and Radiation MedicineClinical Specialist Congenital Hand Anomalies and Dermatology, Great Ormond Street Hospital for Children NHS Foundation Trust, Occupational TherapyPlastic Surgery/Dermatology, Great Ormond Street Hospital for Children, NHS Foundation TrustFairview Health Services/M Health, University of MinnesotaFairview Health Services/M Health, University of MinnesotaCincinnati Children’s Hospital and Medical CentreDEBRA BrazilOrthopaedic Surgery and Developmental Biology, Cincinnati Children’s HospitalAbstract What is already known about this topic? Epidermolysis bullosa (EB) causes blistering and scarring of the hands resulting in contractures fused web spaces and altered function. Surgery is needed to release contractures and web spaces and hand therapy is essential to maintain results, approaches for both differ. What does this study add? These guidelines aim to provide information on the surgical and conservative therapeutic hand management of children and adults diagnosed with EB. They are based on available evidence and expert consensus to assist hand surgeons and therapists in decision making, planning and treatment. They highlight the importance of a holistic multidisciplinary team (MDT) approach, where patient priorities are paramount.https://doi.org/10.1186/s13023-022-02282-0 |
| spellingShingle | Rachel Box Catina Bernardis Alexander Pleshkov Nicky Jessop Catherine Miller Jennifer Skye Virginia O’Brien Matthew Veerkamp Anna Carolina Ferreira da Rocha Roger Cornwall Hand surgery and hand therapy clinical practice guideline for epidermolysis bullosa Orphanet Journal of Rare Diseases |
| title | Hand surgery and hand therapy clinical practice guideline for epidermolysis bullosa |
| title_full | Hand surgery and hand therapy clinical practice guideline for epidermolysis bullosa |
| title_fullStr | Hand surgery and hand therapy clinical practice guideline for epidermolysis bullosa |
| title_full_unstemmed | Hand surgery and hand therapy clinical practice guideline for epidermolysis bullosa |
| title_short | Hand surgery and hand therapy clinical practice guideline for epidermolysis bullosa |
| title_sort | hand surgery and hand therapy clinical practice guideline for epidermolysis bullosa |
| url | https://doi.org/10.1186/s13023-022-02282-0 |
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