Anesthetic management of a parturient with tuberous sclerosis for emergency cesarean section- a case report
Abstract Background Tuberous sclerosis is an autosomal dominant neurocutaneous disorder characterized by hamartoma formation in various organ systems leading to highly variable clinical presentation. These patients pose a challenge to anesthesiologists due to multisystem involvement. Case presentati...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
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SpringerOpen
2023-06-01
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| Series: | Ain Shams Journal of Anesthesiology |
| Subjects: | |
| Online Access: | https://doi.org/10.1186/s42077-023-00336-4 |
| _version_ | 1797811957848342528 |
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| author | Nitu Yadav Amit Kumar Vandna Arora Pragya Sharma Rashmi Arora Suresh K. Singhal |
| author_facet | Nitu Yadav Amit Kumar Vandna Arora Pragya Sharma Rashmi Arora Suresh K. Singhal |
| author_sort | Nitu Yadav |
| collection | DOAJ |
| description | Abstract Background Tuberous sclerosis is an autosomal dominant neurocutaneous disorder characterized by hamartoma formation in various organ systems leading to highly variable clinical presentation. These patients pose a challenge to anesthesiologists due to multisystem involvement. Case presentation Herein, we report the successful anesthetic management of a 25-year-old parturient with tuberous sclerosis who underwent an emergency cesarean section in view of cephalopelvic disproportion. She had a seizure disorder, bilateral renal angiomyolipomas, angiofibroma over the cheeks, periungual fibroma on the right toe, and nodular lesions near the base of the tongue and oropharynx. We opted for regional anesthesia to avoid airway instrumentation, drug interaction, and renal insult. Conclusions Anesthetic management of tuberous sclerosis depends upon the extent and severity of the involvement of various organs. Careful assessment, thorough evaluation, and preoperative planning are crucial for dealing with the difficulties and complications encountered during the management of these cases. |
| first_indexed | 2024-03-13T07:30:27Z |
| format | Article |
| id | doaj.art-5ae08ddc692e4b95b6c5405bb2295952 |
| institution | Directory Open Access Journal |
| issn | 2090-925X |
| language | English |
| last_indexed | 2024-03-13T07:30:27Z |
| publishDate | 2023-06-01 |
| publisher | SpringerOpen |
| record_format | Article |
| series | Ain Shams Journal of Anesthesiology |
| spelling | doaj.art-5ae08ddc692e4b95b6c5405bb22959522023-06-04T11:06:58ZengSpringerOpenAin Shams Journal of Anesthesiology2090-925X2023-06-011511410.1186/s42077-023-00336-4Anesthetic management of a parturient with tuberous sclerosis for emergency cesarean section- a case reportNitu Yadav0Amit Kumar1Vandna Arora2Pragya Sharma3Rashmi Arora4Suresh K. Singhal5Department of Anaesthesiology, Pt. B.D. Sharma PGIMSDepartment of Anaesthesiology, Pt. B.D. Sharma PGIMSDepartment of Anaesthesiology, Pt. B.D. Sharma PGIMSDepartment of Anaesthesiology, Pt. B.D. Sharma PGIMSDepartment of Anaesthesiology, Pt. B.D. Sharma PGIMSDepartment of Anaesthesiology, Pt. B.D. Sharma PGIMSAbstract Background Tuberous sclerosis is an autosomal dominant neurocutaneous disorder characterized by hamartoma formation in various organ systems leading to highly variable clinical presentation. These patients pose a challenge to anesthesiologists due to multisystem involvement. Case presentation Herein, we report the successful anesthetic management of a 25-year-old parturient with tuberous sclerosis who underwent an emergency cesarean section in view of cephalopelvic disproportion. She had a seizure disorder, bilateral renal angiomyolipomas, angiofibroma over the cheeks, periungual fibroma on the right toe, and nodular lesions near the base of the tongue and oropharynx. We opted for regional anesthesia to avoid airway instrumentation, drug interaction, and renal insult. Conclusions Anesthetic management of tuberous sclerosis depends upon the extent and severity of the involvement of various organs. Careful assessment, thorough evaluation, and preoperative planning are crucial for dealing with the difficulties and complications encountered during the management of these cases.https://doi.org/10.1186/s42077-023-00336-4Tuberous sclerosisRegional anesthesiaPregnancySeizure disorderHamartoma formationAngiomyolipomas |
| spellingShingle | Nitu Yadav Amit Kumar Vandna Arora Pragya Sharma Rashmi Arora Suresh K. Singhal Anesthetic management of a parturient with tuberous sclerosis for emergency cesarean section- a case report Ain Shams Journal of Anesthesiology Tuberous sclerosis Regional anesthesia Pregnancy Seizure disorder Hamartoma formation Angiomyolipomas |
| title | Anesthetic management of a parturient with tuberous sclerosis for emergency cesarean section- a case report |
| title_full | Anesthetic management of a parturient with tuberous sclerosis for emergency cesarean section- a case report |
| title_fullStr | Anesthetic management of a parturient with tuberous sclerosis for emergency cesarean section- a case report |
| title_full_unstemmed | Anesthetic management of a parturient with tuberous sclerosis for emergency cesarean section- a case report |
| title_short | Anesthetic management of a parturient with tuberous sclerosis for emergency cesarean section- a case report |
| title_sort | anesthetic management of a parturient with tuberous sclerosis for emergency cesarean section a case report |
| topic | Tuberous sclerosis Regional anesthesia Pregnancy Seizure disorder Hamartoma formation Angiomyolipomas |
| url | https://doi.org/10.1186/s42077-023-00336-4 |
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