Prosthodontic management of a young edentulous patient having Papillon–Lefévre syndrome: A rare case report

Papillon–Lefevre syndrome is a rare autosomal recessive disorder, in which the clinical manifestations are periodontitis which results in premature loss of both deciduous and permanent teeth and palmoplantar keratinization. The palmoplantar keratoderma typically has its onset between the ages of 1 a...

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Main Authors: Ruhi Bajaj, Meenu Garg, Salil Pawah, Ramesh Gupta
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2017-01-01
Series:The Saint's International Dental Journal
Subjects:
Online Access:http://www.sidj.org/article.asp?issn=2454-3160;year=2017;volume=3;issue=1;spage=11;epage=14;aulast=Bajaj
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author Ruhi Bajaj
Meenu Garg
Salil Pawah
Ramesh Gupta
author_facet Ruhi Bajaj
Meenu Garg
Salil Pawah
Ramesh Gupta
author_sort Ruhi Bajaj
collection DOAJ
description Papillon–Lefevre syndrome is a rare autosomal recessive disorder, in which the clinical manifestations are periodontitis which results in premature loss of both deciduous and permanent teeth and palmoplantar keratinization. The palmoplantar keratoderma typically has its onset between the ages of 1 and 4 years and severe periodontitis starts at the age of 3 or 4 years. The deciduous teeth frequently fall out by about age five and most of the permanent teeth may also be lost by approximately age 17. In the present case, a young, edentulous male of this syndrome having most the characteristic features was treated by modified complete denture prosthesis considering his young age and low socioeconomic status.
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spelling doaj.art-722354c5388c47dda59ce186e1189a462022-12-21T22:53:55ZengWolters Kluwer Medknow PublicationsThe Saint's International Dental Journal2454-31602589-73732017-01-0131111410.4103/sidj.sidj_5_17Prosthodontic management of a young edentulous patient having Papillon–Lefévre syndrome: A rare case reportRuhi BajajMeenu GargSalil PawahRamesh GuptaPapillon–Lefevre syndrome is a rare autosomal recessive disorder, in which the clinical manifestations are periodontitis which results in premature loss of both deciduous and permanent teeth and palmoplantar keratinization. The palmoplantar keratoderma typically has its onset between the ages of 1 and 4 years and severe periodontitis starts at the age of 3 or 4 years. The deciduous teeth frequently fall out by about age five and most of the permanent teeth may also be lost by approximately age 17. In the present case, a young, edentulous male of this syndrome having most the characteristic features was treated by modified complete denture prosthesis considering his young age and low socioeconomic status.http://www.sidj.org/article.asp?issn=2454-3160;year=2017;volume=3;issue=1;spage=11;epage=14;aulast=Bajajkeratodermapapillon–lefevre syndromeperiodontitis
spellingShingle Ruhi Bajaj
Meenu Garg
Salil Pawah
Ramesh Gupta
Prosthodontic management of a young edentulous patient having Papillon–Lefévre syndrome: A rare case report
The Saint's International Dental Journal
keratoderma
papillon–lefevre syndrome
periodontitis
title Prosthodontic management of a young edentulous patient having Papillon–Lefévre syndrome: A rare case report
title_full Prosthodontic management of a young edentulous patient having Papillon–Lefévre syndrome: A rare case report
title_fullStr Prosthodontic management of a young edentulous patient having Papillon–Lefévre syndrome: A rare case report
title_full_unstemmed Prosthodontic management of a young edentulous patient having Papillon–Lefévre syndrome: A rare case report
title_short Prosthodontic management of a young edentulous patient having Papillon–Lefévre syndrome: A rare case report
title_sort prosthodontic management of a young edentulous patient having papillon lefevre syndrome a rare case report
topic keratoderma
papillon–lefevre syndrome
periodontitis
url http://www.sidj.org/article.asp?issn=2454-3160;year=2017;volume=3;issue=1;spage=11;epage=14;aulast=Bajaj
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