Isolated unilateral absence of pulmonary artery (IUAPA) in adults: A case series and review of literature
Abstract Unilateral Absence of Pulmonary Artery (UAPA) is a rare congenital malformation that is usually associated with cardiac anomalies. When there is no congenital cardiac abnormality it is rarer still and is termed isolated unilateral absence of pulmonary artery (IUAPA) (4). IUAPA may remain un...
| Main Authors: | , , |
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| Format: | Article |
| Language: | English |
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Wiley
2023-01-01
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| Series: | Respirology Case Reports |
| Subjects: | |
| Online Access: | https://doi.org/10.1002/rcr2.1073 |
| _version_ | 1797976231996555264 |
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| author | Yi Jia Loo Rajesh Thomas Lokesh Yagnik |
| author_facet | Yi Jia Loo Rajesh Thomas Lokesh Yagnik |
| author_sort | Yi Jia Loo |
| collection | DOAJ |
| description | Abstract Unilateral Absence of Pulmonary Artery (UAPA) is a rare congenital malformation that is usually associated with cardiac anomalies. When there is no congenital cardiac abnormality it is rarer still and is termed isolated unilateral absence of pulmonary artery (IUAPA) (4). IUAPA may remain undetected until adulthood and frequently found incidentally on imaging for other indications. Symptoms are usually secondary to complications which include pulmonary hypertension, recurrent respiratory tract infections, bronchiectasis and haemoptysis. We report two cases with widely contrasting presentation and trajectories, leading to individualized management strategies. |
| first_indexed | 2024-04-11T04:47:48Z |
| format | Article |
| id | doaj.art-6fc99fdf796447f9bf01745e3878c358 |
| institution | Directory Open Access Journal |
| issn | 2051-3380 |
| language | English |
| last_indexed | 2024-04-11T04:47:48Z |
| publishDate | 2023-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Respirology Case Reports |
| spelling | doaj.art-6fc99fdf796447f9bf01745e3878c3582022-12-27T07:06:30ZengWileyRespirology Case Reports2051-33802023-01-01111n/an/a10.1002/rcr2.1073Isolated unilateral absence of pulmonary artery (IUAPA) in adults: A case series and review of literatureYi Jia Loo0Rajesh Thomas1Lokesh Yagnik2Department of Respiratory Medicine Fiona Stanley Hospital Perth Western Australia AustraliaDepartment of Respiratory Medicine Sir Charles Gairdner Hospital Perth Western Australia AustraliaDepartment of Respiratory Medicine Fiona Stanley Hospital Perth Western Australia AustraliaAbstract Unilateral Absence of Pulmonary Artery (UAPA) is a rare congenital malformation that is usually associated with cardiac anomalies. When there is no congenital cardiac abnormality it is rarer still and is termed isolated unilateral absence of pulmonary artery (IUAPA) (4). IUAPA may remain undetected until adulthood and frequently found incidentally on imaging for other indications. Symptoms are usually secondary to complications which include pulmonary hypertension, recurrent respiratory tract infections, bronchiectasis and haemoptysis. We report two cases with widely contrasting presentation and trajectories, leading to individualized management strategies.https://doi.org/10.1002/rcr2.1073congenitalhaemoptysisisolated unilateral absence of pulmonary arterysymptomstreatment |
| spellingShingle | Yi Jia Loo Rajesh Thomas Lokesh Yagnik Isolated unilateral absence of pulmonary artery (IUAPA) in adults: A case series and review of literature Respirology Case Reports congenital haemoptysis isolated unilateral absence of pulmonary artery symptoms treatment |
| title | Isolated unilateral absence of pulmonary artery (IUAPA) in adults: A case series and review of literature |
| title_full | Isolated unilateral absence of pulmonary artery (IUAPA) in adults: A case series and review of literature |
| title_fullStr | Isolated unilateral absence of pulmonary artery (IUAPA) in adults: A case series and review of literature |
| title_full_unstemmed | Isolated unilateral absence of pulmonary artery (IUAPA) in adults: A case series and review of literature |
| title_short | Isolated unilateral absence of pulmonary artery (IUAPA) in adults: A case series and review of literature |
| title_sort | isolated unilateral absence of pulmonary artery iuapa in adults a case series and review of literature |
| topic | congenital haemoptysis isolated unilateral absence of pulmonary artery symptoms treatment |
| url | https://doi.org/10.1002/rcr2.1073 |
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