Challenging diagnosis of Kaposiform lymphangiomatosis: Unveiling a rare primary lymphatic disorder
Kaposiform lymphangiomatosis (KLA) is a rare and complex lymphatic anomaly associated with substantial morbidity and mortality. It features diffuse and multifocal malformed lymphatic channels, often leading to diagnostic difficulties due to its uncommon occurrence and non-specific clinical presentat...
| Main Authors: | , |
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| Format: | Article |
| Language: | English |
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Elsevier
2024-02-01
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| Series: | Radiology Case Reports |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S193004332300821X |
| _version_ | 1797398708747239424 |
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| author | Rafael Ospino, BS Claire Brookmeyer, MD |
| author_facet | Rafael Ospino, BS Claire Brookmeyer, MD |
| author_sort | Rafael Ospino, BS |
| collection | DOAJ |
| description | Kaposiform lymphangiomatosis (KLA) is a rare and complex lymphatic anomaly associated with substantial morbidity and mortality. It features diffuse and multifocal malformed lymphatic channels, often leading to diagnostic difficulties due to its uncommon occurrence and non-specific clinical presentation. This case report emphasizes the crucial role of expert radiologists in accurately diagnosing a challenging KLA case initially mistaken for a neoplasm. |
| first_indexed | 2024-03-09T01:29:23Z |
| format | Article |
| id | doaj.art-706b022bb9c4422597d1b16d6a2876ec |
| institution | Directory Open Access Journal |
| issn | 1930-0433 |
| language | English |
| last_indexed | 2024-03-09T01:29:23Z |
| publishDate | 2024-02-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Radiology Case Reports |
| spelling | doaj.art-706b022bb9c4422597d1b16d6a2876ec2023-12-10T06:14:32ZengElsevierRadiology Case Reports1930-04332024-02-01192547552Challenging diagnosis of Kaposiform lymphangiomatosis: Unveiling a rare primary lymphatic disorderRafael Ospino, BS0Claire Brookmeyer, MD1Johns Hopkins University School of Medicine, 601 N Caroline St, Suite 6214, Baltimore, MD, USARussell H. Morgan Department of Radiology, Johns Hopkins School of Medicine, 601 N Caroline St, Suite 6214, Baltimore, MD, USA; Corresponding author.Kaposiform lymphangiomatosis (KLA) is a rare and complex lymphatic anomaly associated with substantial morbidity and mortality. It features diffuse and multifocal malformed lymphatic channels, often leading to diagnostic difficulties due to its uncommon occurrence and non-specific clinical presentation. This case report emphasizes the crucial role of expert radiologists in accurately diagnosing a challenging KLA case initially mistaken for a neoplasm.http://www.sciencedirect.com/science/article/pii/S193004332300821XLymphatic anomaliesComputer tomographyMagnetic resonanceMTOR-inhibitorsKaposiform lymphangiomatosis |
| spellingShingle | Rafael Ospino, BS Claire Brookmeyer, MD Challenging diagnosis of Kaposiform lymphangiomatosis: Unveiling a rare primary lymphatic disorder Radiology Case Reports Lymphatic anomalies Computer tomography Magnetic resonance MTOR-inhibitors Kaposiform lymphangiomatosis |
| title | Challenging diagnosis of Kaposiform lymphangiomatosis: Unveiling a rare primary lymphatic disorder |
| title_full | Challenging diagnosis of Kaposiform lymphangiomatosis: Unveiling a rare primary lymphatic disorder |
| title_fullStr | Challenging diagnosis of Kaposiform lymphangiomatosis: Unveiling a rare primary lymphatic disorder |
| title_full_unstemmed | Challenging diagnosis of Kaposiform lymphangiomatosis: Unveiling a rare primary lymphatic disorder |
| title_short | Challenging diagnosis of Kaposiform lymphangiomatosis: Unveiling a rare primary lymphatic disorder |
| title_sort | challenging diagnosis of kaposiform lymphangiomatosis unveiling a rare primary lymphatic disorder |
| topic | Lymphatic anomalies Computer tomography Magnetic resonance MTOR-inhibitors Kaposiform lymphangiomatosis |
| url | http://www.sciencedirect.com/science/article/pii/S193004332300821X |
| work_keys_str_mv | AT rafaelospinobs challengingdiagnosisofkaposiformlymphangiomatosisunveilingarareprimarylymphaticdisorder AT clairebrookmeyermd challengingdiagnosisofkaposiformlymphangiomatosisunveilingarareprimarylymphaticdisorder |