Constrictive pericarditis in a patient with inherited factor VII deficiency

Constrictive pericarditis (CP) is the final stage of a chronic inflammatory process characterized by fibrous thickening and calcification of the pericardium that impairs diastolic filling, reduces cardiac output, and ultimately leads to heart failure. We present a clinical case of CP in a patient wi...

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Bibliographic Details
Main Authors: R V PONOMAREV, S V MODEL, N I ZOZULYA, V A IVANOV, D A PODCHASOV, E A MERSHINA, V E SINITSYN, E A LUKINA
Format: Article
Language:Russian
Published: "Consilium Medicum" Publishing house 2018-07-01
Series:Терапевтический архив
Subjects:
Online Access:https://ter-arkhiv.ru/0040-3660/article/view/32796
Description
Summary:Constrictive pericarditis (CP) is the final stage of a chronic inflammatory process characterized by fibrous thickening and calcification of the pericardium that impairs diastolic filling, reduces cardiac output, and ultimately leads to heart failure. We present a clinical case of CP in a patient with rare inherited bleeding disorder - factor VII deficiency. Heart failure due to CP was suspected based on clinical symptoms, results of ultrasonic and radiological investigations. The diagnosis was verified by the results of cardiac magnetic resonance imaging. Pericardectomy was performed resulting in significant improvement in the patient’s condition.
ISSN:0040-3660
2309-5342