Primary immunodeficiency in adults: total variable immune deficiency clinical manifestations, immunological and genetic defects, treatment

The most prevalent form of primary immunodeficiency with a total defect of antibody production in adults is common variable immunodeficiency (CVID). Compared to other forms of primary immunodeficiency, CVID is characterized by later onset of clinical manifestations represented by infectious, autoimm...

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Main Authors: Aleksandr Viktorovich Karaulov, Irina Valentinovna Sidorenko, Vladimir Vladimirovich Androsov, Anna Sergeevna Kapustina, A V Karaulov, I V Sidorenko, V V Androsov, A S Kapustina
Format: Article
Language:Russian
Published: "Consilium Medicum" Publishing house 2011-10-01
Series:Терапевтический архив
Subjects:
Online Access:https://ter-arkhiv.ru/0040-3660/article/view/30936
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author Aleksandr Viktorovich Karaulov
Irina Valentinovna Sidorenko
Vladimir Vladimirovich Androsov
Anna Sergeevna Kapustina
A V Karaulov
I V Sidorenko
V V Androsov
A S Kapustina
author_facet Aleksandr Viktorovich Karaulov
Irina Valentinovna Sidorenko
Vladimir Vladimirovich Androsov
Anna Sergeevna Kapustina
A V Karaulov
I V Sidorenko
V V Androsov
A S Kapustina
author_sort Aleksandr Viktorovich Karaulov
collection DOAJ
description The most prevalent form of primary immunodeficiency with a total defect of antibody production in adults is common variable immunodeficiency (CVID). Compared to other forms of primary immunodeficiency, CVID is characterized by later onset of clinical manifestations represented by infectious, autoimmune and malignant diseases. To avoid development of complications and patient incapacitating, it is necessary to make an early diagnosis and initiate regular replacement therapy with intravenous immunoglobulins.
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spelling doaj.art-5c06b678b7fa43168934b8836ec8de452022-12-22T03:47:15Zrus"Consilium Medicum" Publishing houseТерапевтический архив0040-36602309-53422011-10-018310495427952Primary immunodeficiency in adults: total variable immune deficiency clinical manifestations, immunological and genetic defects, treatmentAleksandr Viktorovich KaraulovIrina Valentinovna SidorenkoVladimir Vladimirovich AndrosovAnna Sergeevna KapustinaA V Karaulov0I V Sidorenko1V V Androsov2A S Kapustina3I.M. Sechenov First Moscow State Medical UniversityI.M. Sechenov First Moscow State Medical UniversityCity hospital N 7, MoscowI.M. Sechenov First Moscow State Medical UniversityThe most prevalent form of primary immunodeficiency with a total defect of antibody production in adults is common variable immunodeficiency (CVID). Compared to other forms of primary immunodeficiency, CVID is characterized by later onset of clinical manifestations represented by infectious, autoimmune and malignant diseases. To avoid development of complications and patient incapacitating, it is necessary to make an early diagnosis and initiate regular replacement therapy with intravenous immunoglobulins.https://ter-arkhiv.ru/0040-3660/article/view/30936primary immunodeficiencycommon variable immunodeficiencyintravenous immunoglobulins
spellingShingle Aleksandr Viktorovich Karaulov
Irina Valentinovna Sidorenko
Vladimir Vladimirovich Androsov
Anna Sergeevna Kapustina
A V Karaulov
I V Sidorenko
V V Androsov
A S Kapustina
Primary immunodeficiency in adults: total variable immune deficiency clinical manifestations, immunological and genetic defects, treatment
Терапевтический архив
primary immunodeficiency
common variable immunodeficiency
intravenous immunoglobulins
title Primary immunodeficiency in adults: total variable immune deficiency clinical manifestations, immunological and genetic defects, treatment
title_full Primary immunodeficiency in adults: total variable immune deficiency clinical manifestations, immunological and genetic defects, treatment
title_fullStr Primary immunodeficiency in adults: total variable immune deficiency clinical manifestations, immunological and genetic defects, treatment
title_full_unstemmed Primary immunodeficiency in adults: total variable immune deficiency clinical manifestations, immunological and genetic defects, treatment
title_short Primary immunodeficiency in adults: total variable immune deficiency clinical manifestations, immunological and genetic defects, treatment
title_sort primary immunodeficiency in adults total variable immune deficiency clinical manifestations immunological and genetic defects treatment
topic primary immunodeficiency
common variable immunodeficiency
intravenous immunoglobulins
url https://ter-arkhiv.ru/0040-3660/article/view/30936
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