A Case of Prune Belly Syndrome
Prune belly syndrome (PBS) is a rare congenital disorder characterized by deficient abdominal wall muscles, urinary tract malformation, and, in males, cryptorchidism. We present a case of PBS in China. The patient was a newborn baby boy who had wrinkled, “prune-like” abdominal skin, bilateral crypto...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Elsevier
2015-06-01
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| Series: | Pediatrics and Neonatology |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S1875957213000661 |
| _version_ | 1817992367799533568 |
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| author | Wei Xu Hui Wu Dong-Xuan Wang Zhi-Hong Mu |
| author_facet | Wei Xu Hui Wu Dong-Xuan Wang Zhi-Hong Mu |
| author_sort | Wei Xu |
| collection | DOAJ |
| description | Prune belly syndrome (PBS) is a rare congenital disorder characterized by deficient abdominal wall muscles, urinary tract malformation, and, in males, cryptorchidism. We present a case of PBS in China. The patient was a newborn baby boy who had wrinkled, “prune-like” abdominal skin, bilateral cryptorchidism, and urinary system malformation, complicated with hypoplasia of the lung and branch of the coronary artery–right ventricular fistula. His kidney function was inadequate. The patient subsequently died at age 28 days due to septicemia from a severe urinary tract infection. |
| first_indexed | 2024-04-14T01:25:29Z |
| format | Article |
| id | doaj.art-61b0103ee7524da286fa867ad70cf70e |
| institution | Directory Open Access Journal |
| issn | 1875-9572 |
| language | English |
| last_indexed | 2024-04-14T01:25:29Z |
| publishDate | 2015-06-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Pediatrics and Neonatology |
| spelling | doaj.art-61b0103ee7524da286fa867ad70cf70e2022-12-22T02:20:27ZengElsevierPediatrics and Neonatology1875-95722015-06-0156319319610.1016/j.pedneo.2013.03.014A Case of Prune Belly SyndromeWei Xu0Hui Wu1Dong-Xuan Wang2Zhi-Hong Mu3Department of Neonatology, The First Hospital of Jilin University, Changchun 130021, People's Republic of ChinaDepartment of Neonatology, The First Hospital of Jilin University, Changchun 130021, People's Republic of ChinaDepartment of Ultrasonic Diagnosis, The First Hospital of Jilin University, Changchun 130021, People's Republic of ChinaDepartment of Neonatology, The First Hospital of Jilin University, Changchun 130021, People's Republic of ChinaPrune belly syndrome (PBS) is a rare congenital disorder characterized by deficient abdominal wall muscles, urinary tract malformation, and, in males, cryptorchidism. We present a case of PBS in China. The patient was a newborn baby boy who had wrinkled, “prune-like” abdominal skin, bilateral cryptorchidism, and urinary system malformation, complicated with hypoplasia of the lung and branch of the coronary artery–right ventricular fistula. His kidney function was inadequate. The patient subsequently died at age 28 days due to septicemia from a severe urinary tract infection.http://www.sciencedirect.com/science/article/pii/S1875957213000661abdominal wall musculature deficiencybilateral cryptorchidismprune belly syndromeurinary tract anomalies |
| spellingShingle | Wei Xu Hui Wu Dong-Xuan Wang Zhi-Hong Mu A Case of Prune Belly Syndrome Pediatrics and Neonatology abdominal wall musculature deficiency bilateral cryptorchidism prune belly syndrome urinary tract anomalies |
| title | A Case of Prune Belly Syndrome |
| title_full | A Case of Prune Belly Syndrome |
| title_fullStr | A Case of Prune Belly Syndrome |
| title_full_unstemmed | A Case of Prune Belly Syndrome |
| title_short | A Case of Prune Belly Syndrome |
| title_sort | case of prune belly syndrome |
| topic | abdominal wall musculature deficiency bilateral cryptorchidism prune belly syndrome urinary tract anomalies |
| url | http://www.sciencedirect.com/science/article/pii/S1875957213000661 |
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