Intra-Abdominal Desmoplastic Small Round Cell Tumor in A 45-Year-Old Man: A Case Report

Intra-abdominal desmoplastic small round cell tumor is a rare entity with a few reports worldwide. This tumor commonly occurs in children and adolescent and occurrence in adult age group is very rare. Here, we describe an adult male with symptoms of intestinal obstruction due to abdominal mass, loca...

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Bibliographic Details
Main Authors: Mandana Ashrafi, Hiva Saffar, Seyed Rasoul Mirsharifi, Seyed Mohammad Tavangar
Format: Article
Language:English
Published: Tehran University of Medical Sciences 2013-08-01
Series:Acta Medica Iranica
Subjects:
Online Access:https://acta.tums.ac.ir/index.php/acta/article/view/4388
Description
Summary:Intra-abdominal desmoplastic small round cell tumor is a rare entity with a few reports worldwide. This tumor commonly occurs in children and adolescent and occurrence in adult age group is very rare. Here, we describe an adult male with symptoms of intestinal obstruction due to abdominal mass, located in splenic flexure. After resection, the diagnosis of intra-abdominal desmoplastic small round cell tumor was established by pathologic and immunohistochemical studies. We emphasize that albeit being rare, this tumor should be mentioned as one of the differential diagnoses of widespread intra-abdominal lesions in any age group.  A brief review of epidemiology, clinical manifestations as well as pathological and molecular features is also included in the paper.
ISSN:0044-6025
1735-9694