Cerebral pseudotumoral form of Behçet’s disease: About 3 cases
Behçet’s disease is a multisystem vasculitis which can involve the nervous system known as Neuro-Behçet’s disease. Neurological involvement is uncommon in Behçet’s disease, and has a highly variable prevalence. An atypical rare form with pseudotumoral lesions has been described in literature and onl...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Elsevier
2020-06-01
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| Series: | Interdisciplinary Neurosurgery |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2214751919302403 |
| _version_ | 1819099618474983424 |
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| author | Malek Mansour Manel Ben Hmidene Asma Ouerdiene Ines Bedoui Ridha Mrissa |
| author_facet | Malek Mansour Manel Ben Hmidene Asma Ouerdiene Ines Bedoui Ridha Mrissa |
| author_sort | Malek Mansour |
| collection | DOAJ |
| description | Behçet’s disease is a multisystem vasculitis which can involve the nervous system known as Neuro-Behçet’s disease. Neurological involvement is uncommon in Behçet’s disease, and has a highly variable prevalence. An atypical rare form with pseudotumoral lesions has been described in literature and only a few cases have been reported. We report herein a case of three patients with pseudotumoral neuro-Behçet’s disease aged between 30 and 45 years old, with a history of recurrent orogenital ulceration. All patients presented with neurological symptoms associated with at least one large space-occupying lesion on cerebral imaging. Behçet’s disease was diagnosed according to the International Study Group criteria. All cases received corticosteroids and immunosuppressant agents with a spectacular clinical and radiological improvement. Keywords: Behçet’s disease, Neuro-Behçet’s disease, Atypical form, Pseudotumoral form |
| first_indexed | 2024-12-22T00:49:45Z |
| format | Article |
| id | doaj.art-70e5cde6bc4f458b99c3ac049e51d4f9 |
| institution | Directory Open Access Journal |
| issn | 2214-7519 |
| language | English |
| last_indexed | 2024-12-22T00:49:45Z |
| publishDate | 2020-06-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Interdisciplinary Neurosurgery |
| spelling | doaj.art-70e5cde6bc4f458b99c3ac049e51d4f92022-12-21T18:44:28ZengElsevierInterdisciplinary Neurosurgery2214-75192020-06-0120Cerebral pseudotumoral form of Behçet’s disease: About 3 casesMalek Mansour0Manel Ben Hmidene1Asma Ouerdiene2Ines Bedoui3Ridha Mrissa4Military Hospital of Instruction of Tunis 1008 Mont Fleury, TunisiaMilitary Hospital of Instruction of Tunis 1008 Mont Fleury, TunisiaMilitary Hospital of Instruction of Tunis 1008 Mont Fleury, Tunisia; Corresponding author.Military Hospital of Instruction of Tunis 1008 Mont Fleury, TunisiaMilitary Hospital of Instruction of Tunis 1008 Mont Fleury, TunisiaBehçet’s disease is a multisystem vasculitis which can involve the nervous system known as Neuro-Behçet’s disease. Neurological involvement is uncommon in Behçet’s disease, and has a highly variable prevalence. An atypical rare form with pseudotumoral lesions has been described in literature and only a few cases have been reported. We report herein a case of three patients with pseudotumoral neuro-Behçet’s disease aged between 30 and 45 years old, with a history of recurrent orogenital ulceration. All patients presented with neurological symptoms associated with at least one large space-occupying lesion on cerebral imaging. Behçet’s disease was diagnosed according to the International Study Group criteria. All cases received corticosteroids and immunosuppressant agents with a spectacular clinical and radiological improvement. Keywords: Behçet’s disease, Neuro-Behçet’s disease, Atypical form, Pseudotumoral formhttp://www.sciencedirect.com/science/article/pii/S2214751919302403 |
| spellingShingle | Malek Mansour Manel Ben Hmidene Asma Ouerdiene Ines Bedoui Ridha Mrissa Cerebral pseudotumoral form of Behçet’s disease: About 3 cases Interdisciplinary Neurosurgery |
| title | Cerebral pseudotumoral form of Behçet’s disease: About 3 cases |
| title_full | Cerebral pseudotumoral form of Behçet’s disease: About 3 cases |
| title_fullStr | Cerebral pseudotumoral form of Behçet’s disease: About 3 cases |
| title_full_unstemmed | Cerebral pseudotumoral form of Behçet’s disease: About 3 cases |
| title_short | Cerebral pseudotumoral form of Behçet’s disease: About 3 cases |
| title_sort | cerebral pseudotumoral form of behcet s disease about 3 cases |
| url | http://www.sciencedirect.com/science/article/pii/S2214751919302403 |
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