Lupus miliaris disseminatus faciei
Abstract: Lupus miliaris disseminatus faciei is a rare inflammatory dermatosis of unknown etiology that primarily affects young adults. Clinically, it is characterized by an asymptomatic papular eruption mainly involving the central face, typically on and around the eyelids. Characteristic histopath...
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Format: | Article |
Language: | English |
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Sociedade Brasileira de Dermatologia
2017-12-01
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Series: | Anais Brasileiros de Dermatologia |
Subjects: | |
Online Access: | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962017000600851&tlng=en |
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author | Helena Toda-Brito João Manuel Pires Aranha Ermelindo Silva Tavares |
author_facet | Helena Toda-Brito João Manuel Pires Aranha Ermelindo Silva Tavares |
author_sort | Helena Toda-Brito |
collection | DOAJ |
description | Abstract: Lupus miliaris disseminatus faciei is a rare inflammatory dermatosis of unknown etiology that primarily affects young adults. Clinically, it is characterized by an asymptomatic papular eruption mainly involving the central face, typically on and around the eyelids. Characteristic histopathological features include dermal epithelioid cell granulomas with central necrosis and surrounding lymphocytic infiltrate with multinucleate giant cells. Lupus miliaris disseminatus faciei has a spontaneously resolving course, yet can be cosmetically debilitating given the location and potential for scarring. Treatment is difficult and there is a lack of controlled studies. We report a new case of lupus miliaris disseminatus faciei successfully treated with minocycline and systemic steroids, and briefly discuss its nosology and therapeutic options. |
first_indexed | 2024-12-23T19:03:49Z |
format | Article |
id | doaj.art-6b14d7d26de34ba590c73ab8daf1184a |
institution | Directory Open Access Journal |
issn | 0365-0596 |
language | English |
last_indexed | 2024-12-23T19:03:49Z |
publishDate | 2017-12-01 |
publisher | Sociedade Brasileira de Dermatologia |
record_format | Article |
series | Anais Brasileiros de Dermatologia |
spelling | doaj.art-6b14d7d26de34ba590c73ab8daf1184a2022-12-21T17:34:39ZengSociedade Brasileira de DermatologiaAnais Brasileiros de Dermatologia0365-05962017-12-0192685185310.1590/abd1806-4841.20174534Lupus miliaris disseminatus facieiHelena Toda-BritoJoão Manuel Pires AranhaErmelindo Silva TavaresAbstract: Lupus miliaris disseminatus faciei is a rare inflammatory dermatosis of unknown etiology that primarily affects young adults. Clinically, it is characterized by an asymptomatic papular eruption mainly involving the central face, typically on and around the eyelids. Characteristic histopathological features include dermal epithelioid cell granulomas with central necrosis and surrounding lymphocytic infiltrate with multinucleate giant cells. Lupus miliaris disseminatus faciei has a spontaneously resolving course, yet can be cosmetically debilitating given the location and potential for scarring. Treatment is difficult and there is a lack of controlled studies. We report a new case of lupus miliaris disseminatus faciei successfully treated with minocycline and systemic steroids, and briefly discuss its nosology and therapeutic options.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962017000600851&tlng=enMinocyclineGranulomaPrednisolone |
spellingShingle | Helena Toda-Brito João Manuel Pires Aranha Ermelindo Silva Tavares Lupus miliaris disseminatus faciei Anais Brasileiros de Dermatologia Minocycline Granuloma Prednisolone |
title | Lupus miliaris disseminatus faciei |
title_full | Lupus miliaris disseminatus faciei |
title_fullStr | Lupus miliaris disseminatus faciei |
title_full_unstemmed | Lupus miliaris disseminatus faciei |
title_short | Lupus miliaris disseminatus faciei |
title_sort | lupus miliaris disseminatus faciei |
topic | Minocycline Granuloma Prednisolone |
url | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962017000600851&tlng=en |
work_keys_str_mv | AT helenatodabrito lupusmiliarisdisseminatusfaciei AT joaomanuelpiresaranha lupusmiliarisdisseminatusfaciei AT ermelindosilvatavares lupusmiliarisdisseminatusfaciei |