Fibrocartilaginous dysplasia: What do we know so far?
Fibrocartilaginous dysplasia has been described as a rare variant of fibrous dysplasia. This lesion will appear in imaging as ground glass matrix similar to fibrous dysplasia, but it will also show rings and arcs calcifications. In turn, this can lead to misdiagnosing fibrocartilaginous dysplasia as...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Elsevier
2023-05-01
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| Series: | Radiology Case Reports |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S1930043323000754 |
| _version_ | 1827975254814752768 |
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| author | Asma Alshalan, MD Yasser Asiri, MD Ayed AlGarni, MD Bader Tayara, MD |
| author_facet | Asma Alshalan, MD Yasser Asiri, MD Ayed AlGarni, MD Bader Tayara, MD |
| author_sort | Asma Alshalan, MD |
| collection | DOAJ |
| description | Fibrocartilaginous dysplasia has been described as a rare variant of fibrous dysplasia. This lesion will appear in imaging as ground glass matrix similar to fibrous dysplasia, but it will also show rings and arcs calcifications. In turn, this can lead to misdiagnosing fibrocartilaginous dysplasia as primary cartilaginous lesion such as enchondroma or chondrosarcoma, neccesating histopathological confirmation. We report a case of fibrocartilaginous dysplasia in a 19 years old male with polyostotic fibrous dysplasia with prior pathologic fracture of the left femur. The patient presented with progressive swelling of the left thigh, imaging was done and showed enlargement of the fibrous dysplasia in the left femur with new rings and arcs matrix mineralization. The lesion was biopsied and microscopic evaluation revealed mainly cartilage islands with fibro-osseous tissue. We also discuss the possible origin of the cartilaginous component in this lesion, and its clinical course. |
| first_indexed | 2024-04-09T20:08:39Z |
| format | Article |
| id | doaj.art-5b6e84c6e78446daac0f43294d7c0f66 |
| institution | Directory Open Access Journal |
| issn | 1930-0433 |
| language | English |
| last_indexed | 2024-04-09T20:08:39Z |
| publishDate | 2023-05-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Radiology Case Reports |
| spelling | doaj.art-5b6e84c6e78446daac0f43294d7c0f662023-04-01T08:46:08ZengElsevierRadiology Case Reports1930-04332023-05-0118517631766Fibrocartilaginous dysplasia: What do we know so far?Asma Alshalan, MD0Yasser Asiri, MD1Ayed AlGarni, MD2Bader Tayara, MD3Department of Radiology, King Fahad Specialist Hospital, Ammar Bin Thabit St.. Al Merikbat, Dammam 32253, Saudi Arabia; Corresponding author.Department of Radiology, King Fahad Specialist Hospital, Ammar Bin Thabit St.. Al Merikbat, Dammam 32253, Saudi ArabiaDepartment of Pathology, King Fahad Specialist Hospital, Dammam, Saudi ArabiaDepartment of Orthopedic Surgery, King Fahad Specialist Hospital, Dammam, Saudi ArabiaFibrocartilaginous dysplasia has been described as a rare variant of fibrous dysplasia. This lesion will appear in imaging as ground glass matrix similar to fibrous dysplasia, but it will also show rings and arcs calcifications. In turn, this can lead to misdiagnosing fibrocartilaginous dysplasia as primary cartilaginous lesion such as enchondroma or chondrosarcoma, neccesating histopathological confirmation. We report a case of fibrocartilaginous dysplasia in a 19 years old male with polyostotic fibrous dysplasia with prior pathologic fracture of the left femur. The patient presented with progressive swelling of the left thigh, imaging was done and showed enlargement of the fibrous dysplasia in the left femur with new rings and arcs matrix mineralization. The lesion was biopsied and microscopic evaluation revealed mainly cartilage islands with fibro-osseous tissue. We also discuss the possible origin of the cartilaginous component in this lesion, and its clinical course.http://www.sciencedirect.com/science/article/pii/S1930043323000754Fibrocartilaginous dysplasiaFibrous dysplasia with cartilaginous differentiationFibrous dysplasia |
| spellingShingle | Asma Alshalan, MD Yasser Asiri, MD Ayed AlGarni, MD Bader Tayara, MD Fibrocartilaginous dysplasia: What do we know so far? Radiology Case Reports Fibrocartilaginous dysplasia Fibrous dysplasia with cartilaginous differentiation Fibrous dysplasia |
| title | Fibrocartilaginous dysplasia: What do we know so far? |
| title_full | Fibrocartilaginous dysplasia: What do we know so far? |
| title_fullStr | Fibrocartilaginous dysplasia: What do we know so far? |
| title_full_unstemmed | Fibrocartilaginous dysplasia: What do we know so far? |
| title_short | Fibrocartilaginous dysplasia: What do we know so far? |
| title_sort | fibrocartilaginous dysplasia what do we know so far |
| topic | Fibrocartilaginous dysplasia Fibrous dysplasia with cartilaginous differentiation Fibrous dysplasia |
| url | http://www.sciencedirect.com/science/article/pii/S1930043323000754 |
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