The neuronal ceroid lipofuscinosis <it>Cln8 </it>gene expression is developmentally regulated in mouse brain and up-regulated in the hippocampal kindling model of epilepsy
<p>Abstract</p> <p>Background</p> <p>The neuronal ceroid lipofuscinoses (NCLs) are a group of inherited neurodegenerative disorders characterized by accumulation of autofluorescent material in many tissues, especially in neurons. Mutations in the <it>CLN8 </it&...
Main Authors: | Kuronen Mervi, Kopra Outi, Aalto Antti, Lonka Liina, Kokaia Zaal, Saarma Mart, Lehesjoki Anna-Elina |
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Format: | Article |
Language: | English |
Published: |
BMC
2005-04-01
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Series: | BMC Neuroscience |
Online Access: | http://www.biomedcentral.com/1471-2202/6/27 |
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