Pulmonary artery perforation due to off-label stent

This is the case of 13-year-old teenage girl diagnosed with pulmonary atresia with intact ventricular septum treated in the neonatal period with valvulotomy with radiofrequency and percutaneous pulmonary valvuloplasty. Since then, the patient has developed severe pulmonary regurgitation and moderate...

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Main Authors: Alejandro Rasines-Rodríguez, César Abelleira Pardeiro, Enrique José Balbacid Domingo
Format: Article
Language:English
Published: Permanyer 2023-02-01
Series:REC: Interventional Cardiology (English Ed.)
Online Access:https://recintervcardiol.org/en/index.php?option=com_content&view=article&id=915
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author Alejandro Rasines-Rodríguez
César Abelleira Pardeiro
Enrique José Balbacid Domingo
author_facet Alejandro Rasines-Rodríguez
César Abelleira Pardeiro
Enrique José Balbacid Domingo
author_sort Alejandro Rasines-Rodríguez
collection DOAJ
description This is the case of 13-year-old teenage girl diagnosed with pulmonary atresia with intact ventricular septum treated in the neonatal period with valvulotomy with radiofrequency and percutaneous pulmonary valvuloplasty. Since then, the patient has developed severe pulmonary regurgitation and moderate tricuspid regurgitation. Valve implantation into the right ventricular outflow tract (RVOT) is decided due to worsening functional class with restrictive behavior of the right ventricle (without anticipated dilatation), and hepatic congestion. Cardiac catheterization reveals the presence of a dilated and pulsatile (pulmonary annulus: 29 mm) RVOT with supravalvular stenosis (minimum diameter: 21 mm), and a 34 mm post-stenotic dilatation (figure 1). A second-staged stent is implanted for percutaneous valve implantation. Given the absence of specific material for RVOTs so dilated, a 30 mm x 40 mm self-expandable Sinus-XL stent (Optimed, Germany) (off-label) is selected for being long enough, easy to implant, having enough navigability for the patient’s age (10-Fr sheath), and requiring less radial strength (favorable for dilated RVOTs). Figure 1. A 14-Fr sheath was used to perform position angiographies (figure 1). A few hours later, the patient showed hemodynamic instability with transthoracic echocardiography findings compatible with cardiac tamponade. An emergency computed tomography scan (figure 2) confirmed the perforation of the pulmonary...
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spelling doaj.art-5aacb815416349a4a2653583ebd89f172023-02-07T15:20:38ZengPermanyerREC: Interventional Cardiology (English Ed.)2604-73222023-02-0151878810.24875/RECICE.M22000316Pulmonary artery perforation due to off-label stentAlejandro Rasines-Rodríguez0César Abelleira Pardeiro1Enrique José Balbacid Domingo2Servicio de Cardiología Infantil, Sección de Hemodinámica Infantil, Hospital Universitario La Paz, Madrid, SpainServicio de Cardiología Infantil, Sección de Hemodinámica Infantil, Hospital Universitario La Paz, Madrid, SpainServicio de Cardiología Infantil, Sección de Hemodinámica Infantil, Hospital Universitario La Paz, Madrid, SpainThis is the case of 13-year-old teenage girl diagnosed with pulmonary atresia with intact ventricular septum treated in the neonatal period with valvulotomy with radiofrequency and percutaneous pulmonary valvuloplasty. Since then, the patient has developed severe pulmonary regurgitation and moderate tricuspid regurgitation. Valve implantation into the right ventricular outflow tract (RVOT) is decided due to worsening functional class with restrictive behavior of the right ventricle (without anticipated dilatation), and hepatic congestion. Cardiac catheterization reveals the presence of a dilated and pulsatile (pulmonary annulus: 29 mm) RVOT with supravalvular stenosis (minimum diameter: 21 mm), and a 34 mm post-stenotic dilatation (figure 1). A second-staged stent is implanted for percutaneous valve implantation. Given the absence of specific material for RVOTs so dilated, a 30 mm x 40 mm self-expandable Sinus-XL stent (Optimed, Germany) (off-label) is selected for being long enough, easy to implant, having enough navigability for the patient’s age (10-Fr sheath), and requiring less radial strength (favorable for dilated RVOTs). Figure 1. A 14-Fr sheath was used to perform position angiographies (figure 1). A few hours later, the patient showed hemodynamic instability with transthoracic echocardiography findings compatible with cardiac tamponade. An emergency computed tomography scan (figure 2) confirmed the perforation of the pulmonary...https://recintervcardiol.org/en/index.php?option=com_content&view=article&id=915
spellingShingle Alejandro Rasines-Rodríguez
César Abelleira Pardeiro
Enrique José Balbacid Domingo
Pulmonary artery perforation due to off-label stent
REC: Interventional Cardiology (English Ed.)
title Pulmonary artery perforation due to off-label stent
title_full Pulmonary artery perforation due to off-label stent
title_fullStr Pulmonary artery perforation due to off-label stent
title_full_unstemmed Pulmonary artery perforation due to off-label stent
title_short Pulmonary artery perforation due to off-label stent
title_sort pulmonary artery perforation due to off label stent
url https://recintervcardiol.org/en/index.php?option=com_content&view=article&id=915
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AT cesarabelleirapardeiro pulmonaryarteryperforationduetoofflabelstent
AT enriquejosebalbaciddomingo pulmonaryarteryperforationduetoofflabelstent