Giant nevus unius lateralis: Two cases
Verrucous epidermal nevus is a common type of keratinocyte hamartoma present at birth or occurring later in life. Widespread multiple epidermal nevi (EN) may reflect genetic or chromosomal mosaicism. Blaschko has documented characteristic linear, zosteriform, unilateral or systematized patterns with...
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Format: | Article |
Language: | English |
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Wolters Kluwer Medknow Publications
2017-01-01
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Series: | Indian Journal of Paediatric Dermatology |
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Online Access: | http://www.ijpd.in/article.asp?issn=2319-7250;year=2017;volume=18;issue=4;spage=310;epage=313;aulast=Ovhal |
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author | Ajay Govindrao Ovhal Shruthi Vasanth Kumar Deshkulakarani Viraj Jitendra Sadrani |
author_facet | Ajay Govindrao Ovhal Shruthi Vasanth Kumar Deshkulakarani Viraj Jitendra Sadrani |
author_sort | Ajay Govindrao Ovhal |
collection | DOAJ |
description | Verrucous epidermal nevus is a common type of keratinocyte hamartoma present at birth or occurring later in life. Widespread multiple epidermal nevi (EN) may reflect genetic or chromosomal mosaicism. Blaschko has documented characteristic linear, zosteriform, unilateral or systematized patterns with streaks and swirls. They are resistant to treatment with the risk of recurrence. Giant congenital nevus unius lateralis (NUL) is known for its benign course with good supportive treatment however one particular case had a fatal neonatal outcome due to associated complications. Two interesting rare cases will be reviewed here. |
first_indexed | 2024-04-12T06:55:59Z |
format | Article |
id | doaj.art-61acbb07e138484e8560272f0af438e5 |
institution | Directory Open Access Journal |
issn | 2319-7250 |
language | English |
last_indexed | 2024-04-12T06:55:59Z |
publishDate | 2017-01-01 |
publisher | Wolters Kluwer Medknow Publications |
record_format | Article |
series | Indian Journal of Paediatric Dermatology |
spelling | doaj.art-61acbb07e138484e8560272f0af438e52022-12-22T03:43:10ZengWolters Kluwer Medknow PublicationsIndian Journal of Paediatric Dermatology2319-72502017-01-0118431031310.4103/ijpd.IJPD_64_17Giant nevus unius lateralis: Two casesAjay Govindrao OvhalShruthi Vasanth Kumar DeshkulakaraniViraj Jitendra SadraniVerrucous epidermal nevus is a common type of keratinocyte hamartoma present at birth or occurring later in life. Widespread multiple epidermal nevi (EN) may reflect genetic or chromosomal mosaicism. Blaschko has documented characteristic linear, zosteriform, unilateral or systematized patterns with streaks and swirls. They are resistant to treatment with the risk of recurrence. Giant congenital nevus unius lateralis (NUL) is known for its benign course with good supportive treatment however one particular case had a fatal neonatal outcome due to associated complications. Two interesting rare cases will be reviewed here.http://www.ijpd.in/article.asp?issn=2319-7250;year=2017;volume=18;issue=4;spage=310;epage=313;aulast=OvhalBlaschko's linesdisembryoplasiaepidermal nevusnevus unius lateralis |
spellingShingle | Ajay Govindrao Ovhal Shruthi Vasanth Kumar Deshkulakarani Viraj Jitendra Sadrani Giant nevus unius lateralis: Two cases Indian Journal of Paediatric Dermatology Blaschko's lines disembryoplasia epidermal nevus nevus unius lateralis |
title | Giant nevus unius lateralis: Two cases |
title_full | Giant nevus unius lateralis: Two cases |
title_fullStr | Giant nevus unius lateralis: Two cases |
title_full_unstemmed | Giant nevus unius lateralis: Two cases |
title_short | Giant nevus unius lateralis: Two cases |
title_sort | giant nevus unius lateralis two cases |
topic | Blaschko's lines disembryoplasia epidermal nevus nevus unius lateralis |
url | http://www.ijpd.in/article.asp?issn=2319-7250;year=2017;volume=18;issue=4;spage=310;epage=313;aulast=Ovhal |
work_keys_str_mv | AT ajaygovindraoovhal giantnevusuniuslateralistwocases AT shruthivasanthkumardeshkulakarani giantnevusuniuslateralistwocases AT virajjitendrasadrani giantnevusuniuslateralistwocases |