Electrocardiographic Changes and Arrhythmia in Fabry Disease

Electrocardiographic Changes and Arrhythmia in Fabry Disease

Fabry disease is an X-chromosome-linked lysosomal storage disease characterized by a deficient activity or, in most males, absence of the enzyme alpha-galactosidase A (a-Gal A) leading to systemic, primary lysosomal accumulation of globotriaosylceramide (Gb3). Multi-system morbidity commonly develop...

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Bibliographic Details
Main Author:	Mehdi eNamdar
Format:	Article
Language:	English
Published:	Frontiers Media S.A. 2016-03-01
Series:	Frontiers in Cardiovascular Medicine
Subjects:	Electrocardiography Fabry Disease Lysosomal Storage Diseases Sphingolipidoses arrhythmia
Online Access:	http://journal.frontiersin.org/Journal/10.3389/fcvm.2016.00007/full

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