Retroperitoneal desmoid tumor in a patient with familial adenomatous polyposis: A case report
Desmoid tumors are benign fibroblastic neoplasms, with locally invasive features and a tendency of recurrence. They are considered an aggressive non-metastatic fibromatosis. The retroperitoneal location is extremely rare. Their exact mechanism of occurrence is still controversial, but could be relat...
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| Format: | Article |
| Language: | English |
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Elsevier
2022-09-01
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| Series: | Radiology Case Reports |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S193004332200365X |
| _version_ | 1818096195347677184 |
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| author | Fathia Aidid, MD Narjisse Aichouni, MD Ihssane Afilal, MD Widad Abbou, MD Rachid Jabi, MD Nadir Miry, MD Amal Bennani, MD Imane Kamaoui, MD Siham Nasri, MD Imane Skiker, MD |
| author_facet | Fathia Aidid, MD Narjisse Aichouni, MD Ihssane Afilal, MD Widad Abbou, MD Rachid Jabi, MD Nadir Miry, MD Amal Bennani, MD Imane Kamaoui, MD Siham Nasri, MD Imane Skiker, MD |
| author_sort | Fathia Aidid, MD |
| collection | DOAJ |
| description | Desmoid tumors are benign fibroblastic neoplasms, with locally invasive features and a tendency of recurrence. They are considered an aggressive non-metastatic fibromatosis. The retroperitoneal location is extremely rare. Their exact mechanism of occurrence is still controversial, but could be related to a genetic predisposition, hormonal factors or traumatic factors, including surgery. This entity faces management difficulties due to its rarity, the variable circumstances of its discovery, and the non-specific clinical manifestations. Their sensitivity to chemotherapy and radiotherapy is limited and surgery remains the only curative treatment in symptomatic cases, however observational waiting could consist the most appropriate management in selected asymptomatic patients, moreover it could avoid unnecessary morbidity from surgery or radiotherapy, which makes the management of this condition a multidisciplinary decision and should be adapted to fit the patients individually. We report a case of a retroperitoneal desmoid tumor in a 31-year-old woman with a history of familial adenomatous polyposis, through which we will discuss this extremely rare neoplastic entity. |
| first_indexed | 2024-12-10T23:00:46Z |
| format | Article |
| id | doaj.art-6b9eec8c0c1d4d229eedf625f48a5943 |
| institution | Directory Open Access Journal |
| issn | 1930-0433 |
| language | English |
| last_indexed | 2024-12-10T23:00:46Z |
| publishDate | 2022-09-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Radiology Case Reports |
| spelling | doaj.art-6b9eec8c0c1d4d229eedf625f48a59432022-12-22T01:30:09ZengElsevierRadiology Case Reports1930-04332022-09-0117929102914Retroperitoneal desmoid tumor in a patient with familial adenomatous polyposis: A case reportFathia Aidid, MD0Narjisse Aichouni, MD1Ihssane Afilal, MD2Widad Abbou, MD3Rachid Jabi, MD4Nadir Miry, MD5Amal Bennani, MD6Imane Kamaoui, MD7Siham Nasri, MD8Imane Skiker, MD9Department of Radiology, Faculty of Medicine, Mohammed VI University Hospital, University Mohammed First, BP 4806 Oujda University 60049, MoroccoDepartment of Radiology, Faculty of Medicine, Mohammed VI University Hospital, University Mohammed First, BP 4806 Oujda University 60049, MoroccoDepartment of Radiology, Faculty of Medicine, Mohammed VI University Hospital, University Mohammed First, BP 4806 Oujda University 60049, Morocco; Corresponding author.Department of Radiology, Faculty of Medicine, Mohammed VI University Hospital, University Mohammed First, BP 4806 Oujda University 60049, MoroccoDepartment of General Surgery, Faculty of Medicine, Mohammed VI University Hospital, University Mohammed First, BP 4806 Oujda University 60049, MoroccoDepartment of Pathology, Faculty of Medicine, Mohammed VI University Hospital, University Mohammed First, BP 4806 Oujda University 60049, MoroccoDepartment of Pathology, Faculty of Medicine, Mohammed VI University Hospital, University Mohammed First, BP 4806 Oujda University 60049, MoroccoDepartment of Radiology, Faculty of Medicine, Mohammed VI University Hospital, University Mohammed First, BP 4806 Oujda University 60049, MoroccoDepartment of Radiology, Faculty of Medicine, Mohammed VI University Hospital, University Mohammed First, BP 4806 Oujda University 60049, MoroccoDepartment of Radiology, Faculty of Medicine, Mohammed VI University Hospital, University Mohammed First, BP 4806 Oujda University 60049, MoroccoDesmoid tumors are benign fibroblastic neoplasms, with locally invasive features and a tendency of recurrence. They are considered an aggressive non-metastatic fibromatosis. The retroperitoneal location is extremely rare. Their exact mechanism of occurrence is still controversial, but could be related to a genetic predisposition, hormonal factors or traumatic factors, including surgery. This entity faces management difficulties due to its rarity, the variable circumstances of its discovery, and the non-specific clinical manifestations. Their sensitivity to chemotherapy and radiotherapy is limited and surgery remains the only curative treatment in symptomatic cases, however observational waiting could consist the most appropriate management in selected asymptomatic patients, moreover it could avoid unnecessary morbidity from surgery or radiotherapy, which makes the management of this condition a multidisciplinary decision and should be adapted to fit the patients individually. We report a case of a retroperitoneal desmoid tumor in a 31-year-old woman with a history of familial adenomatous polyposis, through which we will discuss this extremely rare neoplastic entity.http://www.sciencedirect.com/science/article/pii/S193004332200365XRetroperitonealDesmoid tumorFamilial adenomatous polyposisRare tumor |
| spellingShingle | Fathia Aidid, MD Narjisse Aichouni, MD Ihssane Afilal, MD Widad Abbou, MD Rachid Jabi, MD Nadir Miry, MD Amal Bennani, MD Imane Kamaoui, MD Siham Nasri, MD Imane Skiker, MD Retroperitoneal desmoid tumor in a patient with familial adenomatous polyposis: A case report Radiology Case Reports Retroperitoneal Desmoid tumor Familial adenomatous polyposis Rare tumor |
| title | Retroperitoneal desmoid tumor in a patient with familial adenomatous polyposis: A case report |
| title_full | Retroperitoneal desmoid tumor in a patient with familial adenomatous polyposis: A case report |
| title_fullStr | Retroperitoneal desmoid tumor in a patient with familial adenomatous polyposis: A case report |
| title_full_unstemmed | Retroperitoneal desmoid tumor in a patient with familial adenomatous polyposis: A case report |
| title_short | Retroperitoneal desmoid tumor in a patient with familial adenomatous polyposis: A case report |
| title_sort | retroperitoneal desmoid tumor in a patient with familial adenomatous polyposis a case report |
| topic | Retroperitoneal Desmoid tumor Familial adenomatous polyposis Rare tumor |
| url | http://www.sciencedirect.com/science/article/pii/S193004332200365X |
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