Rapid Regression of Exudative Maculopathy in Idiopathic Retinitis, Vasculitis, Aneurysms and Neuroretinitis Syndrome after Intravitreal Ranibizumab

The idiopathic retinitis, vasculitis, aneurysms and neuroretinitis syndrome is a rare retinal vascular disorder characterized by multiple leaking aneurysmal dilations, retinal vasculitis, neuroretinitis and peripheral vascular ischemia. Visual loss mainly occurs due to the development of retinal neo...

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Main Authors: Cristina Marín-Lambíes, Roberto Gallego-Pinazo, David Salom, Javier Navarrete, Manuel Díaz-Llopis
Format: Article
Language:English
Published: Karger Publishers 2012-08-01
Series:Case Reports in Ophthalmology
Subjects:
Online Access:http://www.karger.com/Article/FullText/341821
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author Cristina Marín-Lambíes
Roberto Gallego-Pinazo
David Salom
Javier Navarrete
Manuel Díaz-Llopis
author_facet Cristina Marín-Lambíes
Roberto Gallego-Pinazo
David Salom
Javier Navarrete
Manuel Díaz-Llopis
author_sort Cristina Marín-Lambíes
collection DOAJ
description The idiopathic retinitis, vasculitis, aneurysms and neuroretinitis syndrome is a rare retinal vascular disorder characterized by multiple leaking aneurysmal dilations, retinal vasculitis, neuroretinitis and peripheral vascular ischemia. Visual loss mainly occurs due to the development of retinal neovascularization and/or exudative maculopathy. Although the treatment of choice has not yet been established, retinal photocoagulation seems to be the best option to control the disease and to prevent its progression. Herein, we report a case of idiopathic retinitis, vasculitis, aneurysms and neuroretinitis syndrome with both retinal neovascularization and macular exudation successfully managed with intravitreal ranibizumab (Lucentis®) as adjunctive therapy to retinal photocoagulation.
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spelling doaj.art-6c465018d5dd489e866a1b7f2e8d8ac62022-12-22T01:25:56ZengKarger PublishersCase Reports in Ophthalmology1663-26992012-08-013225125710.1159/000341821341821Rapid Regression of Exudative Maculopathy in Idiopathic Retinitis, Vasculitis, Aneurysms and Neuroretinitis Syndrome after Intravitreal RanibizumabCristina Marín-LambíesRoberto Gallego-PinazoDavid SalomJavier NavarreteManuel Díaz-LlopisThe idiopathic retinitis, vasculitis, aneurysms and neuroretinitis syndrome is a rare retinal vascular disorder characterized by multiple leaking aneurysmal dilations, retinal vasculitis, neuroretinitis and peripheral vascular ischemia. Visual loss mainly occurs due to the development of retinal neovascularization and/or exudative maculopathy. Although the treatment of choice has not yet been established, retinal photocoagulation seems to be the best option to control the disease and to prevent its progression. Herein, we report a case of idiopathic retinitis, vasculitis, aneurysms and neuroretinitis syndrome with both retinal neovascularization and macular exudation successfully managed with intravitreal ranibizumab (Lucentis®) as adjunctive therapy to retinal photocoagulation.http://www.karger.com/Article/FullText/341821Idiopathic retinitis, vasculitis, aneurysms and neuroretinitis syndromeExudative maculopathyRanibizumab
spellingShingle Cristina Marín-Lambíes
Roberto Gallego-Pinazo
David Salom
Javier Navarrete
Manuel Díaz-Llopis
Rapid Regression of Exudative Maculopathy in Idiopathic Retinitis, Vasculitis, Aneurysms and Neuroretinitis Syndrome after Intravitreal Ranibizumab
Case Reports in Ophthalmology
Idiopathic retinitis, vasculitis, aneurysms and neuroretinitis syndrome
Exudative maculopathy
Ranibizumab
title Rapid Regression of Exudative Maculopathy in Idiopathic Retinitis, Vasculitis, Aneurysms and Neuroretinitis Syndrome after Intravitreal Ranibizumab
title_full Rapid Regression of Exudative Maculopathy in Idiopathic Retinitis, Vasculitis, Aneurysms and Neuroretinitis Syndrome after Intravitreal Ranibizumab
title_fullStr Rapid Regression of Exudative Maculopathy in Idiopathic Retinitis, Vasculitis, Aneurysms and Neuroretinitis Syndrome after Intravitreal Ranibizumab
title_full_unstemmed Rapid Regression of Exudative Maculopathy in Idiopathic Retinitis, Vasculitis, Aneurysms and Neuroretinitis Syndrome after Intravitreal Ranibizumab
title_short Rapid Regression of Exudative Maculopathy in Idiopathic Retinitis, Vasculitis, Aneurysms and Neuroretinitis Syndrome after Intravitreal Ranibizumab
title_sort rapid regression of exudative maculopathy in idiopathic retinitis vasculitis aneurysms and neuroretinitis syndrome after intravitreal ranibizumab
topic Idiopathic retinitis, vasculitis, aneurysms and neuroretinitis syndrome
Exudative maculopathy
Ranibizumab
url http://www.karger.com/Article/FullText/341821
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