Temperature-sensitive Recurrent, Reversible Auditory Neuropathy in Two Iranian Siblings
Two sibling cases with a temperature-sensitive form of auditory neuropathy from a consanguineous marriage of Iranian descent have been described. They complained about the temporary loss of hearing and compromised speech comprehension after a slight fever or elevating the body temperature by vigorou...
| Main Authors: | , |
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| Format: | Article |
| Language: | English |
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Negah Institute for Scientific Communication
2021-09-01
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| Series: | Iranian Rehabilitation Journal |
| Subjects: | |
| Online Access: | http://irj.uswr.ac.ir/article-1-1433-en.pdf |
| _version_ | 1797669642699800576 |
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| author | Nasrin Yazdani Mohsen Ahadi |
| author_facet | Nasrin Yazdani Mohsen Ahadi |
| author_sort | Nasrin Yazdani |
| collection | DOAJ |
| description | Two sibling cases with a temperature-sensitive form of auditory neuropathy from a consanguineous marriage of Iranian descent have been described. They complained about the temporary loss of hearing and compromised speech comprehension after a slight fever or elevating the body temperature by vigorous exercises. A series of tests including brain MRI, pure-tone audiometry, speech audiometry in quiet and noise, tympanometry, reflexometry, TEOAEs, cochlear microphonic, and ABR were performed in a 24-hours interval at both febrile and afebrile states, and results are reported here. This report is the first example of temperature-sensitive auditory neuropathy in this geographical region. |
| first_indexed | 2024-03-11T20:47:26Z |
| format | Article |
| id | doaj.art-720dc99573bf4d0492bbe67e4be57032 |
| institution | Directory Open Access Journal |
| issn | 1735-3602 1735-3610 |
| language | English |
| last_indexed | 2024-03-11T20:47:26Z |
| publishDate | 2021-09-01 |
| publisher | Negah Institute for Scientific Communication |
| record_format | Article |
| series | Iranian Rehabilitation Journal |
| spelling | doaj.art-720dc99573bf4d0492bbe67e4be570322023-10-01T07:32:29ZengNegah Institute for Scientific CommunicationIranian Rehabilitation Journal1735-36021735-36102021-09-01193337342Temperature-sensitive Recurrent, Reversible Auditory Neuropathy in Two Iranian SiblingsNasrin Yazdani0Mohsen Ahadi1 Department of Otorhinolaryngology, Otorhinolaryngology Research Center, Amir-Alam Hospital, Tehran University of Medical Sciences, Tehran, Iran. Department of Audiology, Rehabilitation Research Center, School of Rehabilitation Sciences, Iran University of Medical Sciences, Tehran, Iran. Two sibling cases with a temperature-sensitive form of auditory neuropathy from a consanguineous marriage of Iranian descent have been described. They complained about the temporary loss of hearing and compromised speech comprehension after a slight fever or elevating the body temperature by vigorous exercises. A series of tests including brain MRI, pure-tone audiometry, speech audiometry in quiet and noise, tympanometry, reflexometry, TEOAEs, cochlear microphonic, and ABR were performed in a 24-hours interval at both febrile and afebrile states, and results are reported here. This report is the first example of temperature-sensitive auditory neuropathy in this geographical region.http://irj.uswr.ac.ir/article-1-1433-en.pdfauditory neuropathytemperature-sensitivecase reportsconsanguineous marriage |
| spellingShingle | Nasrin Yazdani Mohsen Ahadi Temperature-sensitive Recurrent, Reversible Auditory Neuropathy in Two Iranian Siblings Iranian Rehabilitation Journal auditory neuropathy temperature-sensitive case reports consanguineous marriage |
| title | Temperature-sensitive Recurrent, Reversible Auditory Neuropathy in Two Iranian Siblings |
| title_full | Temperature-sensitive Recurrent, Reversible Auditory Neuropathy in Two Iranian Siblings |
| title_fullStr | Temperature-sensitive Recurrent, Reversible Auditory Neuropathy in Two Iranian Siblings |
| title_full_unstemmed | Temperature-sensitive Recurrent, Reversible Auditory Neuropathy in Two Iranian Siblings |
| title_short | Temperature-sensitive Recurrent, Reversible Auditory Neuropathy in Two Iranian Siblings |
| title_sort | temperature sensitive recurrent reversible auditory neuropathy in two iranian siblings |
| topic | auditory neuropathy temperature-sensitive case reports consanguineous marriage |
| url | http://irj.uswr.ac.ir/article-1-1433-en.pdf |
| work_keys_str_mv | AT nasrinyazdani temperaturesensitiverecurrentreversibleauditoryneuropathyintwoiraniansiblings AT mohsenahadi temperaturesensitiverecurrentreversibleauditoryneuropathyintwoiraniansiblings |