Bilateral Implantation of Scleral-Fixated Cionni Endocapsular Rings and Toric Intraocular Lenses in a Pediatric Patient with Marfan’s Syndrome
The management of ectopia lentis in Marfan’s syndrome is challenging. Multiple disease-associated factors conspire to deprive these patients of adequate vision. While optical correction with glasses and contact lenses is usually advocated early on, the irregular astigmatism and even partial aphakia...
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| Format: | Article |
| Language: | English |
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Karger Publishers
2012-01-01
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| Series: | Case Reports in Ophthalmology |
| Subjects: | |
| Online Access: | http://www.karger.com/Article/FullText/335652 |
| _version_ | 1811331463250968576 |
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| author | Howard V. Gimbel Gerardo D. Camoriano Muhammad Aman-Ullah |
| author_facet | Howard V. Gimbel Gerardo D. Camoriano Muhammad Aman-Ullah |
| author_sort | Howard V. Gimbel |
| collection | DOAJ |
| description | The management of ectopia lentis in Marfan’s syndrome is challenging. Multiple disease-associated factors conspire to deprive these patients of adequate vision. While optical correction with glasses and contact lenses is usually advocated early on, the irregular astigmatism and even partial aphakia that accompanies advanced cases generally warrant surgical intervention. Several surgical strategies have been devised to manage these challenging cases, including the combination of endocapsular or pars plana lensectomy and iris or scleral fixation of the intraocular lens (IOL) or IOL-bag complex. All of the reported cases have been implanted with IOLs that correct for myopia only. With toric lenses, it is now possible to correct for corneal astigmatism in these patients as well, provided that the capsular bag is maintained and can be properly centered. We report the combination of scleral-fixated Cionni endocapsular rings and toric IOLs in a pediatric patient with bilateral ectopia lentis secondary to Marfan’s syndrome. |
| first_indexed | 2024-04-13T16:20:45Z |
| format | Article |
| id | doaj.art-67887331a19d46b49d2024a5385dd301 |
| institution | Directory Open Access Journal |
| issn | 1663-2699 |
| language | English |
| last_indexed | 2024-04-13T16:20:45Z |
| publishDate | 2012-01-01 |
| publisher | Karger Publishers |
| record_format | Article |
| series | Case Reports in Ophthalmology |
| spelling | doaj.art-67887331a19d46b49d2024a5385dd3012022-12-22T02:39:56ZengKarger PublishersCase Reports in Ophthalmology1663-26992012-01-0131162310.1159/000335652335652Bilateral Implantation of Scleral-Fixated Cionni Endocapsular Rings and Toric Intraocular Lenses in a Pediatric Patient with Marfan’s SyndromeHoward V. GimbelGerardo D. CamorianoMuhammad Aman-UllahThe management of ectopia lentis in Marfan’s syndrome is challenging. Multiple disease-associated factors conspire to deprive these patients of adequate vision. While optical correction with glasses and contact lenses is usually advocated early on, the irregular astigmatism and even partial aphakia that accompanies advanced cases generally warrant surgical intervention. Several surgical strategies have been devised to manage these challenging cases, including the combination of endocapsular or pars plana lensectomy and iris or scleral fixation of the intraocular lens (IOL) or IOL-bag complex. All of the reported cases have been implanted with IOLs that correct for myopia only. With toric lenses, it is now possible to correct for corneal astigmatism in these patients as well, provided that the capsular bag is maintained and can be properly centered. We report the combination of scleral-fixated Cionni endocapsular rings and toric IOLs in a pediatric patient with bilateral ectopia lentis secondary to Marfan’s syndrome.http://www.karger.com/Article/FullText/335652Ectopia lentisMarfan’s syndromeToric intraocular lensCionni endocapsular ring |
| spellingShingle | Howard V. Gimbel Gerardo D. Camoriano Muhammad Aman-Ullah Bilateral Implantation of Scleral-Fixated Cionni Endocapsular Rings and Toric Intraocular Lenses in a Pediatric Patient with Marfan’s Syndrome Case Reports in Ophthalmology Ectopia lentis Marfan’s syndrome Toric intraocular lens Cionni endocapsular ring |
| title | Bilateral Implantation of Scleral-Fixated Cionni Endocapsular Rings and Toric Intraocular Lenses in a Pediatric Patient with Marfan’s Syndrome |
| title_full | Bilateral Implantation of Scleral-Fixated Cionni Endocapsular Rings and Toric Intraocular Lenses in a Pediatric Patient with Marfan’s Syndrome |
| title_fullStr | Bilateral Implantation of Scleral-Fixated Cionni Endocapsular Rings and Toric Intraocular Lenses in a Pediatric Patient with Marfan’s Syndrome |
| title_full_unstemmed | Bilateral Implantation of Scleral-Fixated Cionni Endocapsular Rings and Toric Intraocular Lenses in a Pediatric Patient with Marfan’s Syndrome |
| title_short | Bilateral Implantation of Scleral-Fixated Cionni Endocapsular Rings and Toric Intraocular Lenses in a Pediatric Patient with Marfan’s Syndrome |
| title_sort | bilateral implantation of scleral fixated cionni endocapsular rings and toric intraocular lenses in a pediatric patient with marfan s syndrome |
| topic | Ectopia lentis Marfan’s syndrome Toric intraocular lens Cionni endocapsular ring |
| url | http://www.karger.com/Article/FullText/335652 |
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