Anaesthetic significance and management of a child with neonatal purpura fulminans
Protein C deficiency is a rare autosomal-dominant disorder of varying severity. Patients with homozygous and compound heterozygous protein C deficiency present with neonatal purpura fulminans (NPF). Other presentations usually include disseminated intravascular coagulation and venous thromboembolism...
| Main Authors: | , , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Wolters Kluwer Medknow Publications
2012-01-01
|
| Series: | Indian Journal of Anaesthesia |
| Subjects: | |
| Online Access: | http://www.ijaweb.org/article.asp?issn=0019-5049;year=2012;volume=56;issue=3;spage=283;epage=286;aulast=Tiwari |
| _version_ | 1828467467886788608 |
|---|---|
| author | Akhilesh Kumar Tiwari Gaurav Singh Tomar Swapnil Tayal Madhur Chadha Mukul Kapoor |
| author_facet | Akhilesh Kumar Tiwari Gaurav Singh Tomar Swapnil Tayal Madhur Chadha Mukul Kapoor |
| author_sort | Akhilesh Kumar Tiwari |
| collection | DOAJ |
| description | Protein C deficiency is a rare autosomal-dominant disorder of varying severity. Patients with homozygous and compound heterozygous protein C deficiency present with neonatal purpura fulminans (NPF). Other presentations usually include disseminated intravascular coagulation and venous thromboembolism. This disorder usually poses a unique anaesthetic challenge to the anaesthesiologist, requiring special precautions to prevent various intra- and post-operative complications. We hereby report the successful anaesthetic management of a 1-month-old infant who presented with NPF. |
| first_indexed | 2024-12-11T04:06:27Z |
| format | Article |
| id | doaj.art-693e7108d31f4336aa43bac9c9c09587 |
| institution | Directory Open Access Journal |
| issn | 0019-5049 |
| language | English |
| last_indexed | 2024-12-11T04:06:27Z |
| publishDate | 2012-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Indian Journal of Anaesthesia |
| spelling | doaj.art-693e7108d31f4336aa43bac9c9c095872022-12-22T01:21:30ZengWolters Kluwer Medknow PublicationsIndian Journal of Anaesthesia0019-50492012-01-0156328328610.4103/0019-5049.98778Anaesthetic significance and management of a child with neonatal purpura fulminansAkhilesh Kumar TiwariGaurav Singh TomarSwapnil TayalMadhur ChadhaMukul KapoorProtein C deficiency is a rare autosomal-dominant disorder of varying severity. Patients with homozygous and compound heterozygous protein C deficiency present with neonatal purpura fulminans (NPF). Other presentations usually include disseminated intravascular coagulation and venous thromboembolism. This disorder usually poses a unique anaesthetic challenge to the anaesthesiologist, requiring special precautions to prevent various intra- and post-operative complications. We hereby report the successful anaesthetic management of a 1-month-old infant who presented with NPF.http://www.ijaweb.org/article.asp?issn=0019-5049;year=2012;volume=56;issue=3;spage=283;epage=286;aulast=TiwariAnaesthesiadisseminated intravascular coagulationneonatal purpura fulminansprotein C |
| spellingShingle | Akhilesh Kumar Tiwari Gaurav Singh Tomar Swapnil Tayal Madhur Chadha Mukul Kapoor Anaesthetic significance and management of a child with neonatal purpura fulminans Indian Journal of Anaesthesia Anaesthesia disseminated intravascular coagulation neonatal purpura fulminans protein C |
| title | Anaesthetic significance and management of a child with neonatal purpura fulminans |
| title_full | Anaesthetic significance and management of a child with neonatal purpura fulminans |
| title_fullStr | Anaesthetic significance and management of a child with neonatal purpura fulminans |
| title_full_unstemmed | Anaesthetic significance and management of a child with neonatal purpura fulminans |
| title_short | Anaesthetic significance and management of a child with neonatal purpura fulminans |
| title_sort | anaesthetic significance and management of a child with neonatal purpura fulminans |
| topic | Anaesthesia disseminated intravascular coagulation neonatal purpura fulminans protein C |
| url | http://www.ijaweb.org/article.asp?issn=0019-5049;year=2012;volume=56;issue=3;spage=283;epage=286;aulast=Tiwari |
| work_keys_str_mv | AT akhileshkumartiwari anaestheticsignificanceandmanagementofachildwithneonatalpurpurafulminans AT gauravsinghtomar anaestheticsignificanceandmanagementofachildwithneonatalpurpurafulminans AT swapniltayal anaestheticsignificanceandmanagementofachildwithneonatalpurpurafulminans AT madhurchadha anaestheticsignificanceandmanagementofachildwithneonatalpurpurafulminans AT mukulkapoor anaestheticsignificanceandmanagementofachildwithneonatalpurpurafulminans |