Pleuropulmonary blastoma in adolescence: A rare tumor beyond first decade of life
Pleuropulmonary blastoma (PPB) is a unique dysontogenetic and a primitive neoplasm occuring almost exclusively in the first decade of life, as a pulmonary- and/or pleural-based tumor with cystic, solid, or combined cystic and solid features. It is characterized histologically by a primitive, variabl...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2015-01-01
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| Series: | Lung India |
| Subjects: | |
| Online Access: | http://www.lungindia.com/article.asp?issn=0970-2113;year=2015;volume=32;issue=3;spage=281;epage=284;aulast=Yadav |
| _version_ | 1828732257600274432 |
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| author | Mukesh K Yadav Manphool Singhal Anmol Bhatia Rakesh Kapoor Nalini Gupta Niranjan Khandelwal |
| author_facet | Mukesh K Yadav Manphool Singhal Anmol Bhatia Rakesh Kapoor Nalini Gupta Niranjan Khandelwal |
| author_sort | Mukesh K Yadav |
| collection | DOAJ |
| description | Pleuropulmonary blastoma (PPB) is a unique dysontogenetic and a primitive neoplasm occuring almost exclusively in the first decade of life, as a pulmonary- and/or pleural-based tumor with cystic, solid, or combined cystic and solid features. It is characterized histologically by a primitive, variably mixed blastematous and sarcomatous tissues. These tumors are usually associated with a poor prognosis. However, with a multimodality treatment approach, the survival of the patient can be prolonged. We herein report two cases of PPB in adolescence, a rare presentation beyond first decade of life with a short review of literature. |
| first_indexed | 2024-04-12T17:58:30Z |
| format | Article |
| id | doaj.art-65cbff90a4494ca0b50690a74f41da61 |
| institution | Directory Open Access Journal |
| issn | 0970-2113 0974-598X |
| language | English |
| last_indexed | 2024-04-12T17:58:30Z |
| publishDate | 2015-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Lung India |
| spelling | doaj.art-65cbff90a4494ca0b50690a74f41da612022-12-22T03:22:15ZengWolters Kluwer Medknow PublicationsLung India0970-21130974-598X2015-01-0132328128410.4103/0970-2113.156255Pleuropulmonary blastoma in adolescence: A rare tumor beyond first decade of lifeMukesh K YadavManphool SinghalAnmol BhatiaRakesh KapoorNalini GuptaNiranjan KhandelwalPleuropulmonary blastoma (PPB) is a unique dysontogenetic and a primitive neoplasm occuring almost exclusively in the first decade of life, as a pulmonary- and/or pleural-based tumor with cystic, solid, or combined cystic and solid features. It is characterized histologically by a primitive, variably mixed blastematous and sarcomatous tissues. These tumors are usually associated with a poor prognosis. However, with a multimodality treatment approach, the survival of the patient can be prolonged. We herein report two cases of PPB in adolescence, a rare presentation beyond first decade of life with a short review of literature.http://www.lungindia.com/article.asp?issn=0970-2113;year=2015;volume=32;issue=3;spage=281;epage=284;aulast=YadavAdolescenceblastomapleuropulmonaryprimitive |
| spellingShingle | Mukesh K Yadav Manphool Singhal Anmol Bhatia Rakesh Kapoor Nalini Gupta Niranjan Khandelwal Pleuropulmonary blastoma in adolescence: A rare tumor beyond first decade of life Lung India Adolescence blastoma pleuropulmonary primitive |
| title | Pleuropulmonary blastoma in adolescence: A rare tumor beyond first decade of life |
| title_full | Pleuropulmonary blastoma in adolescence: A rare tumor beyond first decade of life |
| title_fullStr | Pleuropulmonary blastoma in adolescence: A rare tumor beyond first decade of life |
| title_full_unstemmed | Pleuropulmonary blastoma in adolescence: A rare tumor beyond first decade of life |
| title_short | Pleuropulmonary blastoma in adolescence: A rare tumor beyond first decade of life |
| title_sort | pleuropulmonary blastoma in adolescence a rare tumor beyond first decade of life |
| topic | Adolescence blastoma pleuropulmonary primitive |
| url | http://www.lungindia.com/article.asp?issn=0970-2113;year=2015;volume=32;issue=3;spage=281;epage=284;aulast=Yadav |
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