Constrictive pericarditis in a patient with inherited factor VII deficiency
Constrictive pericarditis (CP) is the final stage of a chronic inflammatory process characterized by fibrous thickening and calcification of the pericardium that impairs diastolic filling, reduces cardiac output, and ultimately leads to heart failure. We present a clinical case of CP in a patient wi...
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Format: | Article |
Language: | Russian |
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"Consilium Medicum" Publishing house
2018-07-01
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Series: | Терапевтический архив |
Subjects: | |
Online Access: | https://ter-arkhiv.ru/0040-3660/article/view/32796 |
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author | R V PONOMAREV S V MODEL N I ZOZULYA V A IVANOV D A PODCHASOV E A MERSHINA V E SINITSYN E A LUKINA |
author_facet | R V PONOMAREV S V MODEL N I ZOZULYA V A IVANOV D A PODCHASOV E A MERSHINA V E SINITSYN E A LUKINA |
author_sort | R V PONOMAREV |
collection | DOAJ |
description | Constrictive pericarditis (CP) is the final stage of a chronic inflammatory process characterized by fibrous thickening and calcification of the pericardium that impairs diastolic filling, reduces cardiac output, and ultimately leads to heart failure. We present a clinical case of CP in a patient with rare inherited bleeding disorder - factor VII deficiency. Heart failure due to CP was suspected based on clinical symptoms, results of ultrasonic and radiological investigations. The diagnosis was verified by the results of cardiac magnetic resonance imaging. Pericardectomy was performed resulting in significant improvement in the patient’s condition. |
first_indexed | 2024-12-16T06:33:02Z |
format | Article |
id | doaj.art-7238e29b652f4a0ea1fa53e41c46e6e6 |
institution | Directory Open Access Journal |
issn | 0040-3660 2309-5342 |
language | Russian |
last_indexed | 2024-12-16T06:33:02Z |
publishDate | 2018-07-01 |
publisher | "Consilium Medicum" Publishing house |
record_format | Article |
series | Терапевтический архив |
spelling | doaj.art-7238e29b652f4a0ea1fa53e41c46e6e62022-12-21T22:40:51Zrus"Consilium Medicum" Publishing houseТерапевтический архив0040-36602309-53422018-07-01907869010.26442/terarkh201890786-9029548Constrictive pericarditis in a patient with inherited factor VII deficiencyR V PONOMAREV0S V MODEL1N I ZOZULYA2V A IVANOV3D A PODCHASOV4E A MERSHINA5V E SINITSYN6E A LUKINA7National Research Center for HematologyNational Research Center for HematologyNational Research Center for HematologyRussian Scientific Center for Surgery named B.V. PetrovskyRussian Scientific Center for Surgery named B.V. PetrovskyFederal Center of Treatment and Rehabilitation Ministry of Health of the RFFederal Center of Treatment and Rehabilitation Ministry of Health of the RFNational Research Center for HematologyConstrictive pericarditis (CP) is the final stage of a chronic inflammatory process characterized by fibrous thickening and calcification of the pericardium that impairs diastolic filling, reduces cardiac output, and ultimately leads to heart failure. We present a clinical case of CP in a patient with rare inherited bleeding disorder - factor VII deficiency. Heart failure due to CP was suspected based on clinical symptoms, results of ultrasonic and radiological investigations. The diagnosis was verified by the results of cardiac magnetic resonance imaging. Pericardectomy was performed resulting in significant improvement in the patient’s condition.https://ter-arkhiv.ru/0040-3660/article/view/32796constrictive pericarditispericardectomyhypoproconvertinemiavii factor deficiency |
spellingShingle | R V PONOMAREV S V MODEL N I ZOZULYA V A IVANOV D A PODCHASOV E A MERSHINA V E SINITSYN E A LUKINA Constrictive pericarditis in a patient with inherited factor VII deficiency Терапевтический архив constrictive pericarditis pericardectomy hypoproconvertinemia vii factor deficiency |
title | Constrictive pericarditis in a patient with inherited factor VII deficiency |
title_full | Constrictive pericarditis in a patient with inherited factor VII deficiency |
title_fullStr | Constrictive pericarditis in a patient with inherited factor VII deficiency |
title_full_unstemmed | Constrictive pericarditis in a patient with inherited factor VII deficiency |
title_short | Constrictive pericarditis in a patient with inherited factor VII deficiency |
title_sort | constrictive pericarditis in a patient with inherited factor vii deficiency |
topic | constrictive pericarditis pericardectomy hypoproconvertinemia vii factor deficiency |
url | https://ter-arkhiv.ru/0040-3660/article/view/32796 |
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