Modified Hybrid Procedure in Hypoplastic Left Heart Syndrome: Initial Experience of a Center in Northeastern Brazil

Abstract Introduction: Although it only corresponds to 2.5% of congenital heart defects, hypoplastic left heart syndrome (HLHS) is responsible for more than 25% of cardiac deaths in the first week of life. Palliative surgery performed after the second week of life is considered an important risk fa...

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Main Authors: Renato Max Faria, Juliana Torres Pacheco, Itamar Ribeiro de Oliveira, José Madson Vidal, Anilton Bezerra Rodrigues Junior, Ana Luiza Lafeta Costa, Vinicius José da Silva Nina, Marcelo Matos Cascudo
Format: Article
Language:English
Published: Sociedade Brasileira de Cirurgia Cardiovascular
Series:Brazilian Journal of Cardiovascular Surgery
Subjects:
Online Access:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0102-76382017000300210&lng=en&tlng=en
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author Renato Max Faria
Juliana Torres Pacheco
Itamar Ribeiro de Oliveira
José Madson Vidal
Anilton Bezerra Rodrigues Junior
Ana Luiza Lafeta Costa
Vinicius José da Silva Nina
Marcelo Matos Cascudo
author_facet Renato Max Faria
Juliana Torres Pacheco
Itamar Ribeiro de Oliveira
José Madson Vidal
Anilton Bezerra Rodrigues Junior
Ana Luiza Lafeta Costa
Vinicius José da Silva Nina
Marcelo Matos Cascudo
author_sort Renato Max Faria
collection DOAJ
description Abstract Introduction: Although it only corresponds to 2.5% of congenital heart defects, hypoplastic left heart syndrome (HLHS) is responsible for more than 25% of cardiac deaths in the first week of life. Palliative surgery performed after the second week of life is considered an important risk factor in the treatment of HLHS. Objective: The aim of this study is to describe the initial experience of a medical center in Northeastern Brazil with a modified off-pump hybrid approach for palliation of HLHS. Methods: From November 2012 through November 2015, the medical records of 8 patients with HLHS undergoing hybrid procedure were retrospectively evaluated in a tertiary private hospital in Northeastern Brazil. The modified off-pump hybrid palliation consisted of stenting of the ductus arteriosus guided by fluoroscopy without contrast and banding of the main pulmonary artery branches. Demographic and clinical variables were recorded for descriptive analysis. Results: Eight patients were included in this study, of whom 37.5% were female. The median age and weight at the time of the procedure was 2 days (p25% and p75% = 2 and 4.5 days, respectively) and 3150 g (p25% and p75% = 3077.5 g and 3400 g, respectively), respectively. The median length in intensive care unit stay was 6 days (p25% and p75% = 3.5% and 8 days, respectively). There were no in-hospital deaths. Four patients have undergone to the second stage of the surgical treatment of HLHS. Conclusion: In this series, the initial experience with the modified off-pump hybrid procedure showed to be safe, allowing a low early mortality rate among children presenting HLHS.
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spelling doaj.art-5cf0f0931a14472583d134103b75d73d2022-12-22T00:26:48ZengSociedade Brasileira de Cirurgia CardiovascularBrazilian Journal of Cardiovascular Surgery1678-974132321021410.21470/1678-9741-2017-0058S0102-76382017000300210Modified Hybrid Procedure in Hypoplastic Left Heart Syndrome: Initial Experience of a Center in Northeastern BrazilRenato Max FariaJuliana Torres PachecoItamar Ribeiro de OliveiraJosé Madson VidalAnilton Bezerra Rodrigues JuniorAna Luiza Lafeta CostaVinicius José da Silva NinaMarcelo Matos CascudoAbstract Introduction: Although it only corresponds to 2.5% of congenital heart defects, hypoplastic left heart syndrome (HLHS) is responsible for more than 25% of cardiac deaths in the first week of life. Palliative surgery performed after the second week of life is considered an important risk factor in the treatment of HLHS. Objective: The aim of this study is to describe the initial experience of a medical center in Northeastern Brazil with a modified off-pump hybrid approach for palliation of HLHS. Methods: From November 2012 through November 2015, the medical records of 8 patients with HLHS undergoing hybrid procedure were retrospectively evaluated in a tertiary private hospital in Northeastern Brazil. The modified off-pump hybrid palliation consisted of stenting of the ductus arteriosus guided by fluoroscopy without contrast and banding of the main pulmonary artery branches. Demographic and clinical variables were recorded for descriptive analysis. Results: Eight patients were included in this study, of whom 37.5% were female. The median age and weight at the time of the procedure was 2 days (p25% and p75% = 2 and 4.5 days, respectively) and 3150 g (p25% and p75% = 3077.5 g and 3400 g, respectively), respectively. The median length in intensive care unit stay was 6 days (p25% and p75% = 3.5% and 8 days, respectively). There were no in-hospital deaths. Four patients have undergone to the second stage of the surgical treatment of HLHS. Conclusion: In this series, the initial experience with the modified off-pump hybrid procedure showed to be safe, allowing a low early mortality rate among children presenting HLHS.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0102-76382017000300210&lng=en&tlng=enHypoplastic Left Heart SyndromeCongenital AbnormalitiesBandagesAngioplastyContrast Media
spellingShingle Renato Max Faria
Juliana Torres Pacheco
Itamar Ribeiro de Oliveira
José Madson Vidal
Anilton Bezerra Rodrigues Junior
Ana Luiza Lafeta Costa
Vinicius José da Silva Nina
Marcelo Matos Cascudo
Modified Hybrid Procedure in Hypoplastic Left Heart Syndrome: Initial Experience of a Center in Northeastern Brazil
Brazilian Journal of Cardiovascular Surgery
Hypoplastic Left Heart Syndrome
Congenital Abnormalities
Bandages
Angioplasty
Contrast Media
title Modified Hybrid Procedure in Hypoplastic Left Heart Syndrome: Initial Experience of a Center in Northeastern Brazil
title_full Modified Hybrid Procedure in Hypoplastic Left Heart Syndrome: Initial Experience of a Center in Northeastern Brazil
title_fullStr Modified Hybrid Procedure in Hypoplastic Left Heart Syndrome: Initial Experience of a Center in Northeastern Brazil
title_full_unstemmed Modified Hybrid Procedure in Hypoplastic Left Heart Syndrome: Initial Experience of a Center in Northeastern Brazil
title_short Modified Hybrid Procedure in Hypoplastic Left Heart Syndrome: Initial Experience of a Center in Northeastern Brazil
title_sort modified hybrid procedure in hypoplastic left heart syndrome initial experience of a center in northeastern brazil
topic Hypoplastic Left Heart Syndrome
Congenital Abnormalities
Bandages
Angioplasty
Contrast Media
url http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0102-76382017000300210&lng=en&tlng=en
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