Severe Spinal Injury in Hirayama Disease
Hirayama disease is a rare neurological disorder characterized by an insidious progressive subacute unilateral or bilateral weakness of the hands and forearm muscles leading to a painless amyotrophy. The disease primarily affects young men in the second to third decades of life. It has always been d...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
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Korean Spine Society
2015-10-01
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| Series: | Asian Spine Journal |
| Subjects: | |
| Online Access: | http://www.asianspinejournal.org/upload/pdf/asj-9-794.pdf |
| _version_ | 1819063345470242816 |
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| author | Cecilia Quarracino Florencia Aguirre Carlos A. Rugilo Luciana De Negri Andrés M. Villa |
| author_facet | Cecilia Quarracino Florencia Aguirre Carlos A. Rugilo Luciana De Negri Andrés M. Villa |
| author_sort | Cecilia Quarracino |
| collection | DOAJ |
| description | Hirayama disease is a rare neurological disorder characterized by an insidious progressive subacute unilateral or bilateral weakness of the hands and forearm muscles leading to a painless amyotrophy. The disease primarily affects young men in the second to third decades of life. It has always been described as a second motor neuron disease, thus sparing the pyramidal and sensitive pathways. It usually has a slow progression course of 3 to 5 years followed by stabilization. Since its initial description by Keyzo Hirayama in 1959, most cases have been reported in Asia, particularly Japan and India, although the disease reportedly has worldwide distribution. |
| first_indexed | 2024-12-21T15:13:12Z |
| format | Article |
| id | doaj.art-6cc9a6f0351547c1ab2649ab60eb586a |
| institution | Directory Open Access Journal |
| issn | 1976-1902 1976-7846 |
| language | English |
| last_indexed | 2024-12-21T15:13:12Z |
| publishDate | 2015-10-01 |
| publisher | Korean Spine Society |
| record_format | Article |
| series | Asian Spine Journal |
| spelling | doaj.art-6cc9a6f0351547c1ab2649ab60eb586a2022-12-21T18:59:13ZengKorean Spine SocietyAsian Spine Journal1976-19021976-78462015-10-019579479710.4184/asj.2015.9.5.794860Severe Spinal Injury in Hirayama DiseaseCecilia Quarracino0Florencia Aguirre1Carlos A. Rugilo2Luciana De Negri3Andrés M. Villa4Neuroimmunology and Electrophysiology Section, Neurology Department, Ramos Mejía Hospital, Buenos Aires University School of Medicine, Buenos Aires, Argentina.Neuroimmunology and Electrophysiology Section, Neurology Department, Ramos Mejía Hospital, Buenos Aires University School of Medicine, Buenos Aires, Argentina.Neuroradiology Section, British Hospital of Buenos Aires, Buenos Aires, Argentina.Neuroimmunology and Electrophysiology Section, Neurology Department, Ramos Mejía Hospital, Buenos Aires University School of Medicine, Buenos Aires, Argentina.Neuroimmunology and Electrophysiology Section, Neurology Department, Ramos Mejía Hospital, Buenos Aires University School of Medicine, Buenos Aires, Argentina.Hirayama disease is a rare neurological disorder characterized by an insidious progressive subacute unilateral or bilateral weakness of the hands and forearm muscles leading to a painless amyotrophy. The disease primarily affects young men in the second to third decades of life. It has always been described as a second motor neuron disease, thus sparing the pyramidal and sensitive pathways. It usually has a slow progression course of 3 to 5 years followed by stabilization. Since its initial description by Keyzo Hirayama in 1959, most cases have been reported in Asia, particularly Japan and India, although the disease reportedly has worldwide distribution.http://www.asianspinejournal.org/upload/pdf/asj-9-794.pdfHirayama diseaseOblique amyotrophyHand atrophySegmental spinal atrophyDynamic myelopathy |
| spellingShingle | Cecilia Quarracino Florencia Aguirre Carlos A. Rugilo Luciana De Negri Andrés M. Villa Severe Spinal Injury in Hirayama Disease Asian Spine Journal Hirayama disease Oblique amyotrophy Hand atrophy Segmental spinal atrophy Dynamic myelopathy |
| title | Severe Spinal Injury in Hirayama Disease |
| title_full | Severe Spinal Injury in Hirayama Disease |
| title_fullStr | Severe Spinal Injury in Hirayama Disease |
| title_full_unstemmed | Severe Spinal Injury in Hirayama Disease |
| title_short | Severe Spinal Injury in Hirayama Disease |
| title_sort | severe spinal injury in hirayama disease |
| topic | Hirayama disease Oblique amyotrophy Hand atrophy Segmental spinal atrophy Dynamic myelopathy |
| url | http://www.asianspinejournal.org/upload/pdf/asj-9-794.pdf |
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