Congenital facial nerve palsy: Single center study

ObjectivesThis study will list the most common comorbidities of congenital facial nerve palsy and how to detect and treat them, with special attention for ENT-problems such as hearing loss. Congenital facial nerve palsy is a very rare entity but in UZ Brussels hospital there was a follow-up of 16 ch...

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Main Authors: Hermine Baelen, Anne-Marie Esschendal, Yannick De Brucker, Ina Foulon, Vedat Topsakal, Frans Gordts
Format: Article
Language:English
Published: Frontiers Media S.A. 2023-02-01
Series:Frontiers in Pediatrics
Subjects:
Online Access:https://www.frontiersin.org/articles/10.3389/fped.2023.1077238/full
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author Hermine Baelen
Hermine Baelen
Anne-Marie Esschendal
Yannick De Brucker
Ina Foulon
Ina Foulon
Vedat Topsakal
Vedat Topsakal
Frans Gordts
Frans Gordts
author_facet Hermine Baelen
Hermine Baelen
Anne-Marie Esschendal
Yannick De Brucker
Ina Foulon
Ina Foulon
Vedat Topsakal
Vedat Topsakal
Frans Gordts
Frans Gordts
author_sort Hermine Baelen
collection DOAJ
description ObjectivesThis study will list the most common comorbidities of congenital facial nerve palsy and how to detect and treat them, with special attention for ENT-problems such as hearing loss. Congenital facial nerve palsy is a very rare entity but in UZ Brussels hospital there was a follow-up of 16 children in the last 30 years.MethodsLiterature review has been done, combined with thorough research of our own series of 16 children with congenital facial nerve palsy.ResultsCongenital facial nerve palsy can be part of a known syndrome, most commonly Moebius syndrome, but can also appear solely. It appears often bilateral and with a severe gradation. In our series, hearing loss is frequently seen in association with congenital facial nerve palsy. Other abnormalities are dysfunction of the abducens nerve, ophthalmological problems, retro- or micrognathism and abnormalities of limbs or heart. The majority of the children in our series underwent radiological imaging (CT and/or MRI): the facial nerve but also the vestibulocochlear nerve and middle and inner ear can be evaluated.ConclusionA multidisciplinary approach of congenital facial nerve palsy is recommended as it can affect various bodily functions. Radiological imaging needs to be done to acquire additional information that can be useful for diagnostic and therapeutic purposes. Although congenital facial nerve palsy may not be treatable itself, its comorbidities can be treated and improve the quality of life of the affected child.
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spelling doaj.art-685d9264402e4f4e85246d597bb6daa32023-02-20T07:22:11ZengFrontiers Media S.A.Frontiers in Pediatrics2296-23602023-02-011110.3389/fped.2023.10772381077238Congenital facial nerve palsy: Single center studyHermine Baelen0Hermine Baelen1Anne-Marie Esschendal2Yannick De Brucker3Ina Foulon4Ina Foulon5Vedat Topsakal6Vedat Topsakal7Frans Gordts8Frans Gordts9Department of Otorhinolaryngology, Head and Neck Surgery University Hospital UZ Brussel, Brussels, BelgiumFaculteit Geneeskunde en Farmacie, Vrije Universiteit Brussel, Brussels, BelgiumDepartment of Otorhinolaryngology, Head and Neck Surgery University Hospital UZ Brussel, Brussels, BelgiumDepartment of Radiology, University Hospital UZ Brussel, Brussels, BelgiumDepartment of Otorhinolaryngology, Head and Neck Surgery University Hospital UZ Brussel, Brussels, BelgiumFaculteit Geneeskunde en Farmacie, Vrije Universiteit Brussel, Brussels, BelgiumDepartment of Otorhinolaryngology, Head and Neck Surgery University Hospital UZ Brussel, Brussels, BelgiumFaculteit Geneeskunde en Farmacie, Vrije Universiteit Brussel, Brussels, BelgiumDepartment of Otorhinolaryngology, Head and Neck Surgery University Hospital UZ Brussel, Brussels, BelgiumFaculteit Geneeskunde en Farmacie, Vrije Universiteit Brussel, Brussels, BelgiumObjectivesThis study will list the most common comorbidities of congenital facial nerve palsy and how to detect and treat them, with special attention for ENT-problems such as hearing loss. Congenital facial nerve palsy is a very rare entity but in UZ Brussels hospital there was a follow-up of 16 children in the last 30 years.MethodsLiterature review has been done, combined with thorough research of our own series of 16 children with congenital facial nerve palsy.ResultsCongenital facial nerve palsy can be part of a known syndrome, most commonly Moebius syndrome, but can also appear solely. It appears often bilateral and with a severe gradation. In our series, hearing loss is frequently seen in association with congenital facial nerve palsy. Other abnormalities are dysfunction of the abducens nerve, ophthalmological problems, retro- or micrognathism and abnormalities of limbs or heart. The majority of the children in our series underwent radiological imaging (CT and/or MRI): the facial nerve but also the vestibulocochlear nerve and middle and inner ear can be evaluated.ConclusionA multidisciplinary approach of congenital facial nerve palsy is recommended as it can affect various bodily functions. Radiological imaging needs to be done to acquire additional information that can be useful for diagnostic and therapeutic purposes. Although congenital facial nerve palsy may not be treatable itself, its comorbidities can be treated and improve the quality of life of the affected child.https://www.frontiersin.org/articles/10.3389/fped.2023.1077238/fullcongenital facial nerve palsyinborn facial nerve palsycongenital syndromesensorineural hearing lossimaging facial nerve
spellingShingle Hermine Baelen
Hermine Baelen
Anne-Marie Esschendal
Yannick De Brucker
Ina Foulon
Ina Foulon
Vedat Topsakal
Vedat Topsakal
Frans Gordts
Frans Gordts
Congenital facial nerve palsy: Single center study
Frontiers in Pediatrics
congenital facial nerve palsy
inborn facial nerve palsy
congenital syndrome
sensorineural hearing loss
imaging facial nerve
title Congenital facial nerve palsy: Single center study
title_full Congenital facial nerve palsy: Single center study
title_fullStr Congenital facial nerve palsy: Single center study
title_full_unstemmed Congenital facial nerve palsy: Single center study
title_short Congenital facial nerve palsy: Single center study
title_sort congenital facial nerve palsy single center study
topic congenital facial nerve palsy
inborn facial nerve palsy
congenital syndrome
sensorineural hearing loss
imaging facial nerve
url https://www.frontiersin.org/articles/10.3389/fped.2023.1077238/full
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