Embryonal rhabdomyosarcoma of the orbit in a child
Rhabdomyosarcoma (RMS) is the most common soft-tissue sarcoma in children and frequently involves the head and neck region with 10% of the cases primarily involving the orbit. It is a highly malignant tumor which can be life-threatening. It usually produces a precipitously progressing unilateral pro...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2018-01-01
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| Series: | Medical Journal of Dr. D.Y. Patil Vidyapeeth |
| Subjects: | |
| Online Access: | http://www.mjdrdypv.org/article.asp?issn=2589-8302;year=2018;volume=11;issue=3;spage=276;epage=278;aulast=Singh |
| _version_ | 1819198801461641216 |
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| author | Aditya Pratap Singh Arun Kumar Gupta Vinay Mathur Dinesh Kumar Barolia |
| author_facet | Aditya Pratap Singh Arun Kumar Gupta Vinay Mathur Dinesh Kumar Barolia |
| author_sort | Aditya Pratap Singh |
| collection | DOAJ |
| description | Rhabdomyosarcoma (RMS) is the most common soft-tissue sarcoma in children and frequently involves the head and neck region with 10% of the cases primarily involving the orbit. It is a highly malignant tumor which can be life-threatening. It usually produces a precipitously progressing unilateral proptosis of sudden onset. Computed tomography and magnetic resonance imaging are important in the evaluation of this tumor. Histologically, embryonal subtype is most common in children. Complete resection followed by chemotherapy and radiotherapy is the preferred treatment of choice. We are reporting here a case of the embryonal RMS of orbit presenting with rapid proptosis of the right eye in a 14-month-old male child. |
| first_indexed | 2024-12-23T03:06:13Z |
| format | Article |
| id | doaj.art-6ed6759ead214646ae486bd027ac9ddb |
| institution | Directory Open Access Journal |
| issn | 2589-8302 2589-8310 |
| language | English |
| last_indexed | 2024-12-23T03:06:13Z |
| publishDate | 2018-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Medical Journal of Dr. D.Y. Patil Vidyapeeth |
| spelling | doaj.art-6ed6759ead214646ae486bd027ac9ddb2022-12-21T18:02:19ZengWolters Kluwer Medknow PublicationsMedical Journal of Dr. D.Y. Patil Vidyapeeth2589-83022589-83102018-01-0111327627810.4103/MJDRDYPU.MJDRDYPU_117_17Embryonal rhabdomyosarcoma of the orbit in a childAditya Pratap SinghArun Kumar GuptaVinay MathurDinesh Kumar BaroliaRhabdomyosarcoma (RMS) is the most common soft-tissue sarcoma in children and frequently involves the head and neck region with 10% of the cases primarily involving the orbit. It is a highly malignant tumor which can be life-threatening. It usually produces a precipitously progressing unilateral proptosis of sudden onset. Computed tomography and magnetic resonance imaging are important in the evaluation of this tumor. Histologically, embryonal subtype is most common in children. Complete resection followed by chemotherapy and radiotherapy is the preferred treatment of choice. We are reporting here a case of the embryonal RMS of orbit presenting with rapid proptosis of the right eye in a 14-month-old male child.http://www.mjdrdypv.org/article.asp?issn=2589-8302;year=2018;volume=11;issue=3;spage=276;epage=278;aulast=SinghEmbryonalorbitproptosisrhabdomyosarcoma |
| spellingShingle | Aditya Pratap Singh Arun Kumar Gupta Vinay Mathur Dinesh Kumar Barolia Embryonal rhabdomyosarcoma of the orbit in a child Medical Journal of Dr. D.Y. Patil Vidyapeeth Embryonal orbit proptosis rhabdomyosarcoma |
| title | Embryonal rhabdomyosarcoma of the orbit in a child |
| title_full | Embryonal rhabdomyosarcoma of the orbit in a child |
| title_fullStr | Embryonal rhabdomyosarcoma of the orbit in a child |
| title_full_unstemmed | Embryonal rhabdomyosarcoma of the orbit in a child |
| title_short | Embryonal rhabdomyosarcoma of the orbit in a child |
| title_sort | embryonal rhabdomyosarcoma of the orbit in a child |
| topic | Embryonal orbit proptosis rhabdomyosarcoma |
| url | http://www.mjdrdypv.org/article.asp?issn=2589-8302;year=2018;volume=11;issue=3;spage=276;epage=278;aulast=Singh |
| work_keys_str_mv | AT adityapratapsingh embryonalrhabdomyosarcomaoftheorbitinachild AT arunkumargupta embryonalrhabdomyosarcomaoftheorbitinachild AT vinaymathur embryonalrhabdomyosarcomaoftheorbitinachild AT dineshkumarbarolia embryonalrhabdomyosarcomaoftheorbitinachild |