Arrhythmogenic Left Ventricular Cardiomyopathy: A Successful Case of Extracorporeal Cardiopulmonary Resuscitation
A 24-year-old man suffered a witnessed cardiac arrest after a padel game. Basic life support was immediately provided. The pre-hospital emergency services team continued the resuscitation efforts, and the patient was accepted for extracorporeal cardiopulmonary resuscitation. The return of spontaneo...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Ordem dos Médicos
2023-06-01
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| Series: | Acta Médica Portuguesa |
| Subjects: | |
| Online Access: | https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/19624 |
| _version_ | 1797729172017119232 |
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| author | Mafalda Gama Isabel Cardoso Mónica Palma Anselmo Sílvia Aguiar Rosa Pedro Gaspar da Costa Philip Fortuna |
| author_facet | Mafalda Gama Isabel Cardoso Mónica Palma Anselmo Sílvia Aguiar Rosa Pedro Gaspar da Costa Philip Fortuna |
| author_sort | Mafalda Gama |
| collection | DOAJ |
| description |
A 24-year-old man suffered a witnessed cardiac arrest after a padel game. Basic life support was immediately provided. The pre-hospital emergency services team continued the resuscitation efforts, and the patient was accepted for extracorporeal cardiopulmonary resuscitation. The return of spontaneous circulation was achieved in 45 minutes. The initial assessment revealed a ST-segment elevation in leads V4-V6 and a dilated left ventricle with severe systolic dysfunction. Coronary angiography was normal. An improvement in left ventricular systolic function was observed and extracorporeal cardiac support was discontinued after 48 hours. Cardiovascular magnetic resonance imaging demonstrated hypokinesia and subepicardial fatty infiltration of the left ventricle lateral wall. Genetic testing detected a variant of uncertain significance in the ANK2 gene. The diagnosis of arrhythmogenic left ventricular myocardiopathy did not fulfill all the current diagnostic criteria, but it is a very likely diagnosis. An implantable cardioverter-defibrillator was placed. The
patient was discharged without physical or cognitive impairment.
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| first_indexed | 2024-03-12T11:25:10Z |
| format | Article |
| id | doaj.art-716e855478374869b0734546066aba34 |
| institution | Directory Open Access Journal |
| issn | 0870-399X 1646-0758 |
| language | English |
| last_indexed | 2024-03-12T11:25:10Z |
| publishDate | 2023-06-01 |
| publisher | Ordem dos Médicos |
| record_format | Article |
| series | Acta Médica Portuguesa |
| spelling | doaj.art-716e855478374869b0734546066aba342023-09-01T09:12:19ZengOrdem dos MédicosActa Médica Portuguesa0870-399X1646-07582023-06-0136910.20344/amp.19624Arrhythmogenic Left Ventricular Cardiomyopathy: A Successful Case of Extracorporeal Cardiopulmonary ResuscitationMafalda Gama0Isabel Cardoso1Mónica Palma Anselmo2Sílvia Aguiar Rosa3Pedro Gaspar da Costa4Philip Fortuna5Unidade de Urgência Médica. Centro Hospitalar Universitário de Lisboa Central. Lisbon.Serviço de Cardiologia. Centro Hospitalar Universitário de Lisboa Central. Lisbon.Hospital Professor Doutor Fernando da Fonseca. Lisbon. Serviço de Cardiologia. Centro Hospitalar Universitário de Lisboa Central. Lisbon.Unidade de Urgência Médica. Centro Hospitalar Universitário de Lisboa Central. Lisbon.Unidade de Urgência Médica. Centro Hospitalar Universitário de Lisboa Central. Lisbon. A 24-year-old man suffered a witnessed cardiac arrest after a padel game. Basic life support was immediately provided. The pre-hospital emergency services team continued the resuscitation efforts, and the patient was accepted for extracorporeal cardiopulmonary resuscitation. The return of spontaneous circulation was achieved in 45 minutes. The initial assessment revealed a ST-segment elevation in leads V4-V6 and a dilated left ventricle with severe systolic dysfunction. Coronary angiography was normal. An improvement in left ventricular systolic function was observed and extracorporeal cardiac support was discontinued after 48 hours. Cardiovascular magnetic resonance imaging demonstrated hypokinesia and subepicardial fatty infiltration of the left ventricle lateral wall. Genetic testing detected a variant of uncertain significance in the ANK2 gene. The diagnosis of arrhythmogenic left ventricular myocardiopathy did not fulfill all the current diagnostic criteria, but it is a very likely diagnosis. An implantable cardioverter-defibrillator was placed. The patient was discharged without physical or cognitive impairment. https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/19624Arrhythmogenic Left Ventricular CardiomyopathyCardiopulmonary ResuscitationExtracorporeal Membrane OxygenationHeart Arrest/therapy |
| spellingShingle | Mafalda Gama Isabel Cardoso Mónica Palma Anselmo Sílvia Aguiar Rosa Pedro Gaspar da Costa Philip Fortuna Arrhythmogenic Left Ventricular Cardiomyopathy: A Successful Case of Extracorporeal Cardiopulmonary Resuscitation Acta Médica Portuguesa Arrhythmogenic Left Ventricular Cardiomyopathy Cardiopulmonary Resuscitation Extracorporeal Membrane Oxygenation Heart Arrest/therapy |
| title | Arrhythmogenic Left Ventricular Cardiomyopathy: A Successful Case of Extracorporeal Cardiopulmonary Resuscitation |
| title_full | Arrhythmogenic Left Ventricular Cardiomyopathy: A Successful Case of Extracorporeal Cardiopulmonary Resuscitation |
| title_fullStr | Arrhythmogenic Left Ventricular Cardiomyopathy: A Successful Case of Extracorporeal Cardiopulmonary Resuscitation |
| title_full_unstemmed | Arrhythmogenic Left Ventricular Cardiomyopathy: A Successful Case of Extracorporeal Cardiopulmonary Resuscitation |
| title_short | Arrhythmogenic Left Ventricular Cardiomyopathy: A Successful Case of Extracorporeal Cardiopulmonary Resuscitation |
| title_sort | arrhythmogenic left ventricular cardiomyopathy a successful case of extracorporeal cardiopulmonary resuscitation |
| topic | Arrhythmogenic Left Ventricular Cardiomyopathy Cardiopulmonary Resuscitation Extracorporeal Membrane Oxygenation Heart Arrest/therapy |
| url | https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/19624 |
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