Splenic Torsion in Heterotaxy Syndrome with Left Isomerism: A Case Report and Literature Review
Splenic torsion is an unusual condition that results in congenital abnormality, especially in the visceral abnormal arrangement. We report the case of an 8.5-year-old boy with features in the right upper quadrant. Radiological investigations revealed heterotaxy syndrome with polysplenia and a hypode...
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MDPI AG
2022-11-01
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| Series: | Diagnostics |
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| Online Access: | https://www.mdpi.com/2075-4418/12/12/2920 |
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| author | I Nok Cheang Yu-Wei Fu Tai-Wai Chin Yao-Jen Hsu Chin-Yen Wu |
| author_facet | I Nok Cheang Yu-Wei Fu Tai-Wai Chin Yao-Jen Hsu Chin-Yen Wu |
| author_sort | I Nok Cheang |
| collection | DOAJ |
| description | Splenic torsion is an unusual condition that results in congenital abnormality, especially in the visceral abnormal arrangement. We report the case of an 8.5-year-old boy with features in the right upper quadrant. Radiological investigations revealed heterotaxy syndrome with polysplenia and a hypodense tumor in the right upper quadrant adjacent to several spleens. We initially treated it as an intra-abdominal tumor. Laparoscopy was performed to check the tumor condition and revealed a congestive tumor located in the abdomen of the right upper quadrant below the central liver, which was suspected to be a torsion spleen without attaching ligaments. Laparoscopic splenectomy was successfully carried out without complications. The pathological report shows splenic tissue with hemorrhagic infarction. Physicians should be vigilant of the differential diagnosis of the acute abdomen in adolescents. |
| first_indexed | 2024-03-09T17:09:20Z |
| format | Article |
| id | doaj.art-6c4ad16a491b42c1b267838e5d95bded |
| institution | Directory Open Access Journal |
| issn | 2075-4418 |
| language | English |
| last_indexed | 2024-03-09T17:09:20Z |
| publishDate | 2022-11-01 |
| publisher | MDPI AG |
| record_format | Article |
| series | Diagnostics |
| spelling | doaj.art-6c4ad16a491b42c1b267838e5d95bded2023-11-24T14:15:31ZengMDPI AGDiagnostics2075-44182022-11-011212292010.3390/diagnostics12122920Splenic Torsion in Heterotaxy Syndrome with Left Isomerism: A Case Report and Literature ReviewI Nok Cheang0Yu-Wei Fu1Tai-Wai Chin2Yao-Jen Hsu3Chin-Yen Wu4Division of Pediatric Surgery, Department of Surgery, Changhua Christian Hospital, Changhua 500-06, TaiwanDivision of Pediatric Surgery, Department of Surgery, Changhua Christian Hospital, Changhua 500-06, TaiwanDivision of Pediatric Surgery, Department of Surgery, Changhua Christian Hospital, Changhua 500-06, TaiwanDivision of Pediatric Surgery, Department of Surgery, Changhua Christian Hospital, Changhua 500-06, TaiwanDepartment of Nursing, Changhua Christian Hospital, Changhua 500-06, TaiwanSplenic torsion is an unusual condition that results in congenital abnormality, especially in the visceral abnormal arrangement. We report the case of an 8.5-year-old boy with features in the right upper quadrant. Radiological investigations revealed heterotaxy syndrome with polysplenia and a hypodense tumor in the right upper quadrant adjacent to several spleens. We initially treated it as an intra-abdominal tumor. Laparoscopy was performed to check the tumor condition and revealed a congestive tumor located in the abdomen of the right upper quadrant below the central liver, which was suspected to be a torsion spleen without attaching ligaments. Laparoscopic splenectomy was successfully carried out without complications. The pathological report shows splenic tissue with hemorrhagic infarction. Physicians should be vigilant of the differential diagnosis of the acute abdomen in adolescents.https://www.mdpi.com/2075-4418/12/12/2920heterotaxyleft isomerismpolyspleniasplenic torsion |
| spellingShingle | I Nok Cheang Yu-Wei Fu Tai-Wai Chin Yao-Jen Hsu Chin-Yen Wu Splenic Torsion in Heterotaxy Syndrome with Left Isomerism: A Case Report and Literature Review Diagnostics heterotaxy left isomerism polysplenia splenic torsion |
| title | Splenic Torsion in Heterotaxy Syndrome with Left Isomerism: A Case Report and Literature Review |
| title_full | Splenic Torsion in Heterotaxy Syndrome with Left Isomerism: A Case Report and Literature Review |
| title_fullStr | Splenic Torsion in Heterotaxy Syndrome with Left Isomerism: A Case Report and Literature Review |
| title_full_unstemmed | Splenic Torsion in Heterotaxy Syndrome with Left Isomerism: A Case Report and Literature Review |
| title_short | Splenic Torsion in Heterotaxy Syndrome with Left Isomerism: A Case Report and Literature Review |
| title_sort | splenic torsion in heterotaxy syndrome with left isomerism a case report and literature review |
| topic | heterotaxy left isomerism polysplenia splenic torsion |
| url | https://www.mdpi.com/2075-4418/12/12/2920 |
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