Cleft palate in Pierre Robin syndrome: A Review of 7 cases
Introduction: Pierre Robin syndrome is a malformative sequence associating retrognathism, glossoptosis and a median cleft palate which is usually large. This poses the problem of its therapeutic management. Purpose: To show the approach of the Stomatology and Maxillofacial Surgery Department of the...
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| Format: | Article |
| Language: | English |
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Elsevier
2023-12-01
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| Series: | Advances in Oral and Maxillofacial Surgery |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2667147623000535 |
| _version_ | 1797447991597989888 |
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| author | A.D.C. Opango M.S.K. Hattab Y. Bennaoui D. Ndélafei Z. Aziz N. Mansouri-Hattab |
| author_facet | A.D.C. Opango M.S.K. Hattab Y. Bennaoui D. Ndélafei Z. Aziz N. Mansouri-Hattab |
| author_sort | A.D.C. Opango |
| collection | DOAJ |
| description | Introduction: Pierre Robin syndrome is a malformative sequence associating retrognathism, glossoptosis and a median cleft palate which is usually large. This poses the problem of its therapeutic management. Purpose: To show the approach of the Stomatology and Maxillofacial Surgery Department of the Mohammed VI University Hospital in the management of cleft palate in Pierre Robin syndrome.This was a retrospective study, covering 5 years, which allowed us to include 7 cases of cleft palate in Pierre Robin syndrome. Our study parameters were epidemiological, clinical, therapeutic and evolutionary. Results: The average age of our patients, at the time of the 1st consultation, was 4 months. There was a slight male predominance with a sex ratio = 1.3. The patients presented a U-shaped cleft in 57.1% of cases, and a V-shaped cleft in 42.9% of cases. Three patients underwent a one-stage closure by velopalatoplasty using the Von Langenbeck technique. Four patients underwent a 2-stage closure, i.e., intravascular veloplasty in the first stage, followed by closure of the residual cleft palate in the second stage. The results were satisfactory. A palatal fistula was noted in 42.8% of cases, which was managed secondarily. Conclusion: The management of cleft palate in Pierre Robin syndrome is a real challenge for the maxillofacial surgeon. |
| first_indexed | 2024-03-09T14:03:55Z |
| format | Article |
| id | doaj.art-6bf3fda9045646818a25ea6d6c32e92d |
| institution | Directory Open Access Journal |
| issn | 2667-1476 |
| language | English |
| last_indexed | 2024-03-09T14:03:55Z |
| publishDate | 2023-12-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Advances in Oral and Maxillofacial Surgery |
| spelling | doaj.art-6bf3fda9045646818a25ea6d6c32e92d2023-11-30T05:11:51ZengElsevierAdvances in Oral and Maxillofacial Surgery2667-14762023-12-0112100441Cleft palate in Pierre Robin syndrome: A Review of 7 casesA.D.C. Opango0M.S.K. Hattab1Y. Bennaoui2D. Ndélafei3Z. Aziz4N. Mansouri-Hattab5Corresponding author.; Department of Maxillofacial and Aesthetic Surgery, CHU Mohammed VI Marrakech. Faculty of Medicine and Pharmacy Marrakech, Cadi Ayyad University, MoroccoDepartment of Maxillofacial and Aesthetic Surgery, CHU Mohammed VI Marrakech. Faculty of Medicine and Pharmacy Marrakech, Cadi Ayyad University, MoroccoDepartment of Maxillofacial and Aesthetic Surgery, CHU Mohammed VI Marrakech. Faculty of Medicine and Pharmacy Marrakech, Cadi Ayyad University, MoroccoDepartment of Maxillofacial and Aesthetic Surgery, CHU Mohammed VI Marrakech. Faculty of Medicine and Pharmacy Marrakech, Cadi Ayyad University, MoroccoDepartment of Maxillofacial and Aesthetic Surgery, CHU Mohammed VI Marrakech. Faculty of Medicine and Pharmacy Marrakech, Cadi Ayyad University, MoroccoDepartment of Maxillofacial and Aesthetic Surgery, CHU Mohammed VI Marrakech. Faculty of Medicine and Pharmacy Marrakech, Cadi Ayyad University, MoroccoIntroduction: Pierre Robin syndrome is a malformative sequence associating retrognathism, glossoptosis and a median cleft palate which is usually large. This poses the problem of its therapeutic management. Purpose: To show the approach of the Stomatology and Maxillofacial Surgery Department of the Mohammed VI University Hospital in the management of cleft palate in Pierre Robin syndrome.This was a retrospective study, covering 5 years, which allowed us to include 7 cases of cleft palate in Pierre Robin syndrome. Our study parameters were epidemiological, clinical, therapeutic and evolutionary. Results: The average age of our patients, at the time of the 1st consultation, was 4 months. There was a slight male predominance with a sex ratio = 1.3. The patients presented a U-shaped cleft in 57.1% of cases, and a V-shaped cleft in 42.9% of cases. Three patients underwent a one-stage closure by velopalatoplasty using the Von Langenbeck technique. Four patients underwent a 2-stage closure, i.e., intravascular veloplasty in the first stage, followed by closure of the residual cleft palate in the second stage. The results were satisfactory. A palatal fistula was noted in 42.8% of cases, which was managed secondarily. Conclusion: The management of cleft palate in Pierre Robin syndrome is a real challenge for the maxillofacial surgeon.http://www.sciencedirect.com/science/article/pii/S2667147623000535Cleft palatePierre Robin syndromeVelopalatoplastyIntravelar veloplastyPalatal fistula |
| spellingShingle | A.D.C. Opango M.S.K. Hattab Y. Bennaoui D. Ndélafei Z. Aziz N. Mansouri-Hattab Cleft palate in Pierre Robin syndrome: A Review of 7 cases Advances in Oral and Maxillofacial Surgery Cleft palate Pierre Robin syndrome Velopalatoplasty Intravelar veloplasty Palatal fistula |
| title | Cleft palate in Pierre Robin syndrome: A Review of 7 cases |
| title_full | Cleft palate in Pierre Robin syndrome: A Review of 7 cases |
| title_fullStr | Cleft palate in Pierre Robin syndrome: A Review of 7 cases |
| title_full_unstemmed | Cleft palate in Pierre Robin syndrome: A Review of 7 cases |
| title_short | Cleft palate in Pierre Robin syndrome: A Review of 7 cases |
| title_sort | cleft palate in pierre robin syndrome a review of 7 cases |
| topic | Cleft palate Pierre Robin syndrome Velopalatoplasty Intravelar veloplasty Palatal fistula |
| url | http://www.sciencedirect.com/science/article/pii/S2667147623000535 |
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