Giant nevus unius lateralis: Two cases

Verrucous epidermal nevus is a common type of keratinocyte hamartoma present at birth or occurring later in life. Widespread multiple epidermal nevi (EN) may reflect genetic or chromosomal mosaicism. Blaschko has documented characteristic linear, zosteriform, unilateral or systematized patterns with...

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Main Authors: Ajay Govindrao Ovhal, Shruthi Vasanth Kumar Deshkulakarani, Viraj Jitendra Sadrani
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2017-01-01
Series:Indian Journal of Paediatric Dermatology
Subjects:
Online Access:http://www.ijpd.in/article.asp?issn=2319-7250;year=2017;volume=18;issue=4;spage=310;epage=313;aulast=Ovhal
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author Ajay Govindrao Ovhal
Shruthi Vasanth Kumar Deshkulakarani
Viraj Jitendra Sadrani
author_facet Ajay Govindrao Ovhal
Shruthi Vasanth Kumar Deshkulakarani
Viraj Jitendra Sadrani
author_sort Ajay Govindrao Ovhal
collection DOAJ
description Verrucous epidermal nevus is a common type of keratinocyte hamartoma present at birth or occurring later in life. Widespread multiple epidermal nevi (EN) may reflect genetic or chromosomal mosaicism. Blaschko has documented characteristic linear, zosteriform, unilateral or systematized patterns with streaks and swirls. They are resistant to treatment with the risk of recurrence. Giant congenital nevus unius lateralis (NUL) is known for its benign course with good supportive treatment however one particular case had a fatal neonatal outcome due to associated complications. Two interesting rare cases will be reviewed here.
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spelling doaj.art-61acbb07e138484e8560272f0af438e52022-12-22T03:43:10ZengWolters Kluwer Medknow PublicationsIndian Journal of Paediatric Dermatology2319-72502017-01-0118431031310.4103/ijpd.IJPD_64_17Giant nevus unius lateralis: Two casesAjay Govindrao OvhalShruthi Vasanth Kumar DeshkulakaraniViraj Jitendra SadraniVerrucous epidermal nevus is a common type of keratinocyte hamartoma present at birth or occurring later in life. Widespread multiple epidermal nevi (EN) may reflect genetic or chromosomal mosaicism. Blaschko has documented characteristic linear, zosteriform, unilateral or systematized patterns with streaks and swirls. They are resistant to treatment with the risk of recurrence. Giant congenital nevus unius lateralis (NUL) is known for its benign course with good supportive treatment however one particular case had a fatal neonatal outcome due to associated complications. Two interesting rare cases will be reviewed here.http://www.ijpd.in/article.asp?issn=2319-7250;year=2017;volume=18;issue=4;spage=310;epage=313;aulast=OvhalBlaschko's linesdisembryoplasiaepidermal nevusnevus unius lateralis
spellingShingle Ajay Govindrao Ovhal
Shruthi Vasanth Kumar Deshkulakarani
Viraj Jitendra Sadrani
Giant nevus unius lateralis: Two cases
Indian Journal of Paediatric Dermatology
Blaschko's lines
disembryoplasia
epidermal nevus
nevus unius lateralis
title Giant nevus unius lateralis: Two cases
title_full Giant nevus unius lateralis: Two cases
title_fullStr Giant nevus unius lateralis: Two cases
title_full_unstemmed Giant nevus unius lateralis: Two cases
title_short Giant nevus unius lateralis: Two cases
title_sort giant nevus unius lateralis two cases
topic Blaschko's lines
disembryoplasia
epidermal nevus
nevus unius lateralis
url http://www.ijpd.in/article.asp?issn=2319-7250;year=2017;volume=18;issue=4;spage=310;epage=313;aulast=Ovhal
work_keys_str_mv AT ajaygovindraoovhal giantnevusuniuslateralistwocases
AT shruthivasanthkumardeshkulakarani giantnevusuniuslateralistwocases
AT virajjitendrasadrani giantnevusuniuslateralistwocases