Lupus miliaris disseminatus faciei

Abstract: Lupus miliaris disseminatus faciei is a rare inflammatory dermatosis of unknown etiology that primarily affects young adults. Clinically, it is characterized by an asymptomatic papular eruption mainly involving the central face, typically on and around the eyelids. Characteristic histopath...

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Main Authors: Helena Toda-Brito, João Manuel Pires Aranha, Ermelindo Silva Tavares
Format: Article
Language:English
Published: Sociedade Brasileira de Dermatologia 2017-12-01
Series:Anais Brasileiros de Dermatologia
Subjects:
Online Access:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962017000600851&tlng=en
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author Helena Toda-Brito
João Manuel Pires Aranha
Ermelindo Silva Tavares
author_facet Helena Toda-Brito
João Manuel Pires Aranha
Ermelindo Silva Tavares
author_sort Helena Toda-Brito
collection DOAJ
description Abstract: Lupus miliaris disseminatus faciei is a rare inflammatory dermatosis of unknown etiology that primarily affects young adults. Clinically, it is characterized by an asymptomatic papular eruption mainly involving the central face, typically on and around the eyelids. Characteristic histopathological features include dermal epithelioid cell granulomas with central necrosis and surrounding lymphocytic infiltrate with multinucleate giant cells. Lupus miliaris disseminatus faciei has a spontaneously resolving course, yet can be cosmetically debilitating given the location and potential for scarring. Treatment is difficult and there is a lack of controlled studies. We report a new case of lupus miliaris disseminatus faciei successfully treated with minocycline and systemic steroids, and briefly discuss its nosology and therapeutic options.
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spelling doaj.art-6b14d7d26de34ba590c73ab8daf1184a2022-12-21T17:34:39ZengSociedade Brasileira de DermatologiaAnais Brasileiros de Dermatologia0365-05962017-12-0192685185310.1590/abd1806-4841.20174534Lupus miliaris disseminatus facieiHelena Toda-BritoJoão Manuel Pires AranhaErmelindo Silva TavaresAbstract: Lupus miliaris disseminatus faciei is a rare inflammatory dermatosis of unknown etiology that primarily affects young adults. Clinically, it is characterized by an asymptomatic papular eruption mainly involving the central face, typically on and around the eyelids. Characteristic histopathological features include dermal epithelioid cell granulomas with central necrosis and surrounding lymphocytic infiltrate with multinucleate giant cells. Lupus miliaris disseminatus faciei has a spontaneously resolving course, yet can be cosmetically debilitating given the location and potential for scarring. Treatment is difficult and there is a lack of controlled studies. We report a new case of lupus miliaris disseminatus faciei successfully treated with minocycline and systemic steroids, and briefly discuss its nosology and therapeutic options.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962017000600851&tlng=enMinocyclineGranulomaPrednisolone
spellingShingle Helena Toda-Brito
João Manuel Pires Aranha
Ermelindo Silva Tavares
Lupus miliaris disseminatus faciei
Anais Brasileiros de Dermatologia
Minocycline
Granuloma
Prednisolone
title Lupus miliaris disseminatus faciei
title_full Lupus miliaris disseminatus faciei
title_fullStr Lupus miliaris disseminatus faciei
title_full_unstemmed Lupus miliaris disseminatus faciei
title_short Lupus miliaris disseminatus faciei
title_sort lupus miliaris disseminatus faciei
topic Minocycline
Granuloma
Prednisolone
url http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962017000600851&tlng=en
work_keys_str_mv AT helenatodabrito lupusmiliarisdisseminatusfaciei
AT joaomanuelpiresaranha lupusmiliarisdisseminatusfaciei
AT ermelindosilvatavares lupusmiliarisdisseminatusfaciei