Level of independence, functional capacity and respiratory muscle strength of patients with mucopolysaccharidosis type VI in the Northeast of Brazil
Abstract Objectives: to assess the functional independence, functional capacity and respiratory muscle strength (RMS) in individuals with mucopolysaccharidosis (MPS) type VI. Methods: in this cross-sectional study, the Pediatric Evaluation of Disability Inventory (PEDI) and the Functional Independ...
Main Authors: | Bárbara Bernardo Rinaldo da Silva Figueirêdo, Paulo André Freire Magalhães, Liívia Barbosa de Andrade, Patrícia Bezerra, Maria do Carmo Menezes Bezerra Duarte |
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Format: | Article |
Language: | English |
Published: |
Instituto Materno Infantil de Pernambuco
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Series: | Revista Brasileira de Saúde Materno Infantil |
Subjects: | |
Online Access: | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1519-38292018000100083&lng=en&tlng=en |
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