Recurrent Rapenzul Syndrome in a Male Child; A Rare Surgical Entity

Rapunzel syndrome is a rare entity when the undigested tuft of hairs accumulated in the stomach and extends beyond the pylorus in the small intestine with a presentation of vomiting, pain in epigastrium and a palpable mass. Recurrence of this pathology is extremely rare, and upto now, only six cases...

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Main Authors: Nand Lal Kella, Mumtaz Ahmed Qureshi, Imtiaz Ahmed Qureshi
Format: Article
Language:English
Published: Liaquat University of Medical and Health Sciences 2018-06-01
Series:JLUMHS
Subjects:
Online Access:https://www.lumhs.edu.pk/jlumhs/Vol17No02/pdfs/09.pdf
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author Nand Lal Kella
Mumtaz Ahmed Qureshi
Imtiaz Ahmed Qureshi
author_facet Nand Lal Kella
Mumtaz Ahmed Qureshi
Imtiaz Ahmed Qureshi
author_sort Nand Lal Kella
collection DOAJ
description Rapunzel syndrome is a rare entity when the undigested tuft of hairs accumulated in the stomach and extends beyond the pylorus in the small intestine with a presentation of vomiting, pain in epigastrium and a palpable mass. Recurrence of this pathology is extremely rare, and upto now, only six cases have been reported. We report a male who was partially deaf and dumb, presented with trichophagia and trichobezoar in the age of 5 and 9 years. Both times gastrostomy was performed and trichobezoars were removed completely which were extending in the small intestine. Post-operative recovery was un-eventful and the patient has been referred to the psychiatrist for further management.
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spelling doaj.art-6026e8a3ba85430e84e1eb27763193a82023-05-30T09:44:52ZengLiaquat University of Medical and Health SciencesJLUMHS1729-03412309-86272018-06-01170210610810.22442/jlumhs.181720560Recurrent Rapenzul Syndrome in a Male Child; A Rare Surgical EntityNand Lal Kella 0Mumtaz Ahmed Qureshi1Imtiaz Ahmed Qureshi2Liaquat University of Medical & Health Sciences (LUMHS), Jamshoro, Sindh-PakistanLiaquat University of Medical & Health Sciences (LUMHS), Jamshoro, Sindh-PakistanLiaquat University of Medical & Health Sciences (LUMHS), Jamshoro, Sindh-PakistanRapunzel syndrome is a rare entity when the undigested tuft of hairs accumulated in the stomach and extends beyond the pylorus in the small intestine with a presentation of vomiting, pain in epigastrium and a palpable mass. Recurrence of this pathology is extremely rare, and upto now, only six cases have been reported. We report a male who was partially deaf and dumb, presented with trichophagia and trichobezoar in the age of 5 and 9 years. Both times gastrostomy was performed and trichobezoars were removed completely which were extending in the small intestine. Post-operative recovery was un-eventful and the patient has been referred to the psychiatrist for further management.https://www.lumhs.edu.pk/jlumhs/Vol17No02/pdfs/09.pdftrichobezoarpsychiatricrapunzel syndromemale child
spellingShingle Nand Lal Kella
Mumtaz Ahmed Qureshi
Imtiaz Ahmed Qureshi
Recurrent Rapenzul Syndrome in a Male Child; A Rare Surgical Entity
JLUMHS
trichobezoar
psychiatric
rapunzel syndrome
male child
title Recurrent Rapenzul Syndrome in a Male Child; A Rare Surgical Entity
title_full Recurrent Rapenzul Syndrome in a Male Child; A Rare Surgical Entity
title_fullStr Recurrent Rapenzul Syndrome in a Male Child; A Rare Surgical Entity
title_full_unstemmed Recurrent Rapenzul Syndrome in a Male Child; A Rare Surgical Entity
title_short Recurrent Rapenzul Syndrome in a Male Child; A Rare Surgical Entity
title_sort recurrent rapenzul syndrome in a male child a rare surgical entity
topic trichobezoar
psychiatric
rapunzel syndrome
male child
url https://www.lumhs.edu.pk/jlumhs/Vol17No02/pdfs/09.pdf
work_keys_str_mv AT nandlalkella recurrentrapenzulsyndromeinamalechildararesurgicalentity
AT mumtazahmedqureshi recurrentrapenzulsyndromeinamalechildararesurgicalentity
AT imtiazahmedqureshi recurrentrapenzulsyndromeinamalechildararesurgicalentity