Flexible bronchoscopy combined with videolaryngoscope for tracheal intubation in a child with Hunter syndrome: a case report

Hunter syndrome (mucopolysaccharidosis type II) has the highest reported prevalence of difficult tracheal intubation among the seven known types of mucopolysaccharidoses. Despite improved difficult airway guidelines and equipment, conventional approaches may fail in some cases. A 10-year-old child...

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Main Authors: Faisal Shamim, Amber Gulamani, Abdullah Nisar, Saima Rashid, Humayun kaleem Siddiqui
Format: Article
Language:English
Published: Pakistan Medical Association 2023-10-01
Series:Journal of the Pakistan Medical Association
Subjects:
Online Access:https://23.88.38.159/index.php/public_html/article/view/8635
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author Faisal Shamim
Amber Gulamani
Abdullah Nisar
Saima Rashid
Humayun kaleem Siddiqui
author_facet Faisal Shamim
Amber Gulamani
Abdullah Nisar
Saima Rashid
Humayun kaleem Siddiqui
author_sort Faisal Shamim
collection DOAJ
description Hunter syndrome (mucopolysaccharidosis type II) has the highest reported prevalence of difficult tracheal intubation among the seven known types of mucopolysaccharidoses. Despite improved difficult airway guidelines and equipment, conventional approaches may fail in some cases. A 10-year-old child with Hunter syndrome, was scheduled for multiple dental extractions. On the first visit, failed intubation was declared as per Difficult Airway Society guidelines in the surgical day-care suite of our institute and the procedure was postponed. The case was then planned to be handled in the main operating room with additional preparation and input from the paediatric otolaryngologist for possible tracheostomy, paediatric intensive care for postoperative need for ventilation, and difficult airway resource faculty for an unconventional approach—videolaryngoscope combined with fibreoptic bronchoscope—which resulted in safe administration of anaesthesia. This case illustrates the importance of meticulous planning in the management of previously failed airway.
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spelling doaj.art-69234affafd6433094307b4c66e101102023-12-22T05:19:49ZengPakistan Medical AssociationJournal of the Pakistan Medical Association0030-99822023-10-01731110.47391/JPMA.8635Flexible bronchoscopy combined with videolaryngoscope for tracheal intubation in a child with Hunter syndrome: a case reportFaisal Shamim0Amber Gulamani1Abdullah Nisar2Saima Rashid3Humayun kaleem Siddiqui4Department of Anaesthesiology, Aga Khan University, Karachi, PakistanDepartment of Anaesthesiology, Aga Khan University, Karachi, PakistanDepartment of Anaesthesiology, Aga Khan University, Karachi, PakistanDepartment of Anaesthesiology, Aga Khan University, Karachi, PakistanDepartment of Surgery, Aga Khan University, Karachi, Pakistan Hunter syndrome (mucopolysaccharidosis type II) has the highest reported prevalence of difficult tracheal intubation among the seven known types of mucopolysaccharidoses. Despite improved difficult airway guidelines and equipment, conventional approaches may fail in some cases. A 10-year-old child with Hunter syndrome, was scheduled for multiple dental extractions. On the first visit, failed intubation was declared as per Difficult Airway Society guidelines in the surgical day-care suite of our institute and the procedure was postponed. The case was then planned to be handled in the main operating room with additional preparation and input from the paediatric otolaryngologist for possible tracheostomy, paediatric intensive care for postoperative need for ventilation, and difficult airway resource faculty for an unconventional approach—videolaryngoscope combined with fibreoptic bronchoscope—which resulted in safe administration of anaesthesia. This case illustrates the importance of meticulous planning in the management of previously failed airway. https://23.88.38.159/index.php/public_html/article/view/8635Mucopolysaccharidosis IIVideolaryngoscopeFibre optic bronchoscopeDifficult airwayEndotracheal intubationCase report
spellingShingle Faisal Shamim
Amber Gulamani
Abdullah Nisar
Saima Rashid
Humayun kaleem Siddiqui
Flexible bronchoscopy combined with videolaryngoscope for tracheal intubation in a child with Hunter syndrome: a case report
Journal of the Pakistan Medical Association
Mucopolysaccharidosis II
Videolaryngoscope
Fibre optic bronchoscope
Difficult airway
Endotracheal intubation
Case report
title Flexible bronchoscopy combined with videolaryngoscope for tracheal intubation in a child with Hunter syndrome: a case report
title_full Flexible bronchoscopy combined with videolaryngoscope for tracheal intubation in a child with Hunter syndrome: a case report
title_fullStr Flexible bronchoscopy combined with videolaryngoscope for tracheal intubation in a child with Hunter syndrome: a case report
title_full_unstemmed Flexible bronchoscopy combined with videolaryngoscope for tracheal intubation in a child with Hunter syndrome: a case report
title_short Flexible bronchoscopy combined with videolaryngoscope for tracheal intubation in a child with Hunter syndrome: a case report
title_sort flexible bronchoscopy combined with videolaryngoscope for tracheal intubation in a child with hunter syndrome a case report
topic Mucopolysaccharidosis II
Videolaryngoscope
Fibre optic bronchoscope
Difficult airway
Endotracheal intubation
Case report
url https://23.88.38.159/index.php/public_html/article/view/8635
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