Recurrent Rapenzul Syndrome in a Male Child; A Rare Surgical Entity

Rapunzel syndrome is a rare entity when the undigested tuft of hairs accumulated in the stomach and extends beyond the pylorus in the small intestine with a presentation of vomiting, pain in epigastrium and a palpable mass. Recurrence of this pathology is extremely rare, and upto now, only six cases...

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Bibliographic Details
Main Authors: Nand Lal Kella, Mumtaz Ahmed Qureshi, Imtiaz Ahmed Qureshi
Format: Article
Language:English
Published: Liaquat University of Medical and Health Sciences 2018-06-01
Series:JLUMHS
Subjects:
Online Access:https://www.lumhs.edu.pk/jlumhs/Vol17No02/pdfs/09.pdf
Description
Summary:Rapunzel syndrome is a rare entity when the undigested tuft of hairs accumulated in the stomach and extends beyond the pylorus in the small intestine with a presentation of vomiting, pain in epigastrium and a palpable mass. Recurrence of this pathology is extremely rare, and upto now, only six cases have been reported. We report a male who was partially deaf and dumb, presented with trichophagia and trichobezoar in the age of 5 and 9 years. Both times gastrostomy was performed and trichobezoars were removed completely which were extending in the small intestine. Post-operative recovery was un-eventful and the patient has been referred to the psychiatrist for further management.
ISSN:1729-0341
2309-8627