Right Atrial Angiosarcoma with Severe Biventricular Dysfunction and Massive Pericardial Effusion

This paper presents the case of a 35 year-old woman with symptoms of heart failure from the last month. A physical examination at admission showed paleness, dyspnea, peripheral edema and fatigue. In a two-dimensional echocardiography and transesophageal echocardiography, normal thickness but severe...

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Main Authors: Feridoun Sabzi, Heidar Dadkhah, Sharam Shojaei, Masoume Mahdavi, Alireza Poormotaabed, Nasrin Javid, Samsam Dabiri
Format: Article
Language:English
Published: Tehran University of Medical Sciences 2013-02-01
Series:Acta Medica Iranica
Subjects:
Online Access:http://acta.tums.ac.ir/index.php/acta/article/view/2410/2143
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author Feridoun Sabzi
Heidar Dadkhah
Sharam Shojaei
Masoume Mahdavi
Alireza Poormotaabed
Nasrin Javid
Samsam Dabiri
author_facet Feridoun Sabzi
Heidar Dadkhah
Sharam Shojaei
Masoume Mahdavi
Alireza Poormotaabed
Nasrin Javid
Samsam Dabiri
author_sort Feridoun Sabzi
collection DOAJ
description This paper presents the case of a 35 year-old woman with symptoms of heart failure from the last month. A physical examination at admission showed paleness, dyspnea, peripheral edema and fatigue. In a two-dimensional echocardiography and transesophageal echocardiography, normal thickness but severe left and right ventricular dysfunction with severe pericardial effusion and thickened pericardium were found. In the enlarged right atrium, an oval-shaped structure was found with features of continuity with lateral right atrial wall and also a bulging of the structure through the orifice of the tricuspid valve to the right ventricle. In the echocardiography, we did not saw any blocking of the tricuspid valve or the inflow from inferior vena cava (IVC) or superior vena cava (SVC) or coronary sinus. On the basis of the echocardiography examination and clinical presentation, tentative diagnosis of the right atrium myxoma was made. A coronary angiography revealed normal coronary arteries and no feeding of tumor by branch of right coronary artery (RCA). Surgical removal of the tumor was performed without complication. The histopathological examination confirmed the diagnosis of angiosarcoma. In the follow-up echocardiography carried out after three months, severe left ventricular (LV) and right ventricular (RV) dysfunction continued and was demonstrated. Magnetic resonance imaging revealed no lymphadenopathy or re-growth of the tumor in the mediastinum or pericardium.
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spelling doaj.art-702833aa39ea497b90ce1b67cf986d7e2022-12-21T23:09:21ZengTehran University of Medical SciencesActa Medica Iranica0044-60251735-96942013-02-01512129134Right Atrial Angiosarcoma with Severe Biventricular Dysfunction and Massive Pericardial EffusionFeridoun SabziHeidar DadkhahSharam ShojaeiMasoume MahdaviAlireza PoormotaabedNasrin JavidSamsam DabiriThis paper presents the case of a 35 year-old woman with symptoms of heart failure from the last month. A physical examination at admission showed paleness, dyspnea, peripheral edema and fatigue. In a two-dimensional echocardiography and transesophageal echocardiography, normal thickness but severe left and right ventricular dysfunction with severe pericardial effusion and thickened pericardium were found. In the enlarged right atrium, an oval-shaped structure was found with features of continuity with lateral right atrial wall and also a bulging of the structure through the orifice of the tricuspid valve to the right ventricle. In the echocardiography, we did not saw any blocking of the tricuspid valve or the inflow from inferior vena cava (IVC) or superior vena cava (SVC) or coronary sinus. On the basis of the echocardiography examination and clinical presentation, tentative diagnosis of the right atrium myxoma was made. A coronary angiography revealed normal coronary arteries and no feeding of tumor by branch of right coronary artery (RCA). Surgical removal of the tumor was performed without complication. The histopathological examination confirmed the diagnosis of angiosarcoma. In the follow-up echocardiography carried out after three months, severe left ventricular (LV) and right ventricular (RV) dysfunction continued and was demonstrated. Magnetic resonance imaging revealed no lymphadenopathy or re-growth of the tumor in the mediastinum or pericardium.http://acta.tums.ac.ir/index.php/acta/article/view/2410/2143AngiosarcomaHeart TumorPericardial Effusion
spellingShingle Feridoun Sabzi
Heidar Dadkhah
Sharam Shojaei
Masoume Mahdavi
Alireza Poormotaabed
Nasrin Javid
Samsam Dabiri
Right Atrial Angiosarcoma with Severe Biventricular Dysfunction and Massive Pericardial Effusion
Acta Medica Iranica
Angiosarcoma
Heart Tumor
Pericardial Effusion
title Right Atrial Angiosarcoma with Severe Biventricular Dysfunction and Massive Pericardial Effusion
title_full Right Atrial Angiosarcoma with Severe Biventricular Dysfunction and Massive Pericardial Effusion
title_fullStr Right Atrial Angiosarcoma with Severe Biventricular Dysfunction and Massive Pericardial Effusion
title_full_unstemmed Right Atrial Angiosarcoma with Severe Biventricular Dysfunction and Massive Pericardial Effusion
title_short Right Atrial Angiosarcoma with Severe Biventricular Dysfunction and Massive Pericardial Effusion
title_sort right atrial angiosarcoma with severe biventricular dysfunction and massive pericardial effusion
topic Angiosarcoma
Heart Tumor
Pericardial Effusion
url http://acta.tums.ac.ir/index.php/acta/article/view/2410/2143
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AT sharamshojaei rightatrialangiosarcomawithseverebiventriculardysfunctionandmassivepericardialeffusion
AT masoumemahdavi rightatrialangiosarcomawithseverebiventriculardysfunctionandmassivepericardialeffusion
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