Primary immunodeficiency in adults: total variable immune deficiency clinical manifestations, immunological and genetic defects, treatment
The most prevalent form of primary immunodeficiency with a total defect of antibody production in adults is common variable immunodeficiency (CVID). Compared to other forms of primary immunodeficiency, CVID is characterized by later onset of clinical manifestations represented by infectious, autoimm...
Main Authors: | , , , , , , , |
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Format: | Article |
Language: | Russian |
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"Consilium Medicum" Publishing house
2011-10-01
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Series: | Терапевтический архив |
Subjects: | |
Online Access: | https://ter-arkhiv.ru/0040-3660/article/view/30936 |
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author | Aleksandr Viktorovich Karaulov Irina Valentinovna Sidorenko Vladimir Vladimirovich Androsov Anna Sergeevna Kapustina A V Karaulov I V Sidorenko V V Androsov A S Kapustina |
author_facet | Aleksandr Viktorovich Karaulov Irina Valentinovna Sidorenko Vladimir Vladimirovich Androsov Anna Sergeevna Kapustina A V Karaulov I V Sidorenko V V Androsov A S Kapustina |
author_sort | Aleksandr Viktorovich Karaulov |
collection | DOAJ |
description | The most prevalent form of primary immunodeficiency with a total defect of antibody production in adults is common variable immunodeficiency (CVID). Compared to other forms of primary immunodeficiency, CVID is characterized by later onset of clinical manifestations represented by infectious, autoimmune and malignant diseases. To avoid development of complications and patient incapacitating, it is necessary to make an early diagnosis and initiate regular replacement therapy with intravenous immunoglobulins. |
first_indexed | 2024-04-12T04:52:25Z |
format | Article |
id | doaj.art-5c06b678b7fa43168934b8836ec8de45 |
institution | Directory Open Access Journal |
issn | 0040-3660 2309-5342 |
language | Russian |
last_indexed | 2024-04-12T04:52:25Z |
publishDate | 2011-10-01 |
publisher | "Consilium Medicum" Publishing house |
record_format | Article |
series | Терапевтический архив |
spelling | doaj.art-5c06b678b7fa43168934b8836ec8de452022-12-22T03:47:15Zrus"Consilium Medicum" Publishing houseТерапевтический архив0040-36602309-53422011-10-018310495427952Primary immunodeficiency in adults: total variable immune deficiency clinical manifestations, immunological and genetic defects, treatmentAleksandr Viktorovich KaraulovIrina Valentinovna SidorenkoVladimir Vladimirovich AndrosovAnna Sergeevna KapustinaA V Karaulov0I V Sidorenko1V V Androsov2A S Kapustina3I.M. Sechenov First Moscow State Medical UniversityI.M. Sechenov First Moscow State Medical UniversityCity hospital N 7, MoscowI.M. Sechenov First Moscow State Medical UniversityThe most prevalent form of primary immunodeficiency with a total defect of antibody production in adults is common variable immunodeficiency (CVID). Compared to other forms of primary immunodeficiency, CVID is characterized by later onset of clinical manifestations represented by infectious, autoimmune and malignant diseases. To avoid development of complications and patient incapacitating, it is necessary to make an early diagnosis and initiate regular replacement therapy with intravenous immunoglobulins.https://ter-arkhiv.ru/0040-3660/article/view/30936primary immunodeficiencycommon variable immunodeficiencyintravenous immunoglobulins |
spellingShingle | Aleksandr Viktorovich Karaulov Irina Valentinovna Sidorenko Vladimir Vladimirovich Androsov Anna Sergeevna Kapustina A V Karaulov I V Sidorenko V V Androsov A S Kapustina Primary immunodeficiency in adults: total variable immune deficiency clinical manifestations, immunological and genetic defects, treatment Терапевтический архив primary immunodeficiency common variable immunodeficiency intravenous immunoglobulins |
title | Primary immunodeficiency in adults: total variable immune deficiency clinical manifestations, immunological and genetic defects, treatment |
title_full | Primary immunodeficiency in adults: total variable immune deficiency clinical manifestations, immunological and genetic defects, treatment |
title_fullStr | Primary immunodeficiency in adults: total variable immune deficiency clinical manifestations, immunological and genetic defects, treatment |
title_full_unstemmed | Primary immunodeficiency in adults: total variable immune deficiency clinical manifestations, immunological and genetic defects, treatment |
title_short | Primary immunodeficiency in adults: total variable immune deficiency clinical manifestations, immunological and genetic defects, treatment |
title_sort | primary immunodeficiency in adults total variable immune deficiency clinical manifestations immunological and genetic defects treatment |
topic | primary immunodeficiency common variable immunodeficiency intravenous immunoglobulins |
url | https://ter-arkhiv.ru/0040-3660/article/view/30936 |
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