Ureteral atresia presenting as an abdominal cyst: A case report
Background: Ureteral atresia is a rare disease that is usually associated with a non-functioning dysplastic kidney. The condition may be unilateral or bilateral, short, or long, and may involve any part of the ureter. Case description: A 4-year-old boy presented with a gradually developing right-sid...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
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Elsevier
2024-03-01
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| Series: | Journal of Pediatric Surgery Case Reports |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2213576624000010 |
| _version_ | 1827324718981578752 |
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| author | Amir Ibrahim Mohamed Mansy Mostafa Kotb Mohamed Abokandil Saber Waheeb |
| author_facet | Amir Ibrahim Mohamed Mansy Mostafa Kotb Mohamed Abokandil Saber Waheeb |
| author_sort | Amir Ibrahim |
| collection | DOAJ |
| description | Background: Ureteral atresia is a rare disease that is usually associated with a non-functioning dysplastic kidney. The condition may be unilateral or bilateral, short, or long, and may involve any part of the ureter. Case description: A 4-year-old boy presented with a gradually developing right-sided abdominal distension. Abdominal examination revealed a right lumbar mas of approximately 20 × 15 cm. Abdominal ultrasound showed a large cystic mass that extended from the hilum of the right kidney and crossed the midline to reach the left side of the abdomen. The left kidney was absent. Voiding cystourethrogram (VCUG) was unremarkable. Magnetic resonance urography (MRU) confirmed the presence of a thin-walled cystic lesion extending from the right renal hilum, crossing midline, reaching the left lumbar region, and the absence of the left kidney. Renal nuclear scan showed a functioning right kidney and an absent left kidney. Exploratory laparotomy via a Pfannenstiel incision revealed a normal right kidney and a large extraperitoneal abdominal cyst. This cyst contained about 200 cc of brownish fluid. The cystic mass was in fact a crossed fused left kidney with a proximal ureteral atresia. Excision of the cyst along with the left ureter was done. The postoperative course was uneventful. Conclusion: Ureteral atresia is a rare condition. It can result in a dysplastic kidney in the form of a large retroperitoneal abdominal cystic mass. |
| first_indexed | 2024-03-07T14:01:06Z |
| format | Article |
| id | doaj.art-6bb9d75a199e4038b38ae483f5616efc |
| institution | Directory Open Access Journal |
| issn | 2213-5766 |
| language | English |
| last_indexed | 2024-03-07T14:01:06Z |
| publishDate | 2024-03-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Journal of Pediatric Surgery Case Reports |
| spelling | doaj.art-6bb9d75a199e4038b38ae483f5616efc2024-03-07T05:27:45ZengElsevierJournal of Pediatric Surgery Case Reports2213-57662024-03-01102102773Ureteral atresia presenting as an abdominal cyst: A case reportAmir Ibrahim0Mohamed Mansy1Mostafa Kotb2Mohamed Abokandil3Saber Waheeb4Nile of Hope Hospital for Congenital Anomalies, Alexandria, Egypt; Alexandria University, Alexandria, Egypt; Corresponding author. Nile of Hope Hospital, Alexandria University Hospital, Egypt.Nile of Hope Hospital for Congenital Anomalies, Alexandria, Egypt; Port Said University, Port Said, EgyptNile of Hope Hospital for Congenital Anomalies, Alexandria, Egypt; Alexandria University, Alexandria, EgyptNile of Hope Hospital for Congenital Anomalies, Alexandria, EgyptNile of Hope Hospital for Congenital Anomalies, Alexandria, Egypt; Alexandria University, Alexandria, EgyptBackground: Ureteral atresia is a rare disease that is usually associated with a non-functioning dysplastic kidney. The condition may be unilateral or bilateral, short, or long, and may involve any part of the ureter. Case description: A 4-year-old boy presented with a gradually developing right-sided abdominal distension. Abdominal examination revealed a right lumbar mas of approximately 20 × 15 cm. Abdominal ultrasound showed a large cystic mass that extended from the hilum of the right kidney and crossed the midline to reach the left side of the abdomen. The left kidney was absent. Voiding cystourethrogram (VCUG) was unremarkable. Magnetic resonance urography (MRU) confirmed the presence of a thin-walled cystic lesion extending from the right renal hilum, crossing midline, reaching the left lumbar region, and the absence of the left kidney. Renal nuclear scan showed a functioning right kidney and an absent left kidney. Exploratory laparotomy via a Pfannenstiel incision revealed a normal right kidney and a large extraperitoneal abdominal cyst. This cyst contained about 200 cc of brownish fluid. The cystic mass was in fact a crossed fused left kidney with a proximal ureteral atresia. Excision of the cyst along with the left ureter was done. The postoperative course was uneventful. Conclusion: Ureteral atresia is a rare condition. It can result in a dysplastic kidney in the form of a large retroperitoneal abdominal cystic mass.http://www.sciencedirect.com/science/article/pii/S2213576624000010Ureteral atresiaCrossed fused kidneyCase report |
| spellingShingle | Amir Ibrahim Mohamed Mansy Mostafa Kotb Mohamed Abokandil Saber Waheeb Ureteral atresia presenting as an abdominal cyst: A case report Journal of Pediatric Surgery Case Reports Ureteral atresia Crossed fused kidney Case report |
| title | Ureteral atresia presenting as an abdominal cyst: A case report |
| title_full | Ureteral atresia presenting as an abdominal cyst: A case report |
| title_fullStr | Ureteral atresia presenting as an abdominal cyst: A case report |
| title_full_unstemmed | Ureteral atresia presenting as an abdominal cyst: A case report |
| title_short | Ureteral atresia presenting as an abdominal cyst: A case report |
| title_sort | ureteral atresia presenting as an abdominal cyst a case report |
| topic | Ureteral atresia Crossed fused kidney Case report |
| url | http://www.sciencedirect.com/science/article/pii/S2213576624000010 |
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