Three Cases of Pierre Robin Sequence with Upper Airway Obstruction Relieved by Nasopharyngeal Airway Insertion
Pierre Robin sequence (PRS), also called Robin sequence, is a congenital anomaly characterized by a triad of micrognathia, glossoptosis, and upper airway obstruction. Infants with PRS can present with varying degrees of respiratory difficulty secondary to upper airway obstruction. There has been no...
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| Format: | Article |
| Language: | English |
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Korean Society of Neonatology
2019-08-01
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| Series: | Neonatal Medicine |
| Subjects: | |
| Online Access: | http://www.neo-med.org/upload/pdf/nm-2019-26-3-179.pdf |
| _version_ | 1819277303940644864 |
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| author | Min-su Oh Yu-Mi Park Young Hwa Jung Chang Won Choi Beyong Il Kim Ji-Won Kwon |
| author_facet | Min-su Oh Yu-Mi Park Young Hwa Jung Chang Won Choi Beyong Il Kim Ji-Won Kwon |
| author_sort | Min-su Oh |
| collection | DOAJ |
| description | Pierre Robin sequence (PRS), also called Robin sequence, is a congenital anomaly characterized by a triad of micrognathia, glossoptosis, and upper airway obstruction. Infants with PRS can present with varying degrees of respiratory difficulty secondary to upper airway obstruction. There has been no consensus for the treatment of upper airway obstruction in infants with PRS, but recent studies recommend attempting non-surgical interventions before surgical treatment. In this case report, we present 3 cases of infants diagnosed with PRS who showed persistent respiratory difficulties after birth. Before considering surgical intervention, insertion of a nasopharyngeal airway was attempted in these infants. Following this procedure, symptoms of upper airway obstruction were relieved, and all infants were discharged without surgical interventions; the nasopharyngeal airway was removed 1 to 2 months later. To date, no infant has shown signs of upper airway obstruction. Nasopharyngeal airway insertion is a highly effective and less invasive treatment option for infants with PRS. However, it is not widely known and used in Korea. Nasopharyngeal airway insertion can be preferentially considered before surgical intervention for upper airway obstruction in such infants. |
| first_indexed | 2024-12-23T23:53:59Z |
| format | Article |
| id | doaj.art-5f83961e03644d43a37b76bd09f00b20 |
| institution | Directory Open Access Journal |
| issn | 2287-9412 2287-9803 |
| language | English |
| last_indexed | 2024-12-23T23:53:59Z |
| publishDate | 2019-08-01 |
| publisher | Korean Society of Neonatology |
| record_format | Article |
| series | Neonatal Medicine |
| spelling | doaj.art-5f83961e03644d43a37b76bd09f00b202022-12-21T17:25:18ZengKorean Society of NeonatologyNeonatal Medicine2287-94122287-98032019-08-0126317918310.5385/nm.2019.26.3.179978Three Cases of Pierre Robin Sequence with Upper Airway Obstruction Relieved by Nasopharyngeal Airway InsertionMin-su Oh0Yu-Mi Park1Young Hwa Jung2Chang Won Choi3Beyong Il Kim4Ji-Won Kwon5 Department of Pediatrics, Jeju National University Hospital, Jeju National University College of Medicine, Jeju, Korea Department of Pediatrics, Seoul National University Bundang Hospital, Seoul National University College of Medicine, Seongnam, Korea Department of Pediatrics, Seoul National University Bundang Hospital, Seoul National University College of Medicine, Seongnam, Korea Department of Pediatrics, Seoul National University Bundang Hospital, Seoul National University College of Medicine, Seongnam, Korea Department of Pediatrics, Seoul National University Bundang Hospital, Seoul National University College of Medicine, Seongnam, Korea Department of Pediatrics, Seoul National University Bundang Hospital, Seoul National University College of Medicine, Seongnam, KoreaPierre Robin sequence (PRS), also called Robin sequence, is a congenital anomaly characterized by a triad of micrognathia, glossoptosis, and upper airway obstruction. Infants with PRS can present with varying degrees of respiratory difficulty secondary to upper airway obstruction. There has been no consensus for the treatment of upper airway obstruction in infants with PRS, but recent studies recommend attempting non-surgical interventions before surgical treatment. In this case report, we present 3 cases of infants diagnosed with PRS who showed persistent respiratory difficulties after birth. Before considering surgical intervention, insertion of a nasopharyngeal airway was attempted in these infants. Following this procedure, symptoms of upper airway obstruction were relieved, and all infants were discharged without surgical interventions; the nasopharyngeal airway was removed 1 to 2 months later. To date, no infant has shown signs of upper airway obstruction. Nasopharyngeal airway insertion is a highly effective and less invasive treatment option for infants with PRS. However, it is not widely known and used in Korea. Nasopharyngeal airway insertion can be preferentially considered before surgical intervention for upper airway obstruction in such infants.http://www.neo-med.org/upload/pdf/nm-2019-26-3-179.pdfpierre robin syndromeupper airway obstructionnasopharyngeal airway |
| spellingShingle | Min-su Oh Yu-Mi Park Young Hwa Jung Chang Won Choi Beyong Il Kim Ji-Won Kwon Three Cases of Pierre Robin Sequence with Upper Airway Obstruction Relieved by Nasopharyngeal Airway Insertion Neonatal Medicine pierre robin syndrome upper airway obstruction nasopharyngeal airway |
| title | Three Cases of Pierre Robin Sequence with Upper Airway Obstruction Relieved by Nasopharyngeal Airway Insertion |
| title_full | Three Cases of Pierre Robin Sequence with Upper Airway Obstruction Relieved by Nasopharyngeal Airway Insertion |
| title_fullStr | Three Cases of Pierre Robin Sequence with Upper Airway Obstruction Relieved by Nasopharyngeal Airway Insertion |
| title_full_unstemmed | Three Cases of Pierre Robin Sequence with Upper Airway Obstruction Relieved by Nasopharyngeal Airway Insertion |
| title_short | Three Cases of Pierre Robin Sequence with Upper Airway Obstruction Relieved by Nasopharyngeal Airway Insertion |
| title_sort | three cases of pierre robin sequence with upper airway obstruction relieved by nasopharyngeal airway insertion |
| topic | pierre robin syndrome upper airway obstruction nasopharyngeal airway |
| url | http://www.neo-med.org/upload/pdf/nm-2019-26-3-179.pdf |
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