An Adult Paratesticular Malignant Ectomesenchymoma With Post-operative Flare-up of Lung Metastasis

Malignant ectomesenchymoma (MEM) which is derived from the remnants of migratory neural crest cells (ectomesenchyme) is a rare and rapidly progressing tumor consisting of neuroectodermal and mesenchymal neoplastic elements. This tumor occurs mostly in children and adolescents, but rarely in adults....

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Main Authors: Wei-Tang Kao, Yi-Te Chiang, Kai-Yi Tzou
Format: Article
Language:English
Published: Elsevier 2015-09-01
Series:Urology Case Reports
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2214442015000960
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author Wei-Tang Kao
Yi-Te Chiang
Kai-Yi Tzou
author_facet Wei-Tang Kao
Yi-Te Chiang
Kai-Yi Tzou
author_sort Wei-Tang Kao
collection DOAJ
description Malignant ectomesenchymoma (MEM) which is derived from the remnants of migratory neural crest cells (ectomesenchyme) is a rare and rapidly progressing tumor consisting of neuroectodermal and mesenchymal neoplastic elements. This tumor occurs mostly in children and adolescents, but rarely in adults. We report a 34-year-old male with left paratesticular malignant ectomesenchymoma who received radical orchiectomy and was followed by post-operative flare-up of lung metastasis within 2 weeks. We present the overall treatment strategies for this extremely rare tumor and related findings.
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spelling doaj.art-7141b13a8d3a4cef9fa5a894fcc3f4202022-12-22T02:53:43ZengElsevierUrology Case Reports2214-44202015-09-013516416610.1016/j.eucr.2015.06.010An Adult Paratesticular Malignant Ectomesenchymoma With Post-operative Flare-up of Lung MetastasisWei-Tang KaoYi-Te ChiangKai-Yi TzouMalignant ectomesenchymoma (MEM) which is derived from the remnants of migratory neural crest cells (ectomesenchyme) is a rare and rapidly progressing tumor consisting of neuroectodermal and mesenchymal neoplastic elements. This tumor occurs mostly in children and adolescents, but rarely in adults. We report a 34-year-old male with left paratesticular malignant ectomesenchymoma who received radical orchiectomy and was followed by post-operative flare-up of lung metastasis within 2 weeks. We present the overall treatment strategies for this extremely rare tumor and related findings.http://www.sciencedirect.com/science/article/pii/S2214442015000960EctomesenchymomaParatesticular tumorLung metastasis
spellingShingle Wei-Tang Kao
Yi-Te Chiang
Kai-Yi Tzou
An Adult Paratesticular Malignant Ectomesenchymoma With Post-operative Flare-up of Lung Metastasis
Urology Case Reports
Ectomesenchymoma
Paratesticular tumor
Lung metastasis
title An Adult Paratesticular Malignant Ectomesenchymoma With Post-operative Flare-up of Lung Metastasis
title_full An Adult Paratesticular Malignant Ectomesenchymoma With Post-operative Flare-up of Lung Metastasis
title_fullStr An Adult Paratesticular Malignant Ectomesenchymoma With Post-operative Flare-up of Lung Metastasis
title_full_unstemmed An Adult Paratesticular Malignant Ectomesenchymoma With Post-operative Flare-up of Lung Metastasis
title_short An Adult Paratesticular Malignant Ectomesenchymoma With Post-operative Flare-up of Lung Metastasis
title_sort adult paratesticular malignant ectomesenchymoma with post operative flare up of lung metastasis
topic Ectomesenchymoma
Paratesticular tumor
Lung metastasis
url http://www.sciencedirect.com/science/article/pii/S2214442015000960
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