Constrictive pericarditis in a patient with inherited factor VII deficiency

Constrictive pericarditis (CP) is the final stage of a chronic inflammatory process characterized by fibrous thickening and calcification of the pericardium that impairs diastolic filling, reduces cardiac output, and ultimately leads to heart failure. We present a clinical case of CP in a patient wi...

Full description

Bibliographic Details
Main Authors: R V PONOMAREV, S V MODEL, N I ZOZULYA, V A IVANOV, D A PODCHASOV, E A MERSHINA, V E SINITSYN, E A LUKINA
Format: Article
Language:Russian
Published: "Consilium Medicum" Publishing house 2018-07-01
Series:Терапевтический архив
Subjects:
Online Access:https://ter-arkhiv.ru/0040-3660/article/view/32796
_version_ 1818577634808823808
author R V PONOMAREV
S V MODEL
N I ZOZULYA
V A IVANOV
D A PODCHASOV
E A MERSHINA
V E SINITSYN
E A LUKINA
author_facet R V PONOMAREV
S V MODEL
N I ZOZULYA
V A IVANOV
D A PODCHASOV
E A MERSHINA
V E SINITSYN
E A LUKINA
author_sort R V PONOMAREV
collection DOAJ
description Constrictive pericarditis (CP) is the final stage of a chronic inflammatory process characterized by fibrous thickening and calcification of the pericardium that impairs diastolic filling, reduces cardiac output, and ultimately leads to heart failure. We present a clinical case of CP in a patient with rare inherited bleeding disorder - factor VII deficiency. Heart failure due to CP was suspected based on clinical symptoms, results of ultrasonic and radiological investigations. The diagnosis was verified by the results of cardiac magnetic resonance imaging. Pericardectomy was performed resulting in significant improvement in the patient’s condition.
first_indexed 2024-12-16T06:33:02Z
format Article
id doaj.art-7238e29b652f4a0ea1fa53e41c46e6e6
institution Directory Open Access Journal
issn 0040-3660
2309-5342
language Russian
last_indexed 2024-12-16T06:33:02Z
publishDate 2018-07-01
publisher "Consilium Medicum" Publishing house
record_format Article
series Терапевтический архив
spelling doaj.art-7238e29b652f4a0ea1fa53e41c46e6e62022-12-21T22:40:51Zrus"Consilium Medicum" Publishing houseТерапевтический архив0040-36602309-53422018-07-01907869010.26442/terarkh201890786-9029548Constrictive pericarditis in a patient with inherited factor VII deficiencyR V PONOMAREV0S V MODEL1N I ZOZULYA2V A IVANOV3D A PODCHASOV4E A MERSHINA5V E SINITSYN6E A LUKINA7National Research Center for HematologyNational Research Center for HematologyNational Research Center for HematologyRussian Scientific Center for Surgery named B.V. PetrovskyRussian Scientific Center for Surgery named B.V. PetrovskyFederal Center of Treatment and Rehabilitation Ministry of Health of the RFFederal Center of Treatment and Rehabilitation Ministry of Health of the RFNational Research Center for HematologyConstrictive pericarditis (CP) is the final stage of a chronic inflammatory process characterized by fibrous thickening and calcification of the pericardium that impairs diastolic filling, reduces cardiac output, and ultimately leads to heart failure. We present a clinical case of CP in a patient with rare inherited bleeding disorder - factor VII deficiency. Heart failure due to CP was suspected based on clinical symptoms, results of ultrasonic and radiological investigations. The diagnosis was verified by the results of cardiac magnetic resonance imaging. Pericardectomy was performed resulting in significant improvement in the patient’s condition.https://ter-arkhiv.ru/0040-3660/article/view/32796constrictive pericarditispericardectomyhypoproconvertinemiavii factor deficiency
spellingShingle R V PONOMAREV
S V MODEL
N I ZOZULYA
V A IVANOV
D A PODCHASOV
E A MERSHINA
V E SINITSYN
E A LUKINA
Constrictive pericarditis in a patient with inherited factor VII deficiency
Терапевтический архив
constrictive pericarditis
pericardectomy
hypoproconvertinemia
vii factor deficiency
title Constrictive pericarditis in a patient with inherited factor VII deficiency
title_full Constrictive pericarditis in a patient with inherited factor VII deficiency
title_fullStr Constrictive pericarditis in a patient with inherited factor VII deficiency
title_full_unstemmed Constrictive pericarditis in a patient with inherited factor VII deficiency
title_short Constrictive pericarditis in a patient with inherited factor VII deficiency
title_sort constrictive pericarditis in a patient with inherited factor vii deficiency
topic constrictive pericarditis
pericardectomy
hypoproconvertinemia
vii factor deficiency
url https://ter-arkhiv.ru/0040-3660/article/view/32796
work_keys_str_mv AT rvponomarev constrictivepericarditisinapatientwithinheritedfactorviideficiency
AT svmodel constrictivepericarditisinapatientwithinheritedfactorviideficiency
AT nizozulya constrictivepericarditisinapatientwithinheritedfactorviideficiency
AT vaivanov constrictivepericarditisinapatientwithinheritedfactorviideficiency
AT dapodchasov constrictivepericarditisinapatientwithinheritedfactorviideficiency
AT eamershina constrictivepericarditisinapatientwithinheritedfactorviideficiency
AT vesinitsyn constrictivepericarditisinapatientwithinheritedfactorviideficiency
AT ealukina constrictivepericarditisinapatientwithinheritedfactorviideficiency