Anaesthetic management of a patient with Eisenmenger syndrome and β-thalassemia major for splenectomy
We describe for the first time, the perioperative care of a patient with a rare combination of Eisenmenger syndrome with β-thalassemia major presenting for splenectomy. Patients with Eisenmenger syndrome have polycythemia because of chronic hypoxia but our patient was anaemic and had thrombocytopeni...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Wolters Kluwer Medknow Publications
2011-01-01
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| Series: | Indian Journal of Anaesthesia |
| Subjects: | |
| Online Access: | http://www.ijaweb.org/article.asp?issn=0019-5049;year=2011;volume=55;issue=2;spage=187;epage=189;aulast=Gupta |
| _version_ | 1818845907715620864 |
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| author | Nishkarsh Gupta Sarbjot Kaur Ajay Goila Mridula Pawar |
| author_facet | Nishkarsh Gupta Sarbjot Kaur Ajay Goila Mridula Pawar |
| author_sort | Nishkarsh Gupta |
| collection | DOAJ |
| description | We describe for the first time, the perioperative care of a patient with a rare combination of Eisenmenger syndrome with β-thalassemia major presenting for splenectomy. Patients with Eisenmenger syndrome have polycythemia because of chronic hypoxia but our patient was anaemic and had thrombocytopenia because of thalassemia major. The management of such a case can be challenging for any anaesthesiologist because of severe V/Q mismatch (high shunt fraction and restrictive lung disease because of hypersplenism), decreased oxygen carrying capacity (anaemia) and increased risk of haemorrhage (thrombocytopenia), along with the potential increase in intracardiac shunt during anaesthesia. |
| first_indexed | 2024-12-19T05:37:07Z |
| format | Article |
| id | doaj.art-64e3b2a7dff84c5093d9d261d05ab510 |
| institution | Directory Open Access Journal |
| issn | 0019-5049 |
| language | English |
| last_indexed | 2024-12-19T05:37:07Z |
| publishDate | 2011-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Indian Journal of Anaesthesia |
| spelling | doaj.art-64e3b2a7dff84c5093d9d261d05ab5102022-12-21T20:34:07ZengWolters Kluwer Medknow PublicationsIndian Journal of Anaesthesia0019-50492011-01-0155218718910.4103/0019-5049.79892Anaesthetic management of a patient with Eisenmenger syndrome and β-thalassemia major for splenectomyNishkarsh GuptaSarbjot KaurAjay GoilaMridula PawarWe describe for the first time, the perioperative care of a patient with a rare combination of Eisenmenger syndrome with β-thalassemia major presenting for splenectomy. Patients with Eisenmenger syndrome have polycythemia because of chronic hypoxia but our patient was anaemic and had thrombocytopenia because of thalassemia major. The management of such a case can be challenging for any anaesthesiologist because of severe V/Q mismatch (high shunt fraction and restrictive lung disease because of hypersplenism), decreased oxygen carrying capacity (anaemia) and increased risk of haemorrhage (thrombocytopenia), along with the potential increase in intracardiac shunt during anaesthesia.http://www.ijaweb.org/article.asp?issn=0019-5049;year=2011;volume=55;issue=2;spage=187;epage=189;aulast=GuptaEisenmenger syndromesplenectomyβ-thalassemia major |
| spellingShingle | Nishkarsh Gupta Sarbjot Kaur Ajay Goila Mridula Pawar Anaesthetic management of a patient with Eisenmenger syndrome and β-thalassemia major for splenectomy Indian Journal of Anaesthesia Eisenmenger syndrome splenectomy β-thalassemia major |
| title | Anaesthetic management of a patient with Eisenmenger syndrome and β-thalassemia major for splenectomy |
| title_full | Anaesthetic management of a patient with Eisenmenger syndrome and β-thalassemia major for splenectomy |
| title_fullStr | Anaesthetic management of a patient with Eisenmenger syndrome and β-thalassemia major for splenectomy |
| title_full_unstemmed | Anaesthetic management of a patient with Eisenmenger syndrome and β-thalassemia major for splenectomy |
| title_short | Anaesthetic management of a patient with Eisenmenger syndrome and β-thalassemia major for splenectomy |
| title_sort | anaesthetic management of a patient with eisenmenger syndrome and β thalassemia major for splenectomy |
| topic | Eisenmenger syndrome splenectomy β-thalassemia major |
| url | http://www.ijaweb.org/article.asp?issn=0019-5049;year=2011;volume=55;issue=2;spage=187;epage=189;aulast=Gupta |
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