Cardiac involvement in Erdheim-Chester disease: a case report.

Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis of unknown etiology characterized by proliferation of lipid-containing foamy histiocytes affecting bones and potentially every organ. There is a wide clinical spectrum of the disease, ranging from asymptomatic bone or soft-tis...

Ausführliche Beschreibung

Bibliographische Detailangaben
Hauptverfasser: Fernando Pivatto Júnior, Diogo Silva Piardi, Felipe Soares Torres
Format: Artikel
Sprache:English
Veröffentlicht: Hospital de Clinicas de Porto Alegre ; Universidade Federal do Rio Grande do Sul (UFRGS) 2015-01-01
Schriftenreihe:Clinical and Biomedical Research
Schlagworte:
Online Zugang:http://seer.ufrgs.br/hcpa/article/view/51436

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