A case of successful coronary angioplasty in an achondroplasia patient with total occlusion of an anomalous right coronary artery (case report)
Abstract Background Coronary interventions in patients of achondroplasia have been reported rarely in the medical literature. Due to short stature and kyphoscoliosis, endovascular access (Cannulation) of the coronary arteries is usually extremely difficult in such patients. Case presentation A 33 ye...
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| Format: | Article |
| Language: | English |
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BMC
2020-07-01
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| Series: | BMC Cardiovascular Disorders |
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| Online Access: | http://link.springer.com/article/10.1186/s12872-020-01612-z |
| _version_ | 1828314864015114240 |
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| author | Mustafa Ibrahiem Mohammed Ali Ahmed Abdalazim Dafallah Albashir Omer Ali Mohamed Ahmed Elawad Makram Aboali Ebied Mohamed |
| author_facet | Mustafa Ibrahiem Mohammed Ali Ahmed Abdalazim Dafallah Albashir Omer Ali Mohamed Ahmed Elawad Makram Aboali Ebied Mohamed |
| author_sort | Mustafa Ibrahiem Mohammed Ali |
| collection | DOAJ |
| description | Abstract Background Coronary interventions in patients of achondroplasia have been reported rarely in the medical literature. Due to short stature and kyphoscoliosis, endovascular access (Cannulation) of the coronary arteries is usually extremely difficult in such patients. Case presentation A 33 years old patient, a known case of achondroplasia, presented with epigastric pain for 3 h duration to a university hospital, Sudan. Her height was 95 cm and her weight was 38 Kg. A trans-femoral approach for coronary angioplasty was preferred. After it has been extremely difficult to cannulate the left system at first, the cannulation has been performed successfully using 5F, JL3.5 catheter. The angiogram depicted total occlusion of the proximal right coronary artery which was found to be originating from the left coronary sinus of the aorta. Successful trans-femoral coronary angioplasty has been performed with stent placement, and no complications encountered. During her last follow up, 1 year after the procedure, she appeared to be free of symptoms and with no further ischemic attacks or procedure-related complications. Conclusions To the best of our knowledge, this is the first reported case of successful coronary angioplasty in achondroplasia patient in whom the occluded artery is an anomalous coronary artery. Literature review, description of the achondroplasia, development of the coronary arteries and the hypothesized theory for the anomaly have been described in this case report. The PCI performed has also been clearly and comprehensively described. |
| first_indexed | 2024-04-13T16:51:12Z |
| format | Article |
| id | doaj.art-635f948945c241c09441b3ee542a99b6 |
| institution | Directory Open Access Journal |
| issn | 1471-2261 |
| language | English |
| last_indexed | 2024-04-13T16:51:12Z |
| publishDate | 2020-07-01 |
| publisher | BMC |
| record_format | Article |
| series | BMC Cardiovascular Disorders |
| spelling | doaj.art-635f948945c241c09441b3ee542a99b62022-12-22T02:38:56ZengBMCBMC Cardiovascular Disorders1471-22612020-07-012011710.1186/s12872-020-01612-zA case of successful coronary angioplasty in an achondroplasia patient with total occlusion of an anomalous right coronary artery (case report)Mustafa Ibrahiem Mohammed Ali0Ahmed Abdalazim Dafallah Albashir1Omer Ali Mohamed Ahmed Elawad2Makram Aboali Ebied Mohamed3Department of Internal Medicine, Faculty of Medicine, University of GeziraTeaching assistant, Faculty of Medicine, University of GeziraResident, Wad Medani Heart CentreResident, Wad Medani Heart CentreAbstract Background Coronary interventions in patients of achondroplasia have been reported rarely in the medical literature. Due to short stature and kyphoscoliosis, endovascular access (Cannulation) of the coronary arteries is usually extremely difficult in such patients. Case presentation A 33 years old patient, a known case of achondroplasia, presented with epigastric pain for 3 h duration to a university hospital, Sudan. Her height was 95 cm and her weight was 38 Kg. A trans-femoral approach for coronary angioplasty was preferred. After it has been extremely difficult to cannulate the left system at first, the cannulation has been performed successfully using 5F, JL3.5 catheter. The angiogram depicted total occlusion of the proximal right coronary artery which was found to be originating from the left coronary sinus of the aorta. Successful trans-femoral coronary angioplasty has been performed with stent placement, and no complications encountered. During her last follow up, 1 year after the procedure, she appeared to be free of symptoms and with no further ischemic attacks or procedure-related complications. Conclusions To the best of our knowledge, this is the first reported case of successful coronary angioplasty in achondroplasia patient in whom the occluded artery is an anomalous coronary artery. Literature review, description of the achondroplasia, development of the coronary arteries and the hypothesized theory for the anomaly have been described in this case report. The PCI performed has also been clearly and comprehensively described.http://link.springer.com/article/10.1186/s12872-020-01612-zAchondroplasiaPercutaneous coronary interventionCoronary arteriesAnomalies |
| spellingShingle | Mustafa Ibrahiem Mohammed Ali Ahmed Abdalazim Dafallah Albashir Omer Ali Mohamed Ahmed Elawad Makram Aboali Ebied Mohamed A case of successful coronary angioplasty in an achondroplasia patient with total occlusion of an anomalous right coronary artery (case report) BMC Cardiovascular Disorders Achondroplasia Percutaneous coronary intervention Coronary arteries Anomalies |
| title | A case of successful coronary angioplasty in an achondroplasia patient with total occlusion of an anomalous right coronary artery (case report) |
| title_full | A case of successful coronary angioplasty in an achondroplasia patient with total occlusion of an anomalous right coronary artery (case report) |
| title_fullStr | A case of successful coronary angioplasty in an achondroplasia patient with total occlusion of an anomalous right coronary artery (case report) |
| title_full_unstemmed | A case of successful coronary angioplasty in an achondroplasia patient with total occlusion of an anomalous right coronary artery (case report) |
| title_short | A case of successful coronary angioplasty in an achondroplasia patient with total occlusion of an anomalous right coronary artery (case report) |
| title_sort | case of successful coronary angioplasty in an achondroplasia patient with total occlusion of an anomalous right coronary artery case report |
| topic | Achondroplasia Percutaneous coronary intervention Coronary arteries Anomalies |
| url | http://link.springer.com/article/10.1186/s12872-020-01612-z |
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