Ectrodactyly: A rare anomaly of limbs
Ectrodactyly refers to the congenital limb malformation, characterized by a deep median cleft of the hand and/or foot due to the absence of central rays. Affected individuals may be recognized by a lobster-claw deformity of their limb extremities that causes severe functional disorders. A combinatio...
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Format: | Article |
Language: | English |
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Wolters Kluwer Medknow Publications
2015-01-01
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Series: | Journal of Dr. NTR University of Health Sciences |
Subjects: | |
Online Access: | http://www.jdrntruhs.org/article.asp?issn=2277-8632;year=2015;volume=4;issue=1;spage=53;epage=55;aulast=SVSG |
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author | Nirmala SVSG Sandeep Chilamakuri Chaitanya Pavuluri Sivakumar Nuvvula Sindhuri Veluru |
author_facet | Nirmala SVSG Sandeep Chilamakuri Chaitanya Pavuluri Sivakumar Nuvvula Sindhuri Veluru |
author_sort | Nirmala SVSG |
collection | DOAJ |
description | Ectrodactyly refers to the congenital limb malformation, characterized by a deep median cleft of the hand and/or foot due to the absence of central rays. Affected individuals may be recognized by a lobster-claw deformity of their limb extremities that causes severe functional disorders. A combination of ectrodactyly, ectodermal dysplasia and cleft (EEC) in the lip or palate is called as EEC syndrome. This paper reports a case of the nonsyn dromic form of ectrodactyly in a 9-year-old girl along with etiological factors and its management. |
first_indexed | 2024-04-13T15:50:55Z |
format | Article |
id | doaj.art-6d6c001a0e104faeb2fd5c56ba55c076 |
institution | Directory Open Access Journal |
issn | 2277-8632 |
language | English |
last_indexed | 2024-04-13T15:50:55Z |
publishDate | 2015-01-01 |
publisher | Wolters Kluwer Medknow Publications |
record_format | Article |
series | Journal of Dr. NTR University of Health Sciences |
spelling | doaj.art-6d6c001a0e104faeb2fd5c56ba55c0762022-12-22T02:40:51ZengWolters Kluwer Medknow PublicationsJournal of Dr. NTR University of Health Sciences2277-86322015-01-0141535510.4103/2277-8632.153329Ectrodactyly: A rare anomaly of limbsNirmala SVSGSandeep ChilamakuriChaitanya PavuluriSivakumar NuvvulaSindhuri VeluruEctrodactyly refers to the congenital limb malformation, characterized by a deep median cleft of the hand and/or foot due to the absence of central rays. Affected individuals may be recognized by a lobster-claw deformity of their limb extremities that causes severe functional disorders. A combination of ectrodactyly, ectodermal dysplasia and cleft (EEC) in the lip or palate is called as EEC syndrome. This paper reports a case of the nonsyn dromic form of ectrodactyly in a 9-year-old girl along with etiological factors and its management.http://www.jdrntruhs.org/article.asp?issn=2277-8632;year=2015;volume=4;issue=1;spage=53;epage=55;aulast=SVSGNonsyndromic ectrodactylysplit foot malformationsplit a hand |
spellingShingle | Nirmala SVSG Sandeep Chilamakuri Chaitanya Pavuluri Sivakumar Nuvvula Sindhuri Veluru Ectrodactyly: A rare anomaly of limbs Journal of Dr. NTR University of Health Sciences Nonsyndromic ectrodactyly split foot malformation split a hand |
title | Ectrodactyly: A rare anomaly of limbs |
title_full | Ectrodactyly: A rare anomaly of limbs |
title_fullStr | Ectrodactyly: A rare anomaly of limbs |
title_full_unstemmed | Ectrodactyly: A rare anomaly of limbs |
title_short | Ectrodactyly: A rare anomaly of limbs |
title_sort | ectrodactyly a rare anomaly of limbs |
topic | Nonsyndromic ectrodactyly split foot malformation split a hand |
url | http://www.jdrntruhs.org/article.asp?issn=2277-8632;year=2015;volume=4;issue=1;spage=53;epage=55;aulast=SVSG |
work_keys_str_mv | AT nirmalasvsg ectrodactylyarareanomalyoflimbs AT sandeepchilamakuri ectrodactylyarareanomalyoflimbs AT chaitanyapavuluri ectrodactylyarareanomalyoflimbs AT sivakumarnuvvula ectrodactylyarareanomalyoflimbs AT sindhuriveluru ectrodactylyarareanomalyoflimbs |