A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung
Tumoral amyloidosis, or amyloidoma, is a benign, but rare form of amyloidosis that has been reported with a favorable prognosis following surgical resection in some case reports. We present a case of acute on chronic respiratory failure secondary to extensive growth of a thoracic amyloidoma causing...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
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Elsevier
2023-01-01
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| Series: | Respiratory Medicine Case Reports |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2213007123000321 |
| _version_ | 1827952956090089472 |
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| author | Smruti Rath Nicholas Joseph Dcunha Neel Bhan Bettye Cox Muhammad Adrish |
| author_facet | Smruti Rath Nicholas Joseph Dcunha Neel Bhan Bettye Cox Muhammad Adrish |
| author_sort | Smruti Rath |
| collection | DOAJ |
| description | Tumoral amyloidosis, or amyloidoma, is a benign, but rare form of amyloidosis that has been reported with a favorable prognosis following surgical resection in some case reports. We present a case of acute on chronic respiratory failure secondary to extensive growth of a thoracic amyloidoma causing atelectasis of the right lung. Our case patient had greater morbidity due to late presentation and extensive disease at diagnosis, precluding any surgical intervention. Radiation therapy and medical management were unsuccessful in reducing disease burden. Early diagnosis and detection are pivotal to improving survival in patients with isolated thoracic amyloidoma. |
| first_indexed | 2024-04-09T14:06:35Z |
| format | Article |
| id | doaj.art-6f974c32155d4dd895996fb2634b5adf |
| institution | Directory Open Access Journal |
| issn | 2213-0071 |
| language | English |
| last_indexed | 2024-04-09T14:06:35Z |
| publishDate | 2023-01-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Respiratory Medicine Case Reports |
| spelling | doaj.art-6f974c32155d4dd895996fb2634b5adf2023-05-07T04:16:47ZengElsevierRespiratory Medicine Case Reports2213-00712023-01-0143101837A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lungSmruti Rath0Nicholas Joseph Dcunha1Neel Bhan2Bettye Cox3Muhammad Adrish4Department of Medicine, Icahn School of Medicine at Mount Sinai Hospital, New York, NY, USADepartment of Pathology, Baylor College of Medicine, Houston, TX, USADepartment of Pulmonary and Critical Care, Baylor College of Medicine, Houston, TX, USADepartment of Pathology, Baylor College of Medicine, Houston, TX, USADepartment of Pulmonary and Critical Care, Baylor College of Medicine, Houston, TX, USA; Corresponding author. Pulmonary, Critical Care, and Sleep Medicine, Division of Pulmonary and Critical Care Medicine, Ben Taub Hospital, 1504 Taub Loop, Houston, TX, 77479, USA.Tumoral amyloidosis, or amyloidoma, is a benign, but rare form of amyloidosis that has been reported with a favorable prognosis following surgical resection in some case reports. We present a case of acute on chronic respiratory failure secondary to extensive growth of a thoracic amyloidoma causing atelectasis of the right lung. Our case patient had greater morbidity due to late presentation and extensive disease at diagnosis, precluding any surgical intervention. Radiation therapy and medical management were unsuccessful in reducing disease burden. Early diagnosis and detection are pivotal to improving survival in patients with isolated thoracic amyloidoma.http://www.sciencedirect.com/science/article/pii/S2213007123000321AmyloidomaTumoral amyloidosisRespiratory failure |
| spellingShingle | Smruti Rath Nicholas Joseph Dcunha Neel Bhan Bettye Cox Muhammad Adrish A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung Respiratory Medicine Case Reports Amyloidoma Tumoral amyloidosis Respiratory failure |
| title | A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung |
| title_full | A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung |
| title_fullStr | A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung |
| title_full_unstemmed | A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung |
| title_short | A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung |
| title_sort | rare case of isolated thoracic al amyloidoma causing complete atelectasis of the right lung |
| topic | Amyloidoma Tumoral amyloidosis Respiratory failure |
| url | http://www.sciencedirect.com/science/article/pii/S2213007123000321 |
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