Retinal Dysplasia Mimicking Retinoblastoma

Retinal dysplasia represents a congenital disorder characterized by abnormal proliferation of retinal tissue causing leukocoria. We present a case of an infant with bilateral leukocoria, clinically diagnosed as retinoblastoma, followed by enucleation of the left eye. Microscopy however, demonstrated...

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Bibliographic Details
Main Authors: Ravikumar HN, Vani Ravikumar, Santosh KV, Annie Joji
Format: Article
Language:English
Published: Light House Polyclinic Mangalore 2012-10-01
Series:Online Journal of Health & Allied Sciences
Subjects:
Online Access:http://www.ojhas.org/issue43/2012-3-10.htm
Description
Summary:Retinal dysplasia represents a congenital disorder characterized by abnormal proliferation of retinal tissue causing leukocoria. We present a case of an infant with bilateral leukocoria, clinically diagnosed as retinoblastoma, followed by enucleation of the left eye. Microscopy however, demonstrated retinal dysplasia consisting of a disorderly proliferation of retinal tissue with formation of rosettes, mimicking retinoblastoma. Microscopic features that aid in differentiating this lesion from retinoblastoma are discussed.
ISSN:0972-5997